This document discusses disorders of sex development and management of congenital adrenal hyperplasia. It defines disorders of sex development as conditions where chromosomal, gonadal or anatomical sex development is atypical. It describes the process of sexual differentiation and defines congenital adrenal hyperplasia. It outlines signs that should prompt suspicion of a disorder of sex development in neonates or infants. It discusses the history, physical exam findings, investigations and management of congenital adrenal hyperplasia, including treatment with glucocorticoids and mineralocorticoids.