Aural atresia is a birth defect affecting 1 in 10,000 births where the external ear canal is malformed or absent. It can occur unilaterally or bilaterally. Various surgical techniques have been developed over 70 years to reconstruct the ear canal and restore hearing. Modern techniques involve drilling away atretic bone, freeing the ossicles, placing grafts, and skin grafting without opening the mastoid bone to reduce complications. Outcomes are better for unilateral cases, while bilateral cases may use hearing aids until at least one ear can be reconstructed surgically. Careful patient selection and meticulous surgery can successfully restore hearing in many cases of aural atresia.