Laryngomalacia is the most common congenital larynx anomaly characterized by partial or complete collapse of the supraglottic structures during inspiration. It is caused by an immature or underdeveloped larynx with floppy tissues. Symptoms may include noisy breathing, difficulty feeding, or more severe cases, cyanosis or apnea. Treatment involves surgical aryepiglottoplasty to divide and remove redundant tissues to widen the airway. Laryngomalacia usually resolves on its own by age 1-2 years as the larynx develops and matures.

1. Congenital disorders of the
Larynx
LARYNGOMALACIA
BY : DR RIZWAN AHMED
[MD PEDIATRICS]

2. PART 1 ―LARYNGOMALACIA

3. WHAT IS LARYNGOMALACIA?
 Most common congenital anomaly of the larynx
 -characterized by partial or complete collapse of the
supraglottic structures on inspiration.
 Laryngo malacia is a congenital softening of the
tissues of the larynx above the vocal cords. This
is the most common cause of
noisy breathing in infancy. The laryngeal structure is
malformed and floppy, causing the tissues to fall
over the airway opening and partially block it.

4. LARYNGOMALACIA..
 Etiology: Unkown
• Theories:
• 1)GERD (gastroesophageal reflux disease)
• 2) Immature neuromuscular control
 Epiglottis is derived from the 3rd and 4th branchial
arches. Overgrowth of the 3rd results in elongation of
the structure and the observed laryngomalacia

5. Congenital disorders of the Larynx
Organogenesis
At birth the larynx is located high in the larynx between
levels C1- C4
By age 2 the larynx begins to descend inferiorly
By age 6 the larynx reaches the adult position between
levels C4 through C7

7. CONGENITAL DISORDERS OF THE LARYNX
EMBRYOGNESIS :
 The larynx develops from the endodermal lining
and the adjacent mesenchyme of the foregut
between the fourth and sixth branchial arches.
 At 20 days' gestation, the foregut is first identifiable
with a ventral laryngotracheal groove
 The laryngotracheal groove continues to deepen
until its lateral edges fuse. By day 26, this tube
descends caudally, where the trachea becomes
separated from the esophagus by the
tracheoesophageal septum with a persistent slitlike
opening into the pharynx.

9. CLINICAL DIAGNOSIS:
 It is considered a benign, transient cause of
inspiratory stridor and is characterized by collapse
of arytenoids, epiglottis and aryepiglottic folds
during the inspiratory phase.
 . The clinical diagnosis comprises of identifying
three anatomic abnormalities
 (1) flaccid epiglottis prolapsing
 backwards during inspiration;
 (2) poorly supported arytenoids that prolapse
forward during inspiration;
 (3) short aryepiglottic folds.

10. NORMAL VS LARYNGO MALACIAC VIEW

11. CAUSES:
 It can be due to the relaxation or a lack of muscle tone in
the upper airway.
 Insufficient or delayed calcium deposition
 The part of the nervous system that gives tone to the
airway is most likely underdeveloped.
 Gastroesophageal reflux (GER) may play an etiological
role in laryngomalacia
 Immature neuromuscular control may be responsible for
the arytenoid prolapse observed in laryngomalacia

12. TYPES:
 Type I: Inward collapse of aryepiglottic folds
 Type II: Long tubular epiglottis infolding on itself (Omega
shaped)
 Type III: Anterior and medial collapse of corniculate and
cuneiform cartilages
 Type IV: Posterior displacement of epiglottis against
posterior pharyngeal wall or inferior collapse towards
vocal folds
 Type V: Short aryepiglottic folds

18. DEGREE OF LARYNGOMALACIA
 Laryngomalacia can be mild, moderate or severe. 99%
of infants with laryngomalacia have mild or moderate
laryngomalacia.
 Mild laryngomalacia:
 noisy breathing or inspiratory stridor.
 no significant airway obstruction, feeding difficulties or
other symptoms associated with laryngomalacia.
 The noisy breathing is annoying to caregivers, but does
not cause other health care problems.
 Infants with mild laryngomalacia usually outgrow the
stridor by 12 – 18 months of age

19. MODERATE LARYNGOMALACIA
 noisy breathing or inspiratory stridor
 Feeding difficulties without poor weight gain
 (vomiting or spitting up)
 Choking on food
 Gastroesophageal reflux)
 Mild to moderate chest and/or neck retractions
(chest and/or neck sinking in with breathing), but no
severe distres

20. SEVERE LARYNGOMALACIA
 Feeding difficulties with poor weight gain
 (chest and/or neck sinking in with breathing)
 Significant cyanosis (turning blue)
 Life threatening apnea (pauses in breathing)
 Heart or lung problems from chronic oxygen
deprivation (low oxygen)
 Airway symptoms severe enough to cause multiple
visits to an emergency department or hospital
 Only 1% of infants with laryngomalacia have severe
laryngomalacia. Infants with severe laryngomalacia
usually need surgery.

21. SYMPTOMS

22.  Noisy breathing (stridor) — An audible wheeze when the baby
inhales . It is often worse when the baby is agitated, feeding,
crying or sleeping on his back.
 High pitched sound
 Difficulty feeding
 Poor weight gain
 Choking while feeding
 Apnea
 Pulling in neck and chest with each breath
 Cyanosis
 Gastro esophageal reflux (vomiting and regurgitation)
 Aspiration

24. TREATMENT
 Surgical management
 -Restoration of an adequate airway can be achieved
 by performing an endoscopic aryepiglottoplasty (sometimes
 termed a supraglottoplasty; Jani et al. 1991).
 Supraglottoplasty
 1) Using cup forceps and microscissors (or alternatively the
carbon dioxide laser), each aryepiglottic fold is first divided to
release it from the edge of the epiglottis,
 2) the redundant mucosa and submucosal tissue are then
excised from over the arytenoids, together if necessary with
part or all of the cuneiform cartilages. The stridor is usually
improved immediately following