1) A 60-year-old Asian male presented with loss of vision and severe headache in his right eye for 3 months. Examination revealed a large pigmented mass in the retrolental space, retinal detachment, and secondary glaucoma in the right eye. 2) Ultrasound and MRI confirmed a choroidal melanoma arising from the cilio-choroidal junction in the right eye, measuring over 1 cm3. 3) The patient underwent enucleation of the right eye. Histopathology revealed a Type A spindle cell melanoma with occasional mitoses and no scleral extension.