Woman 33yo, with history onset one year ago, fever and some red macula appeared at abdominal skin that biopsy result of macula was lipoma. But it is not in stop of progress, a lot of red macula were getting more over 2 legs and upper arms to her right face.

1. CASE 430: FACIAL EDEMA, Dr PHAN THANH HAI, Dr LE
NGOC VINH [MEDIC CA MAU], MEDIC MEDICAL CENTER,
HCMC, VIETNAM
Woman 33yo, from Ca mau province, with history onset one year ago, fever
and some red macula appeared at abdominal skin that biopsy result of macula
was lipoma. But it is not in stop of progress, a lot of red macula were getting
more over 2 legs and upper arms to her right face.
In palpation, red macula is hot and induration (Photo1,2.3).
Ultrasound scanning of her right face represents edema of subcutaneous fatty
layer, no hypervascular.

2. CT scan of the face shows normal bone and subcutaneous edema of her right
hemifacial side.

3. MRI also detected facial edema of subcutaneous fatty tissue (MRI 1,2).
Blood tests= pancytopenia, negative ANA test and anti-dsdna, very high ferritin
>2,000, LDH =2,581 UI, beta2 microglobulin= 3,701, CRP = 64 ng/mL, c3 =122
(normal), c4= 66 (n: 15-450), kappa and lambda not detectable.
What is your suggestion for diagnosis of this hemifacial edema case?