Seal of Good Local Governance (SGLG) 2024Final.pptx
ARM
1. ANORECTAL MALFORMATION
Approach Of A Pediatrician To A Case Of
Newborn With ANORECTAL
MALFORMATION
Speakers -Dr.Sushmita Ghosh
Moderator-Dr.M.K.Mohanty(Paed.Surgeon)
Jawaharlal Nehru Hospital & Research Centre
Bhilai Steel Plant Hospital
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2. INTRODUCTION
Anorectal malformation-
Complex disorder ranging from cloaca
(most severe) to perineal fistula.
Invertogram- in 1930
Upto 1948 Surgical correction-Rhodes
Since 1982- PSARP by Alberto Pena
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3. ROLE OF PEDIATRICIAN
Intramural Extramural
(delivery-own hosp.)
*diagnosis (outside delivery)
*initial stabilization *diagnosed outside
*referral to paed.surgeon *stabilization
*treatment of sepsis,if any
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8. NEWBORN WITH ARM (FEMALE)
PERINEAL INSPECTION
FISTULA(APPROX.90%) NO FISTULA(APPROX.10%)
SINGLE OPENING TWO OPENINGs THREE OPENINGs
CLOACA VAGINAL CUTANEOUS
OR (PERINEAL) INVERTOGRAM
VESTIBULAR
>1 CM BOWEL- <1 CM BOWEL-
SKIN DISTANCE SKIN DIST.
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14. INCIDENCE
WORLDWIDE 1:5,000 LIVE BIRTHS
GENETIC PREDISPOSITION IN CERTAIN FAMILIES
ASSOCIATION WITH CERTAIN SYNDROMES-
VACTERL,VATER,DOWN’S SYNDROME
SLIGHT MALE PREPONDERANCE
IN FEMALES-RECTOVESTIBULAR FISTULA MOST COMMON
IN MALES -RECTOURETHRAL FISTULA MOST COMMON
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15. INITIAL MANAGEMENT
RED RUBBER CATHETER INSERTION
NBM & INTRAVENOUS FLUIDS
FIRST LINE ANTIBIOTICS- CLOXACILLIN
& AMIKACIN
INJECTION VITAMIN K
NASOGASTRIC DECOMPRESSION after 24 hrs
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16. ASSOCIATED MALFORMATIONS
(50-60%)
UROGENITAL-
URINARY-UNILATERAL AGENESIS OF KIDNEY
-PUJ OBSTRUCTION
-HYPOSPADIAS
-VUR
GENITAL- BICORNUATE UTERUS
-UTERUS DIDELPHYS
-VAGINAL SEPTUM
-BLIND HEMIVAGINA
-ATRESIA OF CERVIX
-HYDROCOLPOS
CARDIOVASCULAR- 1/3RD Pts
-ASD,PDA most common
-VSD,TOF
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