This document discusses cleft lip and palate, including their development, classification, causes, problems they can create, and methods of surgical repair. Cleft lip and palate are congenital abnormalities caused by a failure of fusion during development of the lip and palate in utero. Surgical repair aims to restore function and appearance, with cleft lip repaired as early as 3 months and cleft palate typically repaired at 18 months. Repair requires a team approach and may involve additional procedures over the patient's lifetime.
2. Cleft lip and Palate
Cleft Lip and Palate are congenital abnormal gaps in the upper
lip, alveolus or palate
Cleft lip occurs due to defect in fusion of medial nasal process
with maxillary process
Cleft palate is due to failure of fusion of palatal processes of
maxilla
3. Development of lip and palate
5th week of intrauterine life following features are developing in the
area of face
Frontonasal process
Medial nasal process
Lateral nasal process
The medial nasal processes fuse
with one another and with
maxillary process to form the upper
lip and premaxilla(primary palate)
Mandibular process fuse in the
midline to form lower lip
The palatal shelves grow medially
from maxillary process and fuse in
the midline to form hard &
soft palate(secondary palate)
4.
5. Development of palate
Primary palate : the triangular part of hard palate
anterior to incisor foramen which originate from the
premaxilla ( frontonasal prominences)
Secondary palate : remaining part of the hard palate
and all soft palate posterior to incisive foramen which
comes from palatine shelves of the maxillary
prominences
6. Cleft lip and palate
Incidence
In 75% of cases it is unilateral: common on left side
In 50% of cases it is combined cleft lip and palate
occurring in 1:600 live births. Common in boys
In 15-25% of cases it is cleft lip alone
In 25-40% of cases it is cleft palate alone occurring in
1:1000 live births. Common in girls
7. Cleft lip and palate-Aetiology
Environmental factors
Vitamin B6 deficiency
Radiation exposure
Drugs(steroids, phenytoin)
Genetic factors
If parents are affected with cleft, risk to first child is 4% and
in second child the risk increases to 17%
Associated anomalies
Anomalies involving heart, skull, nervous system and
extremities
8. Classification-LAHSHAL
L = Lip (right)
A = Alveolus (right)
H = Hard Palate (right)
S = Soft Palate (median)
H = Hard Palate (left)
A = Alveolus (left)
L = Lip (left)
Capital letter = complete cleft
Lowercase letter = incomplete cleft
“.” or “-” = normal
Examples
LA….l = complete right cleft lip and alveolus,
incomplete left cleft lip
LAHS = complete right unilateral cleft lip,
alveolus, hard, and soft palate
9. Classification
I. Cleft lip alone
Unilateral
Bilateral
Median
II. Cleft of primary palate
Complete(absence of pre-maxilla)
Incomplete( rudimentary pre-maxilla)
Unilateral
Bilateral
Median
III. Cleft of secondary palate
Complete(nasal septum and vomer are separated from palatine
process
Incomplete
Submucous
It can be cleft with or without soft palate involvement
IV. Cleft of both primary and secondary palates
V. Cleft lip and cleft palate together
10. Cleft lip and palate
Problems
Cleft lip
Cosmetic
Psychological secondary to cosmetic appearance
Cleft palate
Defective speech
Nasal regurgitation of food
Abnormal facial growth
Abnormal dentition
Hearing problems due to improper opening and closure of
Eustachian tube.
11. Aims of surgical repair
Cleft lip
To give cosmetically acceptable face
Cleft palate
To provide intact roof to the mouth and a mobile soft
competent palate helping in phonation and swallowing
To give well aligned teeth and avoiding loss of hearing
12. Timing of surgical repair
Cleft lip
As early as possible, usually at 3months of age(rule of 10)
10 weeks of age
10 pounds of weight
10gm% of haemoglobin
Cleft palate
Repair is delayed, usually done at 1½ years of age
The problem of nasal regurgitation is tackled by spoon
feeding or by bottle feeding that has long nipple with a big
hole
13. Cleft lip repair
Accurate repair of skin, muscles and mucous membrane
Maintaining of white line and ‘cupid's bow’
To give a long zigzag scar that doesn’t contract to produce
notching
Techniques
Millard technique
14. Cleft palate repair
Pairing the edges of cleft
Raising the mucoperiosteal flaps on either side of cleft
Relaxation incisions on lateral sides to help medial
movement of flaps
Soft palate muscles are dissected from bony edge of the
posterior hard palate, realigned transversely and sutured
Nasal mucosal lining is sutured
Oral mucosal lining is sutured
15. Cleft lip repair
Cleft Lip Repair
Unilateral
rotation-advancement flap developed
by Millard
Complications
Dehiscence
infection
excess tension
17. Cleft lip and palate repair
The overall management of cleft lip and palate requires a
team approach
In cleft palate patients, speech therapy is required after
surgery
Hearing problems require ENT specialist and dental
problems of occlusion require care by orthodontic surgeon
In many cases secondary operations are required during
later life to improve appearance and functions