Cardiac myxomas are the most common primary cardiac tumor. They usually arise from the left atrium but can occur in other chambers. Clinical presentation depends on location, size and mobility of the tumor and can include signs of intracardiac obstruction, embolization, and constitutional symptoms. Echocardiography is the diagnostic tool of choice, showing an atrial mass attached by a stalk. Treatment involves surgical excision which is usually curative, though rare familial forms have a higher recurrence risk.