2. INTRODUCTION
ANO means the anus and RECTAL means rectum.
ANORECTAL MALFORMATION are birth defect or
problems that happen as an unborn baby is
developing during pregnancy with this defect the
anus and rectum don’t develop properly they are
lower part of the digestive tract.
4. CAUSES
URINARY TRACT ABNORMALIIES
ABNORMALITIES OF THE SPINE
DIGESTIVE SYSTEM ABNORMALITIES
VACTERAL(a syndrome in which there are vertebral
, anal, cardiac, tracheal , renal and limb
abnormalities)
6. PATHOPHYSIOLOGY
GENITOURINARY TRACT ORIGINATES FROM
THE EMBRYONIC STRUCTURE CALLED CLOACA
BYY THE WORK OF GESTATION MEMBRANE
SEPARATES THE RECTUM FROM ANUS
IF THE MEMBRANE THAT SEPARATES ANUS IS
NOT ABSORED
UNION OF ANUS AND RECTUM DOES NOT
OCCUR
RESULTNG IN ANORECTAL MALFORMATION
7. SIGN AND SYMPTOMS
LACK OF STOOL
STOOL COMING FROM THE VAGINA
URINE COMING FROM THE ANUS
TROUBLE HAVING A BOWEL MOVEMENT OR
CONSTIPATION
8. DIAGNOSTIC EVALAUTION
DETECTION OF IMPERFORATED ANUS
NO ANAL OPENING
GLOVED FINGER OR THERMOMETER CANNOT
BE INSTERED INTO INFANT RECTUM
NO HISTROY OF PASSAGE OF MECONIUM
PRESENCE OF DISTENSION
PRESENCE OF MECONIUM IN URINE,
INDICATING RECTOVAGINAL FISTULA
10. MANAGEMENT
DURING THE FIRST 24 HOURS THE NEONATES
SHOULD-
PERINEAL EXAMINATION
PROVIDE NOTHING ORALLY
PROVIDE IV FLUID
ANTIBIOTICS
NGT TO EXCLUDE ESOPHAGEAL ATRESIA
ECHOCARDIOGRAM TO EXCLUDE MALFORMATION
0F CARDIAC
RADIOGRAPH
ULTRASOUND
12. NURSING MANAGEMENT
PRE-OPERATIVE NURSING CARE-
AFTER BIRTH AS SOON AS THE ANORMALY IS
NOTICED, ORAL FEEDING SHOULD BE STOPPED
IV FLUID ARE STARTED TO MEET NUTRITIONAL
REQUIREMENTS
ABDOMINAL GIRTH SHOULD BE MEASURED
GASTRIC COMPRESSION SHOULD BE DONE BY
NASOGATRIC ASPIRATION
MONITOR VITAL SIGNS PREPARE THE FAMILY
PSYCHOLOGICALLY FOR INFANT SURGERY
13. POST OPERATIVE CARE-
INTRAVENOUS FEEDING TILL THE WOUND HEALS
PREVENTION OF CONSTIPATION BY EXCLUSIVE
BREASTFEEDING AND PROPER WEANING WITH STOOL
SOFTENER
BOWEL HABIT TRAINING
PROVIDE ENEMA
DON’T USE DIAPER IN CASES OF ANOPLASTY
COLOSTOMY CARE BY CHANING TE COLLECTION
DEVICE
FAMILY SUPPORT , DISCHARGE PLANNING AND HOME
CARE