A 16-year-old male presented with a 4-year history of occipital headaches and neck pain, as well as a 2-year history of loss of pain and temperature sensation in his left upper limb. Examination revealed absent biceps and supinator reflexes on the left side. MRI of the cervical spine showed Arnold-Chiari malformation type 1 with syringomyelia involving the cervical and thoracic spinal cord regions. The patient was diagnosed with syringomyelia associated with Arnold-Chiari malformation type 1.