10. CO2
Methylene
-THF
THF
Glycine
NH3
Glycine to CO2 and NH3
Glycine Cleavage
complex
Glycine cleavage complex , Present in Neonatal
Liver
Deficiency of which leads to hyper glycinemia
Glycine is inhibitory NT , cause neurological
disorder
NADH
NAD
+
12. Oxalic acid
½ O2
oxidation
GlycinePyruvic acid
Alanine
Glyoxylate
Transaminase
Glyoxylate
Alanine
Primary
Oxaluria type I
Mental
retardation
Kidney stone
TRANSAMINATION OF GLYCINE
15. Glutamate Cysteine
γ-Glutamyl cysteine
Glutathione
ADP + Pi
ATP
Synthesis of Glutathione
Glycine
ADP + Pi
ATP
γ Glutamyl cystein
synthetase
+
Glutamyl cystenyl glycine
Glutathione
synthetase
2 G SH
G SSG
N AD P
NAD PH
+ H
Glutathione
r educ tas e
16. Glycine Succinyl COA+
δ Amino levulinic acid
Porphobilinogen Heme
Mitochondria
2 molecules
δ-Amino levulinate
synthaseCO-A + CO2
SYNTHESIS OF HEME
δ Am ino
levulinic acid
17. Synthesis of
Hippuric acid and Bile salts
Benzoic acid
Benzoyl CO A
Benzoyl glycine /
Hippuric acid
Cholic acid
Cholyl CO A
Glyco-cholic acid
CO A SH
ATP
ADP + Pi