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SINDROMUL CHILAIDITI
Felicia Marilena Macovei
Medic rezident Medicina Interna
CUPRINS:
 Definitie
 Etimologie
 Incidenta
 Etiologie
 Simptomatologie
 Diagnostic
 Diagnostic diferential
 Complicatii
 Tratament
 Bibliografie
DEFINITIE
Este o afectiune rara, data de interpozitia
unui segment al intestinului gros sau
subtire intre diafragm si ficat.
Asimptomatic = Semnul Chilaiditi
Asociat cu alte semne = Sindrom
Chilaiditi
ETIMOLOGIE
Dupa numele radiologului grec Dimítrios
Chilaiditi / Kilalditi, nascut in 1883.
Prima data sindromul a fost descris in
1910 cand acesta lucra la Viena.
Semnul ii poarta numele, iar alti medici
pe parcurs i-au adaugat alte semne,
transformandu-l in sindrom.
INCIDENTA
0.025 pana la 0.28% in populatia
generala
Sex masculin mai frecvent decat sex
feminin
ETIOLOGIE
Absenta, laxitate sau elongatia ligamentelor
suspensoare ale colonului transvers sau ale
ligamentului falciform; malpozitii
congenitale.
Tulburari functionale: constipatie cronica,
aerofagie; paralizie diafragmatică, boli
cronice pulmonare; ciroza; obezitate,
multiparitate, ascita.
Retard mintal si schizofrenie
SIMPTOMATOLOGIE
Semnul Chilaiditi = Asimptomatic
Sindrom Chilaiditi = cele mai frecvente
manifestari sunt gastro-intestinale (dureri
abdominale, greață, vărsături,
constipație, inapetenta, distensie
abdominala).
DIAGNOSTIC
Radiografie: prezenta de aer sub
hemidiafragmul drept
Criterii:
- Hemidiafragmul drept ridicat de catre
intestin
- Intestinul destins de aer
- Prezenta haustratiilor intestinale
http://www.radrounds.com/photo/the-chilaiditis-sign
Case courtesy of Maen K H, Radiopaedia.org
Case courtesy of Maen K H, Radiopaedia.org
Case courtesy of Maen K H, Radiopaedia.org
Ecografie abdominala: aer in spatiul
hepatodiafragmatic sau suprapus peste
ficat
Computer tomografie: mai rar utilizata,
confirma prezenta aerului intraluminal
http://www.learningradiology.com/archives05
DIAGNOSTIC DIFERENTIAL
Principalele patologii sunt
pneumoperitoneul si abcesul subfrenic:
- Absenta haustratiilor colonului
- Localizarea aerului nu se modifica la
schimbarea pozitiei pacientului
Hernii diafragmatice, ocluzii intestinale,
volvulus, sau diverticulita, apendicita.
Case courtesy of Maen K H, Radiopaedia.org
Case courtesy of Maen K H, Radiopaedia.org
COMPLICATII
Cele mai frecvente: volvulus cecal, al
flexurii splenice sau al colonului
transvers;
Rar: perforatii ale cecului, apendicita
perforata subdiafragmatica; obstructie
intestinala sau pseudo-obstructie
colonica
Este asociat cu patologii maligne
pulmonare si gastrointestinale
TRATAMENT
Asimptomatic - tratament conservator:
repaus la pat, hidratare intravenoasa,
decompresie intestinala , laxative si
clisme.
Tratament ineficient, complicatii –
interventii chirurgicale de obstruare a
spatiului subfrenic drept.
BIBLIOGRAFIE
 Moaven O, Hodin RA. "Chilaiditi Syndrome: A Rare Entity with Important Differential
Diagnoses". Gastroenterol Hepatol (N Y) 8(4): 276–278. April 2012
 Cedrick, Sangwa Milindi et al. "Syndrome de Chilaiditi Chez Un Nouveau-Né, À Propos
D’un Cas." The Pan African Medical Journal 19 (2014): 239.
 WENG, WEI-HONG et al. “Colonic Interposition between the Liver and Left Diaphragm -
Management of Chilaiditi Syndrome: A Case Report and Literature Review.” Oncology
Letters 7.5 (2014): 1657–1660.
 Keles S, Artac H, Reisli I, Alp H, Koc O "Chilaiditi syndrome as a cause of respiratory
distress". Eur. J. Pediatr. 165 (6): 367–9. June 2006.
 Belkouch A, Htit A, Belyamani L, Zidouh S. "Dyspnoea caused by a Chilaiditi syndrome:
contribution of the non-invasive ventilation“. BMJ Case Rep. August 2013
(2013):756590.
 Sato M, Ishida H et al. "Chilaiditi syndrome: sonographic findings.“ Abdom Imaging.
2000 Jul-Aug;25(4):397-9.
 Walsh SD, Cruikshank JG. "Chilaiditi syndrome". Age Ageing 6 (1): 51–7. February 1977
 Kang, David et al. “Acute Abdominal Pain Secondary to Chilaiditi Syndrome.” Case
Reports in Surgery 2013. Web. 25 June 2015.
 https://en.wikipedia.org/wiki/Chilaiditi_syndrome
 http://radiopaedia.org/articles/chilaiditi-syndrome

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Sindromul Chilaiditi

  • 1. SINDROMUL CHILAIDITI Felicia Marilena Macovei Medic rezident Medicina Interna
  • 2. CUPRINS:  Definitie  Etimologie  Incidenta  Etiologie  Simptomatologie  Diagnostic  Diagnostic diferential  Complicatii  Tratament  Bibliografie
  • 3. DEFINITIE Este o afectiune rara, data de interpozitia unui segment al intestinului gros sau subtire intre diafragm si ficat. Asimptomatic = Semnul Chilaiditi Asociat cu alte semne = Sindrom Chilaiditi
  • 4. ETIMOLOGIE Dupa numele radiologului grec Dimítrios Chilaiditi / Kilalditi, nascut in 1883. Prima data sindromul a fost descris in 1910 cand acesta lucra la Viena. Semnul ii poarta numele, iar alti medici pe parcurs i-au adaugat alte semne, transformandu-l in sindrom.
  • 5. INCIDENTA 0.025 pana la 0.28% in populatia generala Sex masculin mai frecvent decat sex feminin
  • 6. ETIOLOGIE Absenta, laxitate sau elongatia ligamentelor suspensoare ale colonului transvers sau ale ligamentului falciform; malpozitii congenitale. Tulburari functionale: constipatie cronica, aerofagie; paralizie diafragmatică, boli cronice pulmonare; ciroza; obezitate, multiparitate, ascita. Retard mintal si schizofrenie
  • 7. SIMPTOMATOLOGIE Semnul Chilaiditi = Asimptomatic Sindrom Chilaiditi = cele mai frecvente manifestari sunt gastro-intestinale (dureri abdominale, greață, vărsături, constipație, inapetenta, distensie abdominala).
  • 8.
  • 9.
  • 10.
  • 11.
  • 12.
  • 13. DIAGNOSTIC Radiografie: prezenta de aer sub hemidiafragmul drept Criterii: - Hemidiafragmul drept ridicat de catre intestin - Intestinul destins de aer - Prezenta haustratiilor intestinale
  • 15. Case courtesy of Maen K H, Radiopaedia.org
  • 16. Case courtesy of Maen K H, Radiopaedia.org
  • 17. Case courtesy of Maen K H, Radiopaedia.org
  • 18. Ecografie abdominala: aer in spatiul hepatodiafragmatic sau suprapus peste ficat
  • 19. Computer tomografie: mai rar utilizata, confirma prezenta aerului intraluminal http://www.learningradiology.com/archives05
  • 20. DIAGNOSTIC DIFERENTIAL Principalele patologii sunt pneumoperitoneul si abcesul subfrenic: - Absenta haustratiilor colonului - Localizarea aerului nu se modifica la schimbarea pozitiei pacientului Hernii diafragmatice, ocluzii intestinale, volvulus, sau diverticulita, apendicita.
  • 21. Case courtesy of Maen K H, Radiopaedia.org
  • 22. Case courtesy of Maen K H, Radiopaedia.org
  • 23. COMPLICATII Cele mai frecvente: volvulus cecal, al flexurii splenice sau al colonului transvers; Rar: perforatii ale cecului, apendicita perforata subdiafragmatica; obstructie intestinala sau pseudo-obstructie colonica Este asociat cu patologii maligne pulmonare si gastrointestinale
  • 24. TRATAMENT Asimptomatic - tratament conservator: repaus la pat, hidratare intravenoasa, decompresie intestinala , laxative si clisme. Tratament ineficient, complicatii – interventii chirurgicale de obstruare a spatiului subfrenic drept.
  • 25. BIBLIOGRAFIE  Moaven O, Hodin RA. "Chilaiditi Syndrome: A Rare Entity with Important Differential Diagnoses". Gastroenterol Hepatol (N Y) 8(4): 276–278. April 2012  Cedrick, Sangwa Milindi et al. "Syndrome de Chilaiditi Chez Un Nouveau-Né, À Propos D’un Cas." The Pan African Medical Journal 19 (2014): 239.  WENG, WEI-HONG et al. “Colonic Interposition between the Liver and Left Diaphragm - Management of Chilaiditi Syndrome: A Case Report and Literature Review.” Oncology Letters 7.5 (2014): 1657–1660.  Keles S, Artac H, Reisli I, Alp H, Koc O "Chilaiditi syndrome as a cause of respiratory distress". Eur. J. Pediatr. 165 (6): 367–9. June 2006.  Belkouch A, Htit A, Belyamani L, Zidouh S. "Dyspnoea caused by a Chilaiditi syndrome: contribution of the non-invasive ventilation“. BMJ Case Rep. August 2013 (2013):756590.  Sato M, Ishida H et al. "Chilaiditi syndrome: sonographic findings.“ Abdom Imaging. 2000 Jul-Aug;25(4):397-9.  Walsh SD, Cruikshank JG. "Chilaiditi syndrome". Age Ageing 6 (1): 51–7. February 1977  Kang, David et al. “Acute Abdominal Pain Secondary to Chilaiditi Syndrome.” Case Reports in Surgery 2013. Web. 25 June 2015.  https://en.wikipedia.org/wiki/Chilaiditi_syndrome  http://radiopaedia.org/articles/chilaiditi-syndrome