SlideShare a Scribd company logo
CONGENITAL AURAL
ATRESIA
Dr Zeeshan Ali
Resident in
Department of ENT Head and Neck Surgery
CMH Rawalpindi
Case 1
Case detail
Displayed with informed consent of
patient
BERA
CT Scan
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
POSTOPERATIVE CARE
Displayed with informed consent of
patient
Case 2
Case detail
Displayed with informed consent of
patient
Audiometry
CT scan
X ray mastoid
Surgical steps
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Surgery
Displayed with informed consent of
patient
Post operative
Displayed with informed consent of
patient
Post operative
Displayed with informed consent of
patient
CASE DISCUSSION
Epidemiology
 1 in 10,000 to 15,000
births
 10% associated with
syndrome
 Unilateral vs Bilateral
 30% are bilateral
 Atresia : Microtia, 7:1
Embryology
◦ Treacher Collins
syndrome
◦ brachio-otorenal
syndrome
◦ Stickler syndrome
Embryology
◦ Treacher Collins
syndrome
◦ brachio-otorenal
syndrome
◦ Stickler syndrome
◦ Crouzon syndrome
◦ Noonan syndrome
◦ Foetal alcohol syndrome
Embryology
◦ Treacher Collins
syndrome
◦ brachio-otorenal
syndrome
◦ Stickler syndrome
◦ Crouzon syndrome
◦ Noonan syndrome
◦ Foetal alcohol syndrome
◦ Goldenhar’s Syndrome
◦ Hemifacial Microsomia
Embryology
Inner ear, middle ear, and external ear
develop independently
Embryology
‘The better developed the external ear
is, the better developed is the middle
ear’
Development of the Auricle
Embryology (Marx)
Embryology
Embryology
First Branchial Arch-
(Meckel’s)
◦ Malleus
◦ Incus body
 Second Arch (Hyoid)
(Reicherts)
◦ Long process of incus
◦ Stapes suprastructure
 Foot plate from the otic
capsule and 2nd arch
Types of aural atresia
Altman classification
Group 1
 Minor Aplasia-
incomplete
recanalization
Altman classification
Group 2
 Moderate Aplasia-
tympanic bone has
developed but has
failed to recanalize
Altman classification
Group 3
 Severe Aplasia-
complete absence
of the external
canal
De la Cruz Classification
HRCT based
 Mastoid Pneumatization
 Inner ear normality
 Facial nerve
 Footplate
De la Cruz Classification
Minor
Malformations
 Normal mastoid
pneumatization
 Normal oval
window/footplate
 Good facial
nerve–footplate
relationship
 Normal inner ear
De la Cruz Classification
Major
Malformations
 Poor
pneumatization
 Abnormal or
absent oval
window/footplate
 Abnormal course
of facial nerve
 Abnormalities of
inner ear
Grading System (Jahrsdoerfer)
Variable Points
Stapes Present 2
Oval Window Open 1
Facial Nerve 1
Middle Ear Space 1
Mastoid Pneumatization 1
Malleus/Incus Complex 1
Incudostapedial Joint 1
Round Window 1
External Ear Appearance 1
Total Points 10
Prognostic Rating Scale
 10 Excellent
 9 Very good
 8 Good
 7 Fair
 6 Marginal
 ≤5 Poor
de Alarcon A, Jahrsdoerfer RA, Kesser BW. Congenital absence of the oval window: diagnosis, surgery, and audiometric
outcomes. Otol Neurotol. 2008;29:23–28.
Schuknecht’s classification
Type A Type B
Type C Type D
Schuknecht’s classification
Type A Type B
Type C Type D
Schuknecht’s classification
Type A Type B
Type C Type D
Schuknecht’s classification
Type A Type B
Type C Type D
Chiossone’s classification
 Type I - the fossa in
normal position
 Type II - moderately
displaced
Chiossone’s classification
 Type I - the fossa in
normal position
 Type II - moderately
displaced
 Type III - fossa
overlaps the middle
ear
Chiossone’s classification
 Type I - the fossa in
normal position
 Type II - moderately
displaced
 Type III - fossa
overlaps the middle
ear
 Type IV - lack of
mastoid
pneumatization
Initial evaluation
Management
Management
Prerequisite for surgery
 CT scan
 Audiometry
Urgent surgery
 Congenital cholesteatoma
 Draining postoperative atretic ear
 Acute facial palsy
Timing of surgery
 6 year recommended
 Exostosis formation
 Less patient cooperation
 Sufficient costal cartilage
 Mastoid well pneumatised
Complications
 Lateralization of TM 3.4%
 Meatal Stenosis 3.8%
 High-tone SNHL 7.5%
 Facial nerve palsy 1%
Unilateral atretic ear
 Decreased incidence of
‘major ‘complications
 A rewarding operation
 Offer a clean & dry ear
 Binaural hearing
 ‘Minor’ unilateral atresia
 In early childhood
71%
29%
Male
Female
Data
n= 21
Jan 2008-Dec 2014
Data
62%
38%
Unilateral Bilateral
Jan 2008-Dec 2014
Data
Jan 2008-Dec 2014
36%
50%
14%
Atresia
Type I Type II Type III
0
1
2
3
4
5
6
7
8
9
10
CMH
Regional
Intl
Data
Jan 2008-Dec 2014
Nishizaki K, Masuda Y, Karita K.Surgical management and its post-operative complications in congenital aural atresia.Acta
Otolaryngol Suppl.1999;540:42-4.
Oliver ER, Hughley BB, Shonka DC, Kesser BW.Revision aural atresia surgery: indications and outcomes. Otol Neurotol. 2011
Feb;32(2):252-8. doi: 10.1097/MAO.0b013e3182015f27
Restenosis Otorrhea Facial nerve
paralysis
SNHL
Aural atresia regional conference

More Related Content

What's hot

Empty nose syndrome riyadh
Empty nose syndrome riyadhEmpty nose syndrome riyadh
Empty nose syndrome riyadh
Steven Houser
 
Phonosurgery
PhonosurgeryPhonosurgery
Phonosurgery
Vaibhav Lahane
 
OME-Otitis Media with effusion in children
OME-Otitis Media with effusion in childrenOME-Otitis Media with effusion in children
OME-Otitis Media with effusion in children
Razal M
 
Inverted papilloma
Inverted papillomaInverted papilloma
Inverted papilloma
Mohammed Nishad N
 
Ossiculoplasty
OssiculoplastyOssiculoplasty
Ossiculoplasty
Md Roohia
 
EMBRYOLOGY AND MALFORMATION OF EAR
EMBRYOLOGY AND MALFORMATION OF EAREMBRYOLOGY AND MALFORMATION OF EAR
EMBRYOLOGY AND MALFORMATION OF EAR
Manish Kumar
 
Surgical approach to middle ear,mastoid mamoon
Surgical approach to middle ear,mastoid mamoonSurgical approach to middle ear,mastoid mamoon
Surgical approach to middle ear,mastoid mamoon
Mamoon Ameen
 
Intractable aspiration
Intractable aspirationIntractable aspiration
Intractable aspiration
ENT Resident
 
Mucosal folds of the middle ear
Mucosal folds of the middle earMucosal folds of the middle ear
Mucosal folds of the middle ear
Dʀ Smruti Ranjan Samal
 
Endoscopic middle ear surgery
Endoscopic middle ear surgeryEndoscopic middle ear surgery
Endoscopic middle ear surgery
Divya Raana
 
Stem cell therapy in ENT
Stem cell therapy in ENTStem cell therapy in ENT
Stem cell therapy in ENT
SuryaR38
 
Nasal polypi
Nasal polypiNasal polypi
Balloon sinuplasty-slides-091216
Balloon sinuplasty-slides-091216Balloon sinuplasty-slides-091216
Balloon sinuplasty-slides-091216
Karl Daniel, M.D.
 
Petrous apex 360°
Petrous apex 360°Petrous apex 360°
Petrous apex 360°
Murali Chand Nallamothu
 
Sinus tympani prof dr bikash
Sinus tympani prof dr bikashSinus tympani prof dr bikash
Sinus tympani prof dr bikash
Bikash Shrestha
 
Anatomy of temporal bone
Anatomy of temporal boneAnatomy of temporal bone
Anatomy of temporal bone
praneeth koduru
 
Intra operative monitoring facial nerve
Intra operative monitoring facial nerveIntra operative monitoring facial nerve
Intra operative monitoring facial nerve
Md Roohia
 
Cavity obliteration @ sayan
Cavity obliteration  @ sayanCavity obliteration  @ sayan
Cavity obliteration @ sayan
IPGMER
 
Endoscopic anatomy of nose ,paranasal sinus and anterior skull base
Endoscopic anatomy of nose ,paranasal sinus and anterior skull baseEndoscopic anatomy of nose ,paranasal sinus and anterior skull base
Endoscopic anatomy of nose ,paranasal sinus and anterior skull base
Rajat Jain
 
Petrous cholesteatoma sample
Petrous cholesteatoma samplePetrous cholesteatoma sample
Petrous cholesteatoma sample
85160
 

What's hot (20)

Empty nose syndrome riyadh
Empty nose syndrome riyadhEmpty nose syndrome riyadh
Empty nose syndrome riyadh
 
Phonosurgery
PhonosurgeryPhonosurgery
Phonosurgery
 
OME-Otitis Media with effusion in children
OME-Otitis Media with effusion in childrenOME-Otitis Media with effusion in children
OME-Otitis Media with effusion in children
 
Inverted papilloma
Inverted papillomaInverted papilloma
Inverted papilloma
 
Ossiculoplasty
OssiculoplastyOssiculoplasty
Ossiculoplasty
 
EMBRYOLOGY AND MALFORMATION OF EAR
EMBRYOLOGY AND MALFORMATION OF EAREMBRYOLOGY AND MALFORMATION OF EAR
EMBRYOLOGY AND MALFORMATION OF EAR
 
Surgical approach to middle ear,mastoid mamoon
Surgical approach to middle ear,mastoid mamoonSurgical approach to middle ear,mastoid mamoon
Surgical approach to middle ear,mastoid mamoon
 
Intractable aspiration
Intractable aspirationIntractable aspiration
Intractable aspiration
 
Mucosal folds of the middle ear
Mucosal folds of the middle earMucosal folds of the middle ear
Mucosal folds of the middle ear
 
Endoscopic middle ear surgery
Endoscopic middle ear surgeryEndoscopic middle ear surgery
Endoscopic middle ear surgery
 
Stem cell therapy in ENT
Stem cell therapy in ENTStem cell therapy in ENT
Stem cell therapy in ENT
 
Nasal polypi
Nasal polypiNasal polypi
Nasal polypi
 
Balloon sinuplasty-slides-091216
Balloon sinuplasty-slides-091216Balloon sinuplasty-slides-091216
Balloon sinuplasty-slides-091216
 
Petrous apex 360°
Petrous apex 360°Petrous apex 360°
Petrous apex 360°
 
Sinus tympani prof dr bikash
Sinus tympani prof dr bikashSinus tympani prof dr bikash
Sinus tympani prof dr bikash
 
Anatomy of temporal bone
Anatomy of temporal boneAnatomy of temporal bone
Anatomy of temporal bone
 
Intra operative monitoring facial nerve
Intra operative monitoring facial nerveIntra operative monitoring facial nerve
Intra operative monitoring facial nerve
 
Cavity obliteration @ sayan
Cavity obliteration  @ sayanCavity obliteration  @ sayan
Cavity obliteration @ sayan
 
Endoscopic anatomy of nose ,paranasal sinus and anterior skull base
Endoscopic anatomy of nose ,paranasal sinus and anterior skull baseEndoscopic anatomy of nose ,paranasal sinus and anterior skull base
Endoscopic anatomy of nose ,paranasal sinus and anterior skull base
 
Petrous cholesteatoma sample
Petrous cholesteatoma samplePetrous cholesteatoma sample
Petrous cholesteatoma sample
 

Viewers also liked

Challenges of human capacity development in federal universities in akwa ibom...
Challenges of human capacity development in federal universities in akwa ibom...Challenges of human capacity development in federal universities in akwa ibom...
Challenges of human capacity development in federal universities in akwa ibom...
Alexander Decker
 
Diseases of external ear
Diseases of external earDiseases of external ear
Diseases of external ear
Saeed Ullah
 
External auditory canal anatomy pathologies & management
External auditory canal anatomy pathologies & managementExternal auditory canal anatomy pathologies & management
External auditory canal anatomy pathologies & management
Vikas Jorwal
 
Diseases of the external ear
Diseases of the external earDiseases of the external ear
Diseases of the external ear
Ajay Manickam
 
Oesophageal atresia
Oesophageal atresiaOesophageal atresia
Oesophageal atresia
Fahad AlHulaibi
 
Tumours of external and middle ear
Tumours of external and middle earTumours of external and middle ear
Tumours of external and middle ear
Ramesh Parajuli
 
Diseases of external ear
Diseases of external earDiseases of external ear
Diseases of external ear
Balasubramanian Thiagarajan
 
ear disorders
ear disordersear disorders
ear disorders
ligi xavier
 
Otitis externa
Otitis externaOtitis externa
Otitis externa
Ahmed Almumtin
 
Anatomy & embryology ext ear & middle ear
Anatomy & embryology   ext ear & middle earAnatomy & embryology   ext ear & middle ear
Anatomy & embryology ext ear & middle ear
Shafeeq Mohammed
 

Viewers also liked (10)

Challenges of human capacity development in federal universities in akwa ibom...
Challenges of human capacity development in federal universities in akwa ibom...Challenges of human capacity development in federal universities in akwa ibom...
Challenges of human capacity development in federal universities in akwa ibom...
 
Diseases of external ear
Diseases of external earDiseases of external ear
Diseases of external ear
 
External auditory canal anatomy pathologies & management
External auditory canal anatomy pathologies & managementExternal auditory canal anatomy pathologies & management
External auditory canal anatomy pathologies & management
 
Diseases of the external ear
Diseases of the external earDiseases of the external ear
Diseases of the external ear
 
Oesophageal atresia
Oesophageal atresiaOesophageal atresia
Oesophageal atresia
 
Tumours of external and middle ear
Tumours of external and middle earTumours of external and middle ear
Tumours of external and middle ear
 
Diseases of external ear
Diseases of external earDiseases of external ear
Diseases of external ear
 
ear disorders
ear disordersear disorders
ear disorders
 
Otitis externa
Otitis externaOtitis externa
Otitis externa
 
Anatomy & embryology ext ear & middle ear
Anatomy & embryology   ext ear & middle earAnatomy & embryology   ext ear & middle ear
Anatomy & embryology ext ear & middle ear
 

Similar to Aural atresia regional conference

Airway assessment Dr. Tushar
Airway assessment Dr. TusharAirway assessment Dr. Tushar
Otitis media syanthika medsurg
Otitis media syanthika medsurgOtitis media syanthika medsurg
Otitis media syanthika medsurg
SYANTHIKADUTTA
 
OTOGENIC BRAIN ABSCESS by dr.ravindra
OTOGENIC BRAIN ABSCESS by dr.ravindraOTOGENIC BRAIN ABSCESS by dr.ravindra
OTOGENIC BRAIN ABSCESS by dr.ravindra
Ravindra Daggupati
 
Airway assessment and pedictors of difficult airway....must know for anaesthe...
Airway assessment and pedictors of difficult airway....must know for anaesthe...Airway assessment and pedictors of difficult airway....must know for anaesthe...
Airway assessment and pedictors of difficult airway....must know for anaesthe...
drriyas03
 
Diagnosis-of-ent-disorders-you-make-the-call.pptx
Diagnosis-of-ent-disorders-you-make-the-call.pptxDiagnosis-of-ent-disorders-you-make-the-call.pptx
Diagnosis-of-ent-disorders-you-make-the-call.pptx
AshurajHerode1
 
ADENOIDS&ADENOIDECTOMY BY ROOHIA
ADENOIDS&ADENOIDECTOMY BY ROOHIAADENOIDS&ADENOIDECTOMY BY ROOHIA
ADENOIDS&ADENOIDECTOMY BY ROOHIA
Md Roohia
 
Nasopharyngeal Carcinoma
Nasopharyngeal CarcinomaNasopharyngeal Carcinoma
Nasopharyngeal Carcinoma
Balasubramanian Thiagarajan
 
radiographicffffffffffffffffffff aids.pptx
radiographicffffffffffffffffffff aids.pptxradiographicffffffffffffffffffff aids.pptx
radiographicffffffffffffffffffff aids.pptx
MohammadEissaAhmadi
 
Airway management in for seadtion
Airway management in for seadtionAirway management in for seadtion
Airway management in for seadtion
moutasem al mashour
 
CLINICAL AND RADIOLOGICAL EVALUATION OF DEVIATED NASAL SEPTUM IN CLASSIFYING ...
CLINICAL AND RADIOLOGICAL EVALUATION OF DEVIATED NASAL SEPTUM IN CLASSIFYING ...CLINICAL AND RADIOLOGICAL EVALUATION OF DEVIATED NASAL SEPTUM IN CLASSIFYING ...
CLINICAL AND RADIOLOGICAL EVALUATION OF DEVIATED NASAL SEPTUM IN CLASSIFYING ...
Dr.Juveria Majeed
 
OTITIS MEDIA
OTITIS MEDIAOTITIS MEDIA
7 chronic suppurative otitis media with and without cholesteatoma
7 chronic suppurative otitis media with and without cholesteatoma7 chronic suppurative otitis media with and without cholesteatoma
7 chronic suppurative otitis media with and without cholesteatoma
Sumit Prajapati
 
7 chronic suppurative otitis media with and without cholesteatoma
7 chronic suppurative otitis media with and without cholesteatoma7 chronic suppurative otitis media with and without cholesteatoma
7 chronic suppurative otitis media with and without cholesteatoma
Sumit Prajapati
 
Otosclerosis
OtosclerosisOtosclerosis
Otosclerosis
ENT Resident
 
Airway assessment
Airway assessmentAirway assessment
Airway assessment
Saloni Sood
 
CARCINOMA OF THE ORAL CAVITY. Diagnosis and management.t
CARCINOMA OF THE ORAL CAVITY. Diagnosis and management.tCARCINOMA OF THE ORAL CAVITY. Diagnosis and management.t
CARCINOMA OF THE ORAL CAVITY. Diagnosis and management.t
Dr. RIFFAT KHATTAK
 
Special situations in tonsil and Adenoid disorder Special situations in ton...
Special situations in tonsil and Adenoid disorder 	 Special situations in ton...Special situations in tonsil and Adenoid disorder 	 Special situations in ton...
Special situations in tonsil and Adenoid disorder Special situations in ton...
MedicineAndHealthResearch
 
Diseases of the External Ear
Diseases of the External EarDiseases of the External Ear
Diseases of the External Ear
Ausaf Khan
 
Ent gp emergencies (edited)
Ent gp emergencies (edited)Ent gp emergencies (edited)
Ent gp emergencies (edited)
simonlloyd
 
Cholesteatoma & management
Cholesteatoma & managementCholesteatoma & management
Cholesteatoma & management
Prasanna Datta
 

Similar to Aural atresia regional conference (20)

Airway assessment Dr. Tushar
Airway assessment Dr. TusharAirway assessment Dr. Tushar
Airway assessment Dr. Tushar
 
Otitis media syanthika medsurg
Otitis media syanthika medsurgOtitis media syanthika medsurg
Otitis media syanthika medsurg
 
OTOGENIC BRAIN ABSCESS by dr.ravindra
OTOGENIC BRAIN ABSCESS by dr.ravindraOTOGENIC BRAIN ABSCESS by dr.ravindra
OTOGENIC BRAIN ABSCESS by dr.ravindra
 
Airway assessment and pedictors of difficult airway....must know for anaesthe...
Airway assessment and pedictors of difficult airway....must know for anaesthe...Airway assessment and pedictors of difficult airway....must know for anaesthe...
Airway assessment and pedictors of difficult airway....must know for anaesthe...
 
Diagnosis-of-ent-disorders-you-make-the-call.pptx
Diagnosis-of-ent-disorders-you-make-the-call.pptxDiagnosis-of-ent-disorders-you-make-the-call.pptx
Diagnosis-of-ent-disorders-you-make-the-call.pptx
 
ADENOIDS&ADENOIDECTOMY BY ROOHIA
ADENOIDS&ADENOIDECTOMY BY ROOHIAADENOIDS&ADENOIDECTOMY BY ROOHIA
ADENOIDS&ADENOIDECTOMY BY ROOHIA
 
Nasopharyngeal Carcinoma
Nasopharyngeal CarcinomaNasopharyngeal Carcinoma
Nasopharyngeal Carcinoma
 
radiographicffffffffffffffffffff aids.pptx
radiographicffffffffffffffffffff aids.pptxradiographicffffffffffffffffffff aids.pptx
radiographicffffffffffffffffffff aids.pptx
 
Airway management in for seadtion
Airway management in for seadtionAirway management in for seadtion
Airway management in for seadtion
 
CLINICAL AND RADIOLOGICAL EVALUATION OF DEVIATED NASAL SEPTUM IN CLASSIFYING ...
CLINICAL AND RADIOLOGICAL EVALUATION OF DEVIATED NASAL SEPTUM IN CLASSIFYING ...CLINICAL AND RADIOLOGICAL EVALUATION OF DEVIATED NASAL SEPTUM IN CLASSIFYING ...
CLINICAL AND RADIOLOGICAL EVALUATION OF DEVIATED NASAL SEPTUM IN CLASSIFYING ...
 
OTITIS MEDIA
OTITIS MEDIAOTITIS MEDIA
OTITIS MEDIA
 
7 chronic suppurative otitis media with and without cholesteatoma
7 chronic suppurative otitis media with and without cholesteatoma7 chronic suppurative otitis media with and without cholesteatoma
7 chronic suppurative otitis media with and without cholesteatoma
 
7 chronic suppurative otitis media with and without cholesteatoma
7 chronic suppurative otitis media with and without cholesteatoma7 chronic suppurative otitis media with and without cholesteatoma
7 chronic suppurative otitis media with and without cholesteatoma
 
Otosclerosis
OtosclerosisOtosclerosis
Otosclerosis
 
Airway assessment
Airway assessmentAirway assessment
Airway assessment
 
CARCINOMA OF THE ORAL CAVITY. Diagnosis and management.t
CARCINOMA OF THE ORAL CAVITY. Diagnosis and management.tCARCINOMA OF THE ORAL CAVITY. Diagnosis and management.t
CARCINOMA OF THE ORAL CAVITY. Diagnosis and management.t
 
Special situations in tonsil and Adenoid disorder Special situations in ton...
Special situations in tonsil and Adenoid disorder 	 Special situations in ton...Special situations in tonsil and Adenoid disorder 	 Special situations in ton...
Special situations in tonsil and Adenoid disorder Special situations in ton...
 
Diseases of the External Ear
Diseases of the External EarDiseases of the External Ear
Diseases of the External Ear
 
Ent gp emergencies (edited)
Ent gp emergencies (edited)Ent gp emergencies (edited)
Ent gp emergencies (edited)
 
Cholesteatoma & management
Cholesteatoma & managementCholesteatoma & management
Cholesteatoma & management
 

More from ENT Resident

Thyroid carcinomas
Thyroid carcinomasThyroid carcinomas
Thyroid carcinomas
ENT Resident
 
Csf rhinorrhea repair- case report and discussion
Csf rhinorrhea repair- case report and discussionCsf rhinorrhea repair- case report and discussion
Csf rhinorrhea repair- case report and discussion
ENT Resident
 
Parathyroid tumors
Parathyroid tumorsParathyroid tumors
Parathyroid tumors
ENT Resident
 
Meniere's disease
Meniere's diseaseMeniere's disease
Meniere's disease
ENT Resident
 
voice rehabilitation in total laryngectomy
voice rehabilitation in total laryngectomyvoice rehabilitation in total laryngectomy
voice rehabilitation in total laryngectomy
ENT Resident
 
Angiofibroma
AngiofibromaAngiofibroma
Angiofibroma
ENT Resident
 
Facial nerve disorders
Facial nerve disordersFacial nerve disorders
Facial nerve disorders
ENT Resident
 
Dengue in Pakistan
Dengue in PakistanDengue in Pakistan
Dengue in Pakistan
ENT Resident
 

More from ENT Resident (8)

Thyroid carcinomas
Thyroid carcinomasThyroid carcinomas
Thyroid carcinomas
 
Csf rhinorrhea repair- case report and discussion
Csf rhinorrhea repair- case report and discussionCsf rhinorrhea repair- case report and discussion
Csf rhinorrhea repair- case report and discussion
 
Parathyroid tumors
Parathyroid tumorsParathyroid tumors
Parathyroid tumors
 
Meniere's disease
Meniere's diseaseMeniere's disease
Meniere's disease
 
voice rehabilitation in total laryngectomy
voice rehabilitation in total laryngectomyvoice rehabilitation in total laryngectomy
voice rehabilitation in total laryngectomy
 
Angiofibroma
AngiofibromaAngiofibroma
Angiofibroma
 
Facial nerve disorders
Facial nerve disordersFacial nerve disorders
Facial nerve disorders
 
Dengue in Pakistan
Dengue in PakistanDengue in Pakistan
Dengue in Pakistan
 

Recently uploaded

Efficacy of Avartana Sneha in Ayurveda
Efficacy of Avartana Sneha in AyurvedaEfficacy of Avartana Sneha in Ayurveda
Efficacy of Avartana Sneha in Ayurveda
Dr. Jyothirmai Paindla
 
Does Over-Masturbation Contribute to Chronic Prostatitis.pptx
Does Over-Masturbation Contribute to Chronic Prostatitis.pptxDoes Over-Masturbation Contribute to Chronic Prostatitis.pptx
Does Over-Masturbation Contribute to Chronic Prostatitis.pptx
walterHu5
 
Abortion PG Seminar Power point presentation
Abortion PG Seminar Power point presentationAbortion PG Seminar Power point presentation
Abortion PG Seminar Power point presentation
AksshayaRajanbabu
 
CLEAR ALIGNER THERAPY IN ORTHODONTICS .pptx
CLEAR ALIGNER THERAPY IN ORTHODONTICS .pptxCLEAR ALIGNER THERAPY IN ORTHODONTICS .pptx
CLEAR ALIGNER THERAPY IN ORTHODONTICS .pptx
Government Dental College & Hospital Srinagar
 
The Nervous and Chemical Regulation of Respiration
The Nervous and Chemical Regulation of RespirationThe Nervous and Chemical Regulation of Respiration
The Nervous and Chemical Regulation of Respiration
MedicoseAcademics
 
Pharmacology of 5-hydroxytryptamine and Antagonist
Pharmacology of 5-hydroxytryptamine and AntagonistPharmacology of 5-hydroxytryptamine and Antagonist
Pharmacology of 5-hydroxytryptamine and Antagonist
Dr. Nikhilkumar Sakle
 
Clinic ^%[+27633867063*Abortion Pills For Sale In Tembisa Central
Clinic ^%[+27633867063*Abortion Pills For Sale In Tembisa CentralClinic ^%[+27633867063*Abortion Pills For Sale In Tembisa Central
Clinic ^%[+27633867063*Abortion Pills For Sale In Tembisa Central
19various
 
CHEMOTHERAPY_RDP_CHAPTER 1_ANTI TB DRUGS.pdf
CHEMOTHERAPY_RDP_CHAPTER 1_ANTI TB DRUGS.pdfCHEMOTHERAPY_RDP_CHAPTER 1_ANTI TB DRUGS.pdf
CHEMOTHERAPY_RDP_CHAPTER 1_ANTI TB DRUGS.pdf
rishi2789
 
Complementary feeding in infant IAP PROTOCOLS
Complementary feeding in infant IAP PROTOCOLSComplementary feeding in infant IAP PROTOCOLS
Complementary feeding in infant IAP PROTOCOLS
chiranthgowda16
 
vonoprazan A novel drug for GERD presentation
vonoprazan A novel drug for GERD presentationvonoprazan A novel drug for GERD presentation
vonoprazan A novel drug for GERD presentation
Dr.pavithra Anandan
 
Adhd Medication Shortage Uk - trinexpharmacy.com
Adhd Medication Shortage Uk - trinexpharmacy.comAdhd Medication Shortage Uk - trinexpharmacy.com
Adhd Medication Shortage Uk - trinexpharmacy.com
reignlana06
 
Osteoporosis - Definition , Evaluation and Management .pdf
Osteoporosis - Definition , Evaluation and Management .pdfOsteoporosis - Definition , Evaluation and Management .pdf
Osteoporosis - Definition , Evaluation and Management .pdf
Jim Jacob Roy
 
Hemodialysis: Chapter 5, Dialyzers Overview - Dr.Gawad
Hemodialysis: Chapter 5, Dialyzers Overview - Dr.GawadHemodialysis: Chapter 5, Dialyzers Overview - Dr.Gawad
Hemodialysis: Chapter 5, Dialyzers Overview - Dr.Gawad
NephroTube - Dr.Gawad
 
K CỔ TỬ CUNG.pdf tự ghi chép, chữ hơi xấu
K CỔ TỬ CUNG.pdf tự ghi chép, chữ hơi xấuK CỔ TỬ CUNG.pdf tự ghi chép, chữ hơi xấu
K CỔ TỬ CUNG.pdf tự ghi chép, chữ hơi xấu
HongBiThi1
 
Cardiac Assessment for B.sc Nursing Student.pdf
Cardiac Assessment for B.sc Nursing Student.pdfCardiac Assessment for B.sc Nursing Student.pdf
Cardiac Assessment for B.sc Nursing Student.pdf
shivalingatalekar1
 
10 Benefits an EPCR Software should Bring to EMS Organizations
10 Benefits an EPCR Software should Bring to EMS Organizations   10 Benefits an EPCR Software should Bring to EMS Organizations
10 Benefits an EPCR Software should Bring to EMS Organizations
Traumasoft LLC
 
CHEMOTHERAPY_RDP_CHAPTER 2 _LEPROSY.pdf1
CHEMOTHERAPY_RDP_CHAPTER 2 _LEPROSY.pdf1CHEMOTHERAPY_RDP_CHAPTER 2 _LEPROSY.pdf1
CHEMOTHERAPY_RDP_CHAPTER 2 _LEPROSY.pdf1
rishi2789
 
Top Travel Vaccinations in Manchester
Top Travel Vaccinations in ManchesterTop Travel Vaccinations in Manchester
Top Travel Vaccinations in Manchester
NX Healthcare
 
REGULATION FOR COMBINATION PRODUCTS AND MEDICAL DEVICES.pptx
REGULATION FOR COMBINATION PRODUCTS AND MEDICAL DEVICES.pptxREGULATION FOR COMBINATION PRODUCTS AND MEDICAL DEVICES.pptx
REGULATION FOR COMBINATION PRODUCTS AND MEDICAL DEVICES.pptx
LaniyaNasrink
 
CHEMOTHERAPY_RDP_CHAPTER 4_ANTI VIRAL DRUGS.pdf
CHEMOTHERAPY_RDP_CHAPTER 4_ANTI VIRAL DRUGS.pdfCHEMOTHERAPY_RDP_CHAPTER 4_ANTI VIRAL DRUGS.pdf
CHEMOTHERAPY_RDP_CHAPTER 4_ANTI VIRAL DRUGS.pdf
rishi2789
 

Recently uploaded (20)

Efficacy of Avartana Sneha in Ayurveda
Efficacy of Avartana Sneha in AyurvedaEfficacy of Avartana Sneha in Ayurveda
Efficacy of Avartana Sneha in Ayurveda
 
Does Over-Masturbation Contribute to Chronic Prostatitis.pptx
Does Over-Masturbation Contribute to Chronic Prostatitis.pptxDoes Over-Masturbation Contribute to Chronic Prostatitis.pptx
Does Over-Masturbation Contribute to Chronic Prostatitis.pptx
 
Abortion PG Seminar Power point presentation
Abortion PG Seminar Power point presentationAbortion PG Seminar Power point presentation
Abortion PG Seminar Power point presentation
 
CLEAR ALIGNER THERAPY IN ORTHODONTICS .pptx
CLEAR ALIGNER THERAPY IN ORTHODONTICS .pptxCLEAR ALIGNER THERAPY IN ORTHODONTICS .pptx
CLEAR ALIGNER THERAPY IN ORTHODONTICS .pptx
 
The Nervous and Chemical Regulation of Respiration
The Nervous and Chemical Regulation of RespirationThe Nervous and Chemical Regulation of Respiration
The Nervous and Chemical Regulation of Respiration
 
Pharmacology of 5-hydroxytryptamine and Antagonist
Pharmacology of 5-hydroxytryptamine and AntagonistPharmacology of 5-hydroxytryptamine and Antagonist
Pharmacology of 5-hydroxytryptamine and Antagonist
 
Clinic ^%[+27633867063*Abortion Pills For Sale In Tembisa Central
Clinic ^%[+27633867063*Abortion Pills For Sale In Tembisa CentralClinic ^%[+27633867063*Abortion Pills For Sale In Tembisa Central
Clinic ^%[+27633867063*Abortion Pills For Sale In Tembisa Central
 
CHEMOTHERAPY_RDP_CHAPTER 1_ANTI TB DRUGS.pdf
CHEMOTHERAPY_RDP_CHAPTER 1_ANTI TB DRUGS.pdfCHEMOTHERAPY_RDP_CHAPTER 1_ANTI TB DRUGS.pdf
CHEMOTHERAPY_RDP_CHAPTER 1_ANTI TB DRUGS.pdf
 
Complementary feeding in infant IAP PROTOCOLS
Complementary feeding in infant IAP PROTOCOLSComplementary feeding in infant IAP PROTOCOLS
Complementary feeding in infant IAP PROTOCOLS
 
vonoprazan A novel drug for GERD presentation
vonoprazan A novel drug for GERD presentationvonoprazan A novel drug for GERD presentation
vonoprazan A novel drug for GERD presentation
 
Adhd Medication Shortage Uk - trinexpharmacy.com
Adhd Medication Shortage Uk - trinexpharmacy.comAdhd Medication Shortage Uk - trinexpharmacy.com
Adhd Medication Shortage Uk - trinexpharmacy.com
 
Osteoporosis - Definition , Evaluation and Management .pdf
Osteoporosis - Definition , Evaluation and Management .pdfOsteoporosis - Definition , Evaluation and Management .pdf
Osteoporosis - Definition , Evaluation and Management .pdf
 
Hemodialysis: Chapter 5, Dialyzers Overview - Dr.Gawad
Hemodialysis: Chapter 5, Dialyzers Overview - Dr.GawadHemodialysis: Chapter 5, Dialyzers Overview - Dr.Gawad
Hemodialysis: Chapter 5, Dialyzers Overview - Dr.Gawad
 
K CỔ TỬ CUNG.pdf tự ghi chép, chữ hơi xấu
K CỔ TỬ CUNG.pdf tự ghi chép, chữ hơi xấuK CỔ TỬ CUNG.pdf tự ghi chép, chữ hơi xấu
K CỔ TỬ CUNG.pdf tự ghi chép, chữ hơi xấu
 
Cardiac Assessment for B.sc Nursing Student.pdf
Cardiac Assessment for B.sc Nursing Student.pdfCardiac Assessment for B.sc Nursing Student.pdf
Cardiac Assessment for B.sc Nursing Student.pdf
 
10 Benefits an EPCR Software should Bring to EMS Organizations
10 Benefits an EPCR Software should Bring to EMS Organizations   10 Benefits an EPCR Software should Bring to EMS Organizations
10 Benefits an EPCR Software should Bring to EMS Organizations
 
CHEMOTHERAPY_RDP_CHAPTER 2 _LEPROSY.pdf1
CHEMOTHERAPY_RDP_CHAPTER 2 _LEPROSY.pdf1CHEMOTHERAPY_RDP_CHAPTER 2 _LEPROSY.pdf1
CHEMOTHERAPY_RDP_CHAPTER 2 _LEPROSY.pdf1
 
Top Travel Vaccinations in Manchester
Top Travel Vaccinations in ManchesterTop Travel Vaccinations in Manchester
Top Travel Vaccinations in Manchester
 
REGULATION FOR COMBINATION PRODUCTS AND MEDICAL DEVICES.pptx
REGULATION FOR COMBINATION PRODUCTS AND MEDICAL DEVICES.pptxREGULATION FOR COMBINATION PRODUCTS AND MEDICAL DEVICES.pptx
REGULATION FOR COMBINATION PRODUCTS AND MEDICAL DEVICES.pptx
 
CHEMOTHERAPY_RDP_CHAPTER 4_ANTI VIRAL DRUGS.pdf
CHEMOTHERAPY_RDP_CHAPTER 4_ANTI VIRAL DRUGS.pdfCHEMOTHERAPY_RDP_CHAPTER 4_ANTI VIRAL DRUGS.pdf
CHEMOTHERAPY_RDP_CHAPTER 4_ANTI VIRAL DRUGS.pdf
 

Aural atresia regional conference

Editor's Notes

  1. Respected teachers and my fellow colleagues AOA. I dr zeeshan resident in ENT head and neck surgery department CMH rwp will be presenting two cases of congenital aural atresia with different surgical scenarios.
  2. Case no 1 is A 6 year old boy brought to our institute by his consanguineous parents for scheduled ear surgery for bilateral hearing loss since birth. on examination altman grade 3 aural atresia with marx grade 3 microtia were seen bilaterally.
  3. BERA revealed the boy having 60 and 70 db hearing threshold in right and left ear respectively. free field hearing test reveal 60 and 80 db in right and left ear respectively.the boy had been wearing soft band bone conducting hearing aid since birth and studying in a special education school .speech therapist suggest adequate receptive and expressive language with good attention span.
  4. Ct san revealed partially canalised right external auditory canal with aerated middle ear and intact ossicles where as left middle ear showed abnormal configuration with no definitive ossicles.
  5. The boy was graded 9 on Jahrsdoerfer system and planned for surgery of the right ear. Associated risks of total deafness and facial nerve paralysis were explained to the parents.
  6. lateral face and the skin graft donor site were prepared and draped. A 1/2-inch swath of hair is shaved around the external ear
  7. An endaural incision is made and Soft tissue was elevated off the mastoid process in a posterior to anterior direction.
  8. Temporalis facia garft was harvested.
  9. The temporal root of the zygomatic arch and the glenoid fossa were identified and the cribriform area of the mastoid process was used as a landmark for drilling
  10. Drilling was done by staying superior and anteriorly.Care was taken to hug the tegmen and the glenoid fossa
  11. Dense atretic bone was found and followed medially.
  12. fused incus-malleus complex was encountered At a depth of approx 1.5 cm
  13. body of the incus was identified and confirmed by gentle Palpation.
  14. fused malleus head and incus body were found to be mobile on palpation. diamond bur was Used to thin the atretic plate to eggshell thickness and gently picked away in small pieces.
  15. facial nerve was seen having a short vertical segment while making a sharp curve anteriorly. Normal mobile stapes suprastructure was confirmed by gentle palpation. .
  16. peripheral bone was then drilled to gain room for the placement of the fascial graft.
  17. fascia graft was placed directly on the ossicular Mass so as it was Approximately in center of the new tympanic membrane.
  18. a “U”-shaped pedicle flap hinged at the tragal remanent was then positioned into the new ear canal and sutured to a cuff of periosteum.
  19. Following proper placement of the meatus the external ear was stabilized with subcutaneous sutures and ear canal was packed with spongiston wicks and BIPP packs.mastoid dressing was applied.
  20. The patient was discharged on the 2nd postop day and sutures were removed on 1 postop week. here the patient is seen in the 2nd week showing granulating wound with healthy pedicle skin.silver nitrate was applied to the granulations and EAC was packed with antibiotic impregnated gelfoam. the boy is scheduled to have his 1st audiogram in 3rd week postoperatively.
  21. Case no 2 is An 18 year-old female patient referred to our institute with painful post-auricular discharging sinus on her left side associated with swelling and redness around it. examination revealed that the patient had aural stenosis dating since birth and grade II microtia with acute mastoiditis that led to sinus formation on the left side,.. the right ear was completely normal.
  22. Pure tone audiogram showed conductive hearing loss with an air-bone gap of 50 dB on the left side and near normal hearing of right ear
  23. Ct scan show soft tissue density in the left external auditory meatus with intact ossicles.
  24. X ray mastoid showed a sclerosed left mastoid with an opacity in the attic region while a well pneumatised right mastoid.
  25. Patient was prepped for surgery after explaining risks of total deafness and facial nerve paralysis.
  26. lateral face and the skin graft donor site were prepared and draped. A 1/2-inch swath of hair is shaved around the external ear
  27. modified pre-auricular incision was made and unhealthy skin around the sinus excised.
  28. Temporalis fascia graft was harvested and dried on petri dish.
  29. Cortical mastoidectomy was carried out to reveal an automastoidectomy cavity extending into the attic area.
  30. Mastoid cavity was Filled with a large cholesteatoma sac
  31. Whole of the cholesteatoma sac was carefully removed.
  32. here is the magnified view of the isolated Cholesteama sac.
  33. the middle ear was entered via an atticoantrostomy approach And atretic plate found which was carefully drilled away. The ossicular mass in the epitympanum was meticulously dissected free of the atretic plate and left intact after ensuring its mobility.
  34. The horizontal facial nerve was seen medial to the ossicular mass.
  35. then temporalis fascia graft was used to cover the ossicular mass and line the mastoid cavity.
  36. Reconstruction of the external auditory canal was done through removal of the bone lateral to the middle ear space with meatoplasty of the cartilaginous portion
  37. No intra-operative or post-operative complications were seen.
  38. pack was removed on the 10th post-operative day.granulations were seen in the mastod cavity and repacking was done with BIPP. Pt is on periodic visits for the regular cleaning of the mastoid cavity.
  39. Congenital aural atresia occurs once in every 10,000 births. Unilateral atresia is seven times more common than bilateral atresia. Aural atresia is associated with a recognizable syndrome in about 10% of cases. In about 5% of nonsyndromic cases, the birth defect is inherited.
  40. Syndromic conditions associated with congenital aural atresia include: • Treacher Collins; • brachio-otorenal; • Sticklers;
  41. • Crouzons; • Noonan syndrome; • foetal alcohol syndrome;
  42. • CHARGE syndrome coloboma, heart choanal atresia, developmental and growth retardation, genito-urinary malformations and ear anomalies (CHARGE)
  43. The inner ear, middle ear, and external ear develop independently and in such a way that deformity of one does not presuppose deformity of another. Most frequently, abnormalities of the outer and middle ear are encountered in combination with a normal inner ear.
  44. Some of the literature supports the notion that microtia grade indicate the status of middle ear development.
  45. Growth of mesenchymal tissue from the first and second branchial arches forms six hillocks around the primitive meatus that fuse to form the auricle .
  46. Microtia is a result of first and second branchial arch Anomalies and is classified by Marx into 4 grades.
  47. During the second month The first branchial pouch grows outward to form the middle ear cleft while a solid core of epithelium migrates inward from the rudimentary pinna toward the first branchial pouch.
  48. Meckel’s cartilage form the malleus and incus body. Reichert’s cartilage forms the long process of incus and the stapes superstructure while The footplate has a dual origin from the second arch and the otic capsule.
  49. Congenital aural atresia can range in severity from a thin membranous canal atresia to complete lack of tympanic bone, depending on the time of arrest of intrauterine development
  50. Of historical significance is a classification by Altmann. In this system, atresias are categorized into three groups, In Group 1 Some part of the EAC is hypoplastic.
  51. In Group 2 The EAC is completely absent, the tympanic cavity is small, and its content is deformed, and the “atresia plate” is partially or completely osseous
  52. In Group 3 The EAC is absent, and the tympanic cavity is markedly hypoplastic or missing.
  53. The De la Cruz classification includes surgical feasibility guidelines using HRCT, taking into consideration mastoid pneumatization, inner ear normality, facial nerve and footplate relationship.
  54. The malformations are divided into minor and major malformations.
  55. Jahrsdoerfer and colleagues developed a widely used point grading system to guide surgeons in preoperative assessment of the best candidates for hearing improvement. Point allocation is based primarily on the findings on HRCT.
  56. Jahrsdoerfer proposed that the best results are achieved with a score of 8 or better.
  57. Schuknecht’s system is based on a combination of clinical and surgical observations. Type A atresia is limited to the fibrocartilaginous.
  58. type B there is narrowing of the fibrocartilaginous and bony EAC.
  59. Type C is a totally atretic ear canal, but a well-pneumatized tympanic cavity.
  60. Type D is a hypopneumatic atresia which is common in dysplasias such as Treacher Collins syndrome.
  61. Chiossone’s classification is based primarily on the location of the glenoid fossa. Patients with types I and II are ideal surgical candidates.
  62. Type III cases have a tendency toward graft lateralization.
  63. Patients with type IV are not surgical candidates
  64. Where one congenital abnormality is found, others must be sought. After physical examination,evaluation of auditory function should be performed using auditory brainstem response audiometry within the first few days of life. initial evaluation of an older individual is with Audiometry and high-resolution CT scan
  65. In bilateral cases, a bone-conduction hearing aid should be applied as soon as possible, ideally in the third or fourth week of life. A child with aural atresia and associated cephalic abnormalities surgical correction has poor results so BAHA is used in such cases.
  66. Prompt and careful counseling of the parents of a child is necessary to alleviate concerns. The child should be enrolled in special education at an early age to maximize speech and language acquisition, in preparation for “mainstreaming” at preschool age.
  67. There are two requirements for planning surgery in congenital aural atresia: radiographic three-dimensional evaluation of the temporal bone and audiometric evidence of cochlear function
  68. Other conditions mandating prompt surgical intervention are congenital cholesteatoma, a draining postoperative atretic ear, and acute facial palsy. The CT scan should always be reviewed for cholesteatoma,which necessitates surgery at any age
  69. In bilateral or unilateral atresia, auricular reconstruction and atresiaplasty are recommended at 6 years of age. Before this age, there may be a tendency to form exostosis-like bony growth and there is less patient cooperation. the costal cartilage has developed sufficiently to allow for reconstruction and the mastoid has become pneumatized.
  70. Complications of surgery include Lateralization of the tympanic membrane ,stenosis of the meatus ,high-tone SNHL and facial nerve palsy.
  71. Elective surgery in unilateral atresia is a controversial topic .now a day it is rewarding for the surgeon and the patient ….offering benefits of a clean, dry ear with binaural Hearing. it is done in patient with “minor” unilateral atresia it may be offered in childhood with the parents’ consent.
  72. A total of 21 patients of both sexes with congenital aural atresia were operated from January 2008 to Dec 2014 with a male to female ratio of 2.5:1
  73. 26 patients had unilateral atresia while 16 patients had bilateral aural atresia with a ratio of 1.6:1.
  74. Type I meatal atresia was present in 36 % patients, while 50% patients had type II meatal atresia and 14% patients had type III meatal atresia.
  75. Our data was compared with regional and international study which show comparable results. our results showed low rate of restenosis in comparison to the regional and international study.