By: Livson Thomas
M.Sc (N) 2nd Year


WILLIAM
JOHN
LITTLE
(1810-1894)

In 1860s, known as
"Cerebral Paralysis” or
“Little’s Disease”



After an English surgeon who
wrote the 1st medical
descriptions William John
Little.


Cerebral“- Latin Cerebrum;




Af fected par t of brain

“Palsy " -Gr. para- beyond,
lysis – loosening


Lack of muscle control


A motor function disorder








caused by permanent, non-progressive brain
lesion
present at birth or shortly thereafter. (Mosby, 2006)

Non-curable, life-long condition
Damage doesn’t worsen
May be congenital or acquired
A Heterogenous Group
of Movement Disorders
– An umbrella term
– Not a single diagnosis
ements

ation

Balance
Posture
OF CEREBRAL PALSY
An insult or injury to the brain

– Fixed, static lesion(s)
– In single or multiple
areas of the motor
centers of the brain
– Early in CNS deveation


Development Malformations




The brain fails to develop correctly.

Neurological damage



Can occur before, during or after delivery
Rh incompatibility, illness, severe lack of oxygen

* Unknown in many instances
Severe deprivation of
oxygen or
blood flow to the brain
– Hypoxic-ischemic
encephalopathy
or intrapartal
asphyxia
OF CEREBRAL PALSY


Based on the
- extent of the damage
- area of brain damage



Each type involves the way
a person moves
1. PYRAMIDAL
- originates from the motor areas
of the cerebral cortex

2. EXTAPYRAMIDAL
- basal ganglia and cerebellum

3. MIXED
2. According to Type of Movement

Photo from: Saunders, Elsvier.
1. Spastic CP
2. Athethoid CP
3. Ataxic CP
4. Spastic &
Athethoid CP
TYPES
SPASTIC -Stiffness

ATHETOID
--Fluctuating
Uncontrolled
Tone
Movements

ATAXIC
-Unsteady,
Unsteady,

uncoordinated
uncoordinated
According to af fected limbs :
* plegia or paresis - meaning paralyzed or weak:







Paraplegia
Diplegia
Hemiplegia
Quadriplegia
Monoplegia –one limb (extremely rare)
Triplegia
–three limbs (extremely rare)
1. Mild CP- 20% of cases
2. Moderate CP- 50%
- require self help for assisting their

impaired ambulation capacity.
3.Severe CP- 30%
-totally incapacited and bedridden and
they always need care from others.
OF CEREBRAL PALSY
d.
c.

e.
f.

b.
a.

g.
h.
Infancy (0-3 Months)

• Stiff or floppy posture
• Excessive lethargy or
irritability/ High pitched cry
• Poor head control
• Weak suck/ tongue thrust/
tonic bite/ feeding difficulties


Abnormal or prolonged
primitive reflexes
Moro’s reflex
Asymmetric tonic neck reflex
Placing reflex
Landau reflex
ch al
ea nt
r e
to m es
ow elop ton
Sl v
e il e s
d m





Poor ability to
concentrate,
unusual tenseness,
Irritability
OF CEREBRAL PALSY










Hearing and visual
problems

• Bladder and bowel
control problems,
digestive problems
Sensory integration
(gastroesophageal reflux)
problems
Failure-to-thrive, Feeding • Skeletal deformities,
dental problems
problems
• Mental retardation and
Behavioral/emotional
learning disabilities in
difficulties,
some
Communication
• Seizures/ epilepsy
disorders
OF CEREBRAL PALSY





Physical evaluation, Interview
MRI, CT Scan EEG
Laboratory and radiologic work up
Assessment tools


i.e. Peabody Development Motor Skills,
Denver Test II
- INTERVIEW


Include all that may
predispose an infant to
brain damage or CP
 Risk

factors
 Psychosocial factors
 Family adaptation


Of ten admitted to hospitals for
corrective surgeries and other
complications.







Respiratory status
Motor function
Presence of fever
Feeding and weight loss
Any changes in physical state
Medical regimen
-

Physical Examination
P osturing / Poor muscle control and strength
O ropharyngeal problems
S trabismus/ Squint
S
T one (hyper-, hypotonia)
T
E volutional maldevelopment
E
R eflexes (e.g. increaseddeep tendon)
R
* Abnormalities 4/6 strongly point to
CP
OF CEREBRAL PALSY
-



No treatment to cure cerebral palsy.
Brain damage cannot be corrected.

Crucial for children with CP :
 Early Identification;
 Multidisciplinar y Care; and
 Suppor t
I . Nonphysical

Therapy
A. General management
- Proper nutrition and personal care

B. Pharmacologic
Botox, Intrathecal, Baclofen
- control muscle spasms and seizures,
Glycopyrrolate -control drooling
Pamidronate -may help with osteoporosis.
C. Surger y
-To loosen joints,
-Relieve muscle tightness,
- Straightening of dif ferent twists or
unusual cur vatures of leg muscles
- Improve the ability to sit, stand,
and walk.
Selective posterior rhizotomy
In some cases ner ves need to be severed to
decrease muscle tension of inappropriate
contractions.
D. Physical Aids




Or thosis, braces and splints
Positioning devices
Walkers, special scooters, wheelchairs

E. Special Education
F. Rehabilitation Ser vices- Speech and
occupational therapies
G. Family Ser vices - Professional support
H. Other Treatment
-

 

Therapeutic electrical
stimulation,
Acupuncture,
Hyperbaric therapy
Massage Therapy might help
II . Physical Therapy
A. Sitting
- Vertical head control and
control of head and trunk.
B. Standing and walking
- Establish an equal distribution of
weight on each foot, train to use steps or
inclines
C. Prone Development
D. Supine Development
o Head control on supine and positions
NURSING RESPONSIBILITIES
A. Functioning as a member of the
health team
B. Providing counseling and education
for the parents and promote optimal
family functioning
-

Encourage
family
members
to
express
anxieties, frustrations and concerns
Provide emotional support and help with problem
solving as necessary.
Explore support networks. Refer them to support
organizations
C. Promoting physical and
psychological health
-

Administer prescribed medications

-

Encourage self-care by urging the child to participate in
activities of daily living (ADLs) (e.g. using utensils and
implements that are appropriate for the child’s age and
condition).

-

Provide rest periods to foster relaxation. Provide safe &
appropriate toys

-

As necessary, seek referrals for corrective lenses and
hearing device to decrease sensory deprivation related
to vision and hearing losses
D. Assisting with feeding management
and toilet training
Promote adequate fluid and nutritional intake.
 Position upright after meals
- During meals, maintain a quiet, unhurried atmosphere with
as few distractions as possible. The child may need special
utensils and a chair with a solid footrest
- Teach him to place food far back in his mouth to facilitate
swallowing.
- Encourage the child to chew food thoroughly, drink through
a straw, and suck on a lollipop between meals to develop
the muscle control needed to minimize drooling.
-
E. Assisting with rehabilitation therapies
(physical, occupational and speech)

Promote mobility by encouraging the child to perform
age-and
condition-appropriate
motor
activities
- Inform parents but their child will need considerable
help and patience in accomplishing each new
task.
- Encourage them not to focus solely on the child’s
inability to accomplish certain
-
-

Explain the importance of providing positive
feedback.

-

Facilitated communication. Talk to the
child deliberately and slowly, using pictures or
sign language to reinforce speech when needed

-

Technology such as computer use may help
children with severe articulation problems.
F. Providing counseling for educational
and vocational pursuits
G. Preventing child abuse
H. Providing care during hospitalization
Prepare the child and family for
procedures, treatments, appliances and
surgeries if needed. Assign the child a
room with children in the same age-group.
I. Prevent physical injur y by providing the
child with a safe environment, appropriate toys,
and protective gear (helmet, kneepads) if
needed.

J. Prevent physical deformity by ensuring
correct use of prescribed braces and other
devices and by performing ROM exercises.
K. Promote a positive self-image in the
child:
-

Praise his accomplishments
Set realistic and attainable goals
Encourage and appealing physical appearance
Encourage his involvement with age and condition
appropriate peer group activities.
Cerebral Palsy

Cerebral Palsy

  • 1.
  • 2.
     WILLIAM JOHN LITTLE (1810-1894) In 1860s, knownas "Cerebral Paralysis” or “Little’s Disease”  After an English surgeon who wrote the 1st medical descriptions William John Little.
  • 3.
     Cerebral“- Latin Cerebrum;   Affected par t of brain “Palsy " -Gr. para- beyond, lysis – loosening  Lack of muscle control
  • 4.
     A motor functiondisorder      caused by permanent, non-progressive brain lesion present at birth or shortly thereafter. (Mosby, 2006) Non-curable, life-long condition Damage doesn’t worsen May be congenital or acquired
  • 5.
    A Heterogenous Group ofMovement Disorders – An umbrella term – Not a single diagnosis
  • 6.
  • 7.
  • 8.
    An insult orinjury to the brain – Fixed, static lesion(s) – In single or multiple areas of the motor centers of the brain – Early in CNS deveation
  • 9.
     Development Malformations   The brainfails to develop correctly. Neurological damage   Can occur before, during or after delivery Rh incompatibility, illness, severe lack of oxygen * Unknown in many instances
  • 10.
    Severe deprivation of oxygenor blood flow to the brain – Hypoxic-ischemic encephalopathy or intrapartal asphyxia
  • 11.
  • 12.
     Based on the -extent of the damage - area of brain damage  Each type involves the way a person moves
  • 13.
    1. PYRAMIDAL - originatesfrom the motor areas of the cerebral cortex 2. EXTAPYRAMIDAL - basal ganglia and cerebellum 3. MIXED
  • 14.
    2. According toType of Movement Photo from: Saunders, Elsvier.
  • 15.
    1. Spastic CP 2.Athethoid CP 3. Ataxic CP 4. Spastic & Athethoid CP
  • 16.
  • 17.
    According to affected limbs : * plegia or paresis - meaning paralyzed or weak:       Paraplegia Diplegia Hemiplegia Quadriplegia Monoplegia –one limb (extremely rare) Triplegia –three limbs (extremely rare)
  • 18.
    1. Mild CP-20% of cases 2. Moderate CP- 50% - require self help for assisting their impaired ambulation capacity. 3.Severe CP- 30% -totally incapacited and bedridden and they always need care from others.
  • 19.
  • 20.
  • 21.
    Infancy (0-3 Months) •Stiff or floppy posture • Excessive lethargy or irritability/ High pitched cry • Poor head control • Weak suck/ tongue thrust/ tonic bite/ feeding difficulties
  • 22.
     Abnormal or prolonged primitivereflexes Moro’s reflex Asymmetric tonic neck reflex Placing reflex Landau reflex
  • 23.
    ch al ea nt re to m es ow elop ton Sl v e il e s d m
  • 24.
  • 26.
  • 27.
         Hearing and visual problems •Bladder and bowel control problems, digestive problems Sensory integration (gastroesophageal reflux) problems Failure-to-thrive, Feeding • Skeletal deformities, dental problems problems • Mental retardation and Behavioral/emotional learning disabilities in difficulties, some Communication • Seizures/ epilepsy disorders
  • 28.
  • 29.
        Physical evaluation, Interview MRI,CT Scan EEG Laboratory and radiologic work up Assessment tools  i.e. Peabody Development Motor Skills, Denver Test II
  • 31.
  • 32.
     Include all thatmay predispose an infant to brain damage or CP  Risk factors  Psychosocial factors  Family adaptation
  • 33.
     Of ten admittedto hospitals for corrective surgeries and other complications.       Respiratory status Motor function Presence of fever Feeding and weight loss Any changes in physical state Medical regimen
  • 34.
  • 35.
    P osturing /Poor muscle control and strength O ropharyngeal problems S trabismus/ Squint S T one (hyper-, hypotonia) T E volutional maldevelopment E R eflexes (e.g. increaseddeep tendon) R * Abnormalities 4/6 strongly point to CP
  • 36.
  • 37.
    -  No treatment tocure cerebral palsy. Brain damage cannot be corrected. Crucial for children with CP :  Early Identification;  Multidisciplinar y Care; and  Suppor t
  • 38.
  • 39.
    A. General management -Proper nutrition and personal care B. Pharmacologic Botox, Intrathecal, Baclofen - control muscle spasms and seizures, Glycopyrrolate -control drooling Pamidronate -may help with osteoporosis.
  • 40.
    C. Surger y -Toloosen joints, -Relieve muscle tightness, - Straightening of dif ferent twists or unusual cur vatures of leg muscles - Improve the ability to sit, stand, and walk.
  • 41.
    Selective posterior rhizotomy Insome cases ner ves need to be severed to decrease muscle tension of inappropriate contractions.
  • 42.
    D. Physical Aids    Orthosis, braces and splints Positioning devices Walkers, special scooters, wheelchairs E. Special Education F. Rehabilitation Ser vices- Speech and occupational therapies G. Family Ser vices - Professional support
  • 43.
    H. Other Treatment -   Therapeuticelectrical stimulation, Acupuncture, Hyperbaric therapy Massage Therapy might help
  • 44.
  • 45.
    A. Sitting - Verticalhead control and control of head and trunk. B. Standing and walking - Establish an equal distribution of weight on each foot, train to use steps or inclines
  • 46.
    C. Prone Development D.Supine Development o Head control on supine and positions
  • 48.
    NURSING RESPONSIBILITIES A. Functioningas a member of the health team
  • 49.
    B. Providing counselingand education for the parents and promote optimal family functioning - Encourage family members to express anxieties, frustrations and concerns Provide emotional support and help with problem solving as necessary. Explore support networks. Refer them to support organizations
  • 50.
    C. Promoting physicaland psychological health - Administer prescribed medications - Encourage self-care by urging the child to participate in activities of daily living (ADLs) (e.g. using utensils and implements that are appropriate for the child’s age and condition). - Provide rest periods to foster relaxation. Provide safe & appropriate toys - As necessary, seek referrals for corrective lenses and hearing device to decrease sensory deprivation related to vision and hearing losses
  • 51.
    D. Assisting withfeeding management and toilet training Promote adequate fluid and nutritional intake.  Position upright after meals - During meals, maintain a quiet, unhurried atmosphere with as few distractions as possible. The child may need special utensils and a chair with a solid footrest - Teach him to place food far back in his mouth to facilitate swallowing. - Encourage the child to chew food thoroughly, drink through a straw, and suck on a lollipop between meals to develop the muscle control needed to minimize drooling. -
  • 52.
    E. Assisting withrehabilitation therapies (physical, occupational and speech) Promote mobility by encouraging the child to perform age-and condition-appropriate motor activities - Inform parents but their child will need considerable help and patience in accomplishing each new task. - Encourage them not to focus solely on the child’s inability to accomplish certain -
  • 53.
    - Explain the importanceof providing positive feedback. - Facilitated communication. Talk to the child deliberately and slowly, using pictures or sign language to reinforce speech when needed - Technology such as computer use may help children with severe articulation problems.
  • 54.
    F. Providing counselingfor educational and vocational pursuits G. Preventing child abuse H. Providing care during hospitalization Prepare the child and family for procedures, treatments, appliances and surgeries if needed. Assign the child a room with children in the same age-group.
  • 55.
    I. Prevent physicalinjur y by providing the child with a safe environment, appropriate toys, and protective gear (helmet, kneepads) if needed. J. Prevent physical deformity by ensuring correct use of prescribed braces and other devices and by performing ROM exercises.
  • 56.
    K. Promote apositive self-image in the child: - Praise his accomplishments Set realistic and attainable goals Encourage and appealing physical appearance Encourage his involvement with age and condition appropriate peer group activities.

Editor's Notes

  • #3 William John Little He is an English surgeon Suffered childhood poliomyelitis with residual left lower extremity paraparesis, complicated by severe talipes He 1st identified Cerebral Palsy in his publication "On the Deformities of the Human Frame" in the 1860s One of the first to bridge the gap between neurology and orthopaedics CP was then known as "Cerebral Paralysis" or “Little’s Disease
  • #7 CP affectd
  • #17 The cortex controls thought, movement and sensation. An abnormality in the movement area of the cortex can result in spastic cerebral palsy Part 2The basal ganglia helps movement become organised, graceful and economical. An abnormality can result in athetoid cerebral palsy.Part 3The cerebellum coordinates movement, posture and balance. An abnormality can result in ataxic cerebral palsy. 
  • #18 According to affected limbs DiplegiaBoth legs and both arms are affected, but the legs are significantly more affected than the arms. Children with diplegia usually have some clumsiness with their hand movements. HemiplegiaThe leg and arm on one side of the body are affected.QuadriplegiaBoth arms and legs are affected. The muscles of the trunk, face and mouth can also be affected. 
  • #38 to establish locomotion, communication and self-help, gain optimal appearance and integration of motor functions; correct associated defects as effectively as possible and provide educational opportunities based on the individual’s needs and capabilities
  • #46 Physical Therapy - helps strengthen muscles
  • #47 Physical Therapy - helps strengthen muscles