Taurodontism is a condition where the body of the tooth is enlarged at the expense of the root, resulting in an elongated tooth body and short roots. It is caused by a failure of the epithelial root sheath to invaginate properly during tooth development. Taurodontism can range from mild to severe and may affect deciduous or permanent molars either unilaterally or bilaterally. Radiographically, there is an extremely large pulp chamber that extends into the elongated tooth body and short, wide roots. Diagnosis is based on the characteristic rectangular tooth crown and large pulp chamber seen clinically or radiographically. No treatment is needed as taurodontism does not typically cause clinical problems.
Dentin dysplasia (DD) is a rare hereditary disturbance is inherited as an autosomal dominant trait.
unknown etiology that affects approximately 1 :100,000.
In 1972, Witkop classified it into type I and type II which affect both dentitions.DD Type I
Radicular dentin dysplasia
Characterized by:-
1.Both dentitions are affected.
2.Normal appearing crowns
3.No or only rudimentary root development (rootless teeth)
4.Incomplete or total obliteration of the pulp chamber.
5.Teeth may exhibit extreme mobility and exfoliate prematurely.DD type II
coronal dentin dysplasia
Characterized by:-
1.partial pulpal obliteration.
2.Thistle-tube-or flame-shaped coronal pulp chambers
3. Thread-like root canals
4. Usually the absence of periapical radiolucencies.
5. In this type of anomaly, teeth roots are of normal shape and contour.The enamel and the immediately subjacent dentin appear normal.
Deeper layers of dentin show an atypical tubular pattern with an amorphous, atubular area, and irregular organization.
Normal dentinal tubule formation appears to have been blocked so that new dentine forms around obstacles and takes on the characteristic appearances described as “lava flowing around boulders”The radiograph revealed features of dentine dysplasia type I with normal appearance of crown but no root development Autosomal Dominant Disorder:
Manifested in heterozygous states
At least one parent of index case is usually affected
Both males and females are affected.
Clinical feature can be modified by variation in penetrance and expressivity. Some individual inherit the mutant gene but are phenotpically normal. This is reffered to as “incomplete penetrance”.
In many condition the age of onset is delayed.
Inheritance Pattern:
Typical pattern is a heterozygous affected parent with a homozygous unaffected parent.
Every child has one chance in two of having the disease
Both sexes are affected equally..Autosomal Recessive Disorder
Largest category of Mendelian disorder
Usually does not affect the parent of the affected individual, but sibling may show the disease.
Complete penetrance is common.
Onset is frequently early in life.
Usually affect enzymatic proteins.
Pattern Of Inheritance:
Typical pattern is two heterozygous unaffected (carrier) parent.
The triat does not usually affect the parent, but siblings may show the disease
Siblings have one chance in four of being affected
Both sexes affected equally.
Taurodontism is characterized by teeth with enlarged and elongated pulp chambers and apical displacement of the bifurcation or trifurcation of roots. This anomaly occurs either as an isolated, singular trait or in association with syndromes and with some ectodermal anomalies. The aim of this review is to address the etiology, radiographic features and clinical considerations in the treatment of such teeth. It can be seen that taurodontism has until now received insufficient attention from clinicians.
Dentin dysplasia (DD) is a rare hereditary disturbance is inherited as an autosomal dominant trait.
unknown etiology that affects approximately 1 :100,000.
In 1972, Witkop classified it into type I and type II which affect both dentitions.DD Type I
Radicular dentin dysplasia
Characterized by:-
1.Both dentitions are affected.
2.Normal appearing crowns
3.No or only rudimentary root development (rootless teeth)
4.Incomplete or total obliteration of the pulp chamber.
5.Teeth may exhibit extreme mobility and exfoliate prematurely.DD type II
coronal dentin dysplasia
Characterized by:-
1.partial pulpal obliteration.
2.Thistle-tube-or flame-shaped coronal pulp chambers
3. Thread-like root canals
4. Usually the absence of periapical radiolucencies.
5. In this type of anomaly, teeth roots are of normal shape and contour.The enamel and the immediately subjacent dentin appear normal.
Deeper layers of dentin show an atypical tubular pattern with an amorphous, atubular area, and irregular organization.
Normal dentinal tubule formation appears to have been blocked so that new dentine forms around obstacles and takes on the characteristic appearances described as “lava flowing around boulders”The radiograph revealed features of dentine dysplasia type I with normal appearance of crown but no root development Autosomal Dominant Disorder:
Manifested in heterozygous states
At least one parent of index case is usually affected
Both males and females are affected.
Clinical feature can be modified by variation in penetrance and expressivity. Some individual inherit the mutant gene but are phenotpically normal. This is reffered to as “incomplete penetrance”.
In many condition the age of onset is delayed.
Inheritance Pattern:
Typical pattern is a heterozygous affected parent with a homozygous unaffected parent.
Every child has one chance in two of having the disease
Both sexes are affected equally..Autosomal Recessive Disorder
Largest category of Mendelian disorder
Usually does not affect the parent of the affected individual, but sibling may show the disease.
Complete penetrance is common.
Onset is frequently early in life.
Usually affect enzymatic proteins.
Pattern Of Inheritance:
Typical pattern is two heterozygous unaffected (carrier) parent.
The triat does not usually affect the parent, but siblings may show the disease
Siblings have one chance in four of being affected
Both sexes affected equally.
Taurodontism is characterized by teeth with enlarged and elongated pulp chambers and apical displacement of the bifurcation or trifurcation of roots. This anomaly occurs either as an isolated, singular trait or in association with syndromes and with some ectodermal anomalies. The aim of this review is to address the etiology, radiographic features and clinical considerations in the treatment of such teeth. It can be seen that taurodontism has until now received insufficient attention from clinicians.
developmental disturbances of teeth
DEVELOPMENTAL DISTURBANCES IN NUMBER OF TEETH
DEVELOPMENTAL DISTURBANCES IN SIZE OF TEETH
DEVELOPMENTAL DISTURBANCES IN SHAPE OF TEETH
Anodontia
Supernumerary teeth
Predeciduous dentition
Post permanent dentition
Microdontia
Macrodontia
Gemination
Fusion
Concrescence
Dilaceration
Talon cusp
Taurodontism
Supernumerary roots
Characteristics and features of developmental, hereditary and congenital disorders affecting the teeth and other hard tissues. Genetic concepts of development and role of teratogens on developing tissues,
Anomalies of tooth formation and eruption, MISSING TEETH, EXTRA TEETH, ABNORMALITY OF TOOTH SIZE, Crown size, Root size, Abnormality of crown form, ABNORMALITY OF ROOT FORM, All tissues, Cementum defects, Dentine defects, enamel defects, DISTURBANCES OF ERUPTION & EXFOLIATION,
2. General information
• Body of tooth is enlarged at the expense of
root
• characterised by clinical and anatomical
Crown of normal shape and size, an elongated
body and short roots with longitudinally
enlarged pulp Chambers
• Taurodont means resembles that of cud
chewing animal
3. Aetiology
• It is caused by genetically determined trait
• it occurs due to failure of Hertwig's epithelial
root sheath to invaginate at proper horizontal
level
• resulting from odontoblastic deficiency during
dentinogenesis of the root
4. Classification
• Hypotaurodont – it is milder form of
Taurodont and it represents slightly apical and
displacement of pulpal floor
• mesioTaurodont – moderate form and pulpal
floor displacement is about midline of the
root of teeth
• Hypertaurodont – severe form and apical
displacement of pulpal floor is present at the
apex
5. Clinical features
• May affect either deciduous or permanent
dentition and teeth involved are invariably molars
• may be unilateral or bilateral or may exhibit any
combination of quadrant involvement
• rectangular shape rather than the normal
tapering towards root
• associated with certain dermatological conditions
like epidermolysis bullosa, otodental dysplasia
and dyskeratosis congenita
6. Radiographic features
• Pulp chamber is extremely large with much
greater apicoocclusal height than normal
• extension of rectangular pulp chamber occur
into elongated body of the tooth
• the root and root canals are exceedingly short.
Increased dimension between
cementoenamel junction and furcation
