This document discusses the approach of a pediatrician to a newborn with anorectal malformation (ARM). It describes the pediatrician's role in diagnosis, initial stabilization, and referral to a pediatric surgeon. It provides details on clinical examination findings for ARM in males and females. It also discusses associated malformations, initial management including antibiotics and fluids, and investigations like invertogram to classify the ARM.
1. ANORECTAL MALFORMATION
Approach Of A Pediatrician To A Case Of
Newborn With ANORECTAL
MALFORMATION
Speakers -Dr.Sushmita Ghosh
Moderator-Dr.M.K.Mohanty(Paed.Surgeon)
Jawaharlal Nehru Hospital & Research Centre
Bhilai Steel Plant Hospital
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2. INTRODUCTION
Anorectal malformation-
Complex disorder ranging from cloaca
(most severe) to perineal fistula.
Invertogram- in 1930
Upto 1948 Surgical correction-Rhodes
Since 1982- PSARP by Alberto Pena
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3. ROLE OF PEDIATRICIAN
Intramural Extramural
(delivery-own hosp.)
*diagnosis (outside delivery)
*initial stabilization *diagnosed outside
*referral to paed.surgeon *stabilization
*treatment of sepsis,if any
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8. NEWBORN WITH ARM (FEMALE)
PERINEAL INSPECTION
FISTULA(APPROX.90%) NO FISTULA(APPROX.10%)
SINGLE OPENING TWO OPENINGs THREE OPENINGs
CLOACA VAGINAL CUTANEOUS
OR (PERINEAL) INVERTOGRAM
VESTIBULAR
>1 CM BOWEL- <1 CM BOWEL-
SKIN DISTANCE SKIN DIST.
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14. INCIDENCE
WORLDWIDE 1:5,000 LIVE BIRTHS
GENETIC PREDISPOSITION IN CERTAIN FAMILIES
ASSOCIATION WITH CERTAIN SYNDROMES-
VACTERL,VATER,DOWN’S SYNDROME
SLIGHT MALE PREPONDERANCE
IN FEMALES-RECTOVESTIBULAR FISTULA MOST COMMON
IN MALES -RECTOURETHRAL FISTULA MOST COMMON
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15. INITIAL MANAGEMENT
RED RUBBER CATHETER INSERTION
NBM & INTRAVENOUS FLUIDS
FIRST LINE ANTIBIOTICS- CLOXACILLIN
& AMIKACIN
INJECTION VITAMIN K
NASOGASTRIC DECOMPRESSION after 24 hrs
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16. ASSOCIATED MALFORMATIONS
(50-60%)
UROGENITAL-
URINARY-UNILATERAL AGENESIS OF KIDNEY
-PUJ OBSTRUCTION
-HYPOSPADIAS
-VUR
GENITAL- BICORNUATE UTERUS
-UTERUS DIDELPHYS
-VAGINAL SEPTUM
-BLIND HEMIVAGINA
-ATRESIA OF CERVIX
-HYDROCOLPOS
CARDIOVASCULAR- 1/3RD Pts
-ASD,PDA most common
-VSD,TOF
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