This document discusses IgG4-related kidney disease (IgG4-RKD). It first provides a brief overview of IgG4-related disease and describes its clinical features, pathogenesis, laboratory features, imaging features, and pathological features of IgG4-RKD. Key points include that IgG4-RKD mainly affects middle-aged to elderly men and involves a lymphoplasmacytic infiltrate with increased IgG4-positive plasma cells and fibrosis in the kidneys. Diagnosis is based on clinical, serological, radiological, and pathological criteria. Treatment involves steroids and rituximab.