CONGENITAL LATERAL CEREBRAL
     VENTRICULOMEGALY
 FETAL SONOGRAM ASSESMENT




                 FREE LANCE RADIOLOGY
                    CONTINUATION OF
                   EDUCATION IN BASIC
                 DIAGNOSTIC RADIOLOGY
FETAL CEREBRAL LATERAL
        VENTRICULOMEGALY AN OVERVIEW
• Ventriculomegaly : 0.3 to 0.5/
  1000 births .
• Frank hydrocephalus is
  synonymous to overt lateral
  ventriculomegaly
• Ventricles have three dimensional
  architecture &Variable degree of
  enlargement is appreciated in
  different trimesters
• Initially assessment was done
  with
    – RATIO OF
            – MIDLINE to LATERAL WALL OF
                                           Case of fetal cerebral Lateral
              THE VENTRICLE
              MIDLINE TO IPSILATTERAL           ventriculomegaly .
              CALVARIUM
                                            Both the lateral ventricles
                                             show significant and near
                                              symmetrical dilatation.
MILD LATERAL CEREBRAL
           VENTRICULOMEGALY
• Mild lateral cerebral ventriculomegaly ( 10 to 15 mm )
• Isolated ventriculomegaly ( No consequence) . It could
  be earliest manifestation of brain damage .
• CNS and NON CNS anomalies may be associated with
  it .
   – Primary cerebral maldevelopment ( obstructive
     hydrocephalus )
   – Agyria
   – Destructive lesions
   – Periventricular leukomalacia
   – Hypoxia
MILD LATERAL CEREBRAL
                VENTRICULOMEGALY
• NRA : NEAR CALVARIUM REVERBATION
  ARTEFACT LIMITS THE SONIC WINDOW
  HENCE
   – Transverse diameter of the
      ventricular atrium is taken at level
      of glomus of choroid .
   – Measurement is taken in the axial
      plane along the atrium distal to
      transducer . Inside echoes are
      measured
• Values are
    – Mid trimester ( 6 to 7mm +_ 1mm) .
    – 14 to 40 wks ( 7mm +_ 1mm) .
• Some degree of asymmetry in either side
  ventricles is noted .
• Male fetus have larger measurements than
  the female ones.
MILD LATERAL CEREBRAL
                 VENTRICULOMEGALY
• Mild lateral cerebral ventriculomegaly
  ( 10 to 15mm inclusive).
• If unilateral - benign.
•   Consider
     – Fetal MRI
     – Fetal ECG .
     – Fetal corpus callosum assessment
     – Fetal karyotyping.
     – First trimester screening.
•   To note :
     – X linked variety of hydrocephalus develops in
       lateral gestation.
•   Caesarean section may have to be opted due to
    associated macrocrania.
•   Cephalocentesis /Ventriculoamniotic shunting
    are also options
OVERT LATERAL CEREBRAL
            VENTRICULOMEGALY
• Overt cerebral lateral ventriculomegaly
  or hydrocephalus .
   – Atrial width >15mm
   – ( 2 to third trimester) .
   – Associations
       • Neural tube defects .
       • Mid line anomalies .
       • Either aqueductal stenosis / communicating
         hydrocephalus .
• Dangling choroid sign ( choroid away
  from transducer touches the ventricular
  wall and one near to the choroid abuts
  the interventricular septum ) .
CONSIDER

FETAL MRI

FETAL ECG

KARYOTYPING

ASSESS FETAL
CORPUS CALLOSUM




                  UNILATERAL FETAL
                  VENTRICULOMEGALY
                  USUALLY BENIGN
MEASURES THE
AXIAL IMAGE OF THE
VENTRICLE AWAY
FROM THE
TRANSDUCER AT THE
LEVEL OF GLOMUS OF
CHOROID.



AVOID
MEASUREMENT OF
THE VENTRICLE
NEAR TO THE
TRANSDUCER DUE TO
NRA : NEAR
CALVARIUM
REVERBATION
ARTEFACT
                     UNILATERAL FETAL CEREBRAL
                     VENTRICULOMEGALY.
ASSESEMENT OF
CORPUS CALLOSUM
SHOULD BE DONE

3D / 4D IMAGING IS
OF HELP .




                     NORMAL CORPUS CALLOSUM IN
                     CASE OF UNILATERAL
                     VENTRICULOMEGALY ( USUALLY
                     BENIGN)
DANGLING CHOROID
SIGN

CHOROID PLEXUS OF
THE VENTRICLE
AWAY FROM THE
TRANSDUCER ABUTS
THE LATERAL
VENTRICULAR WALL
AND OTHER CHOROID
PLEXUS ABUTS THE
SEPTUM.




                    DANGLING CHOROID SIGN IN
                    CASE OF BILATERAL FETAL
                    VENTRICULOMEGALY
SMALL POSTERIOR
FOSSA

DILATED CENTRAL
CANAL

POSSIBLE ARNOLD
CHIARI
MALFORMATION IN
CASE OF
VENTRICULOMEGALY.

FETAL MR CAN BE OF
HELP.




                     CNS ANOMALIES ASSOCIATED
                     WITH VENTRICULOMEGALY

Congenital lateral ventriculomegaly.

  • 1.
    CONGENITAL LATERAL CEREBRAL VENTRICULOMEGALY FETAL SONOGRAM ASSESMENT FREE LANCE RADIOLOGY CONTINUATION OF EDUCATION IN BASIC DIAGNOSTIC RADIOLOGY
  • 2.
    FETAL CEREBRAL LATERAL VENTRICULOMEGALY AN OVERVIEW • Ventriculomegaly : 0.3 to 0.5/ 1000 births . • Frank hydrocephalus is synonymous to overt lateral ventriculomegaly • Ventricles have three dimensional architecture &Variable degree of enlargement is appreciated in different trimesters • Initially assessment was done with – RATIO OF – MIDLINE to LATERAL WALL OF Case of fetal cerebral Lateral THE VENTRICLE MIDLINE TO IPSILATTERAL ventriculomegaly . CALVARIUM Both the lateral ventricles show significant and near symmetrical dilatation.
  • 3.
    MILD LATERAL CEREBRAL VENTRICULOMEGALY • Mild lateral cerebral ventriculomegaly ( 10 to 15 mm ) • Isolated ventriculomegaly ( No consequence) . It could be earliest manifestation of brain damage . • CNS and NON CNS anomalies may be associated with it . – Primary cerebral maldevelopment ( obstructive hydrocephalus ) – Agyria – Destructive lesions – Periventricular leukomalacia – Hypoxia
  • 4.
    MILD LATERAL CEREBRAL VENTRICULOMEGALY • NRA : NEAR CALVARIUM REVERBATION ARTEFACT LIMITS THE SONIC WINDOW HENCE – Transverse diameter of the ventricular atrium is taken at level of glomus of choroid . – Measurement is taken in the axial plane along the atrium distal to transducer . Inside echoes are measured • Values are – Mid trimester ( 6 to 7mm +_ 1mm) . – 14 to 40 wks ( 7mm +_ 1mm) . • Some degree of asymmetry in either side ventricles is noted . • Male fetus have larger measurements than the female ones.
  • 5.
    MILD LATERAL CEREBRAL VENTRICULOMEGALY • Mild lateral cerebral ventriculomegaly ( 10 to 15mm inclusive). • If unilateral - benign. • Consider – Fetal MRI – Fetal ECG . – Fetal corpus callosum assessment – Fetal karyotyping. – First trimester screening. • To note : – X linked variety of hydrocephalus develops in lateral gestation. • Caesarean section may have to be opted due to associated macrocrania. • Cephalocentesis /Ventriculoamniotic shunting are also options
  • 6.
    OVERT LATERAL CEREBRAL VENTRICULOMEGALY • Overt cerebral lateral ventriculomegaly or hydrocephalus . – Atrial width >15mm – ( 2 to third trimester) . – Associations • Neural tube defects . • Mid line anomalies . • Either aqueductal stenosis / communicating hydrocephalus . • Dangling choroid sign ( choroid away from transducer touches the ventricular wall and one near to the choroid abuts the interventricular septum ) .
  • 7.
    CONSIDER FETAL MRI FETAL ECG KARYOTYPING ASSESSFETAL CORPUS CALLOSUM UNILATERAL FETAL VENTRICULOMEGALY USUALLY BENIGN
  • 8.
    MEASURES THE AXIAL IMAGEOF THE VENTRICLE AWAY FROM THE TRANSDUCER AT THE LEVEL OF GLOMUS OF CHOROID. AVOID MEASUREMENT OF THE VENTRICLE NEAR TO THE TRANSDUCER DUE TO NRA : NEAR CALVARIUM REVERBATION ARTEFACT UNILATERAL FETAL CEREBRAL VENTRICULOMEGALY.
  • 9.
    ASSESEMENT OF CORPUS CALLOSUM SHOULDBE DONE 3D / 4D IMAGING IS OF HELP . NORMAL CORPUS CALLOSUM IN CASE OF UNILATERAL VENTRICULOMEGALY ( USUALLY BENIGN)
  • 10.
    DANGLING CHOROID SIGN CHOROID PLEXUSOF THE VENTRICLE AWAY FROM THE TRANSDUCER ABUTS THE LATERAL VENTRICULAR WALL AND OTHER CHOROID PLEXUS ABUTS THE SEPTUM. DANGLING CHOROID SIGN IN CASE OF BILATERAL FETAL VENTRICULOMEGALY
  • 11.
    SMALL POSTERIOR FOSSA DILATED CENTRAL CANAL POSSIBLEARNOLD CHIARI MALFORMATION IN CASE OF VENTRICULOMEGALY. FETAL MR CAN BE OF HELP. CNS ANOMALIES ASSOCIATED WITH VENTRICULOMEGALY