This is in a simplified version

1. DENTIN DYSPLASIA
By
M.Ambika
BDS 2nd yr

2. Dentin dysplasia- Introduction
• Disturbance of dentin formation.
• Rare Genetic developmental disorder affecting
dentin production of the teeth.
• Normal enamel but atypical dentin formation with
abnormal pulpal morphology

3. First description :
“Ballschmiede”
-reported spontaneous exfoliation of
multiple teeth in four children of one family
This phenomenon is called “Rootless teeth”

4. ETIOLOGY:
 Unknown etiology-that affect approximately
1:100000
 Type1&2- hereditary disease, transmitted as
autosomal dominant .
 Age: Affects the children because of early
loss of teeth.
 Gender: Both males and females are
affected.

5.  Short and conical roots
 Pulp chambers are obliterated by multiple
nodules of poorly organised dentin.
 Affected teeth may exhibit increased mobility
and exfoliate prematurely .

6. Types:
There are two types of dentin dysplasia
Type 1- Radicular
Type 2- Coronal

7. Dentin dysplasia
Dentin dysplasia –Type 1

8. Dentin Dysplasia –Type 2

9. Sign and Symptoms:
Radicular Dentin dysplasia
 Undeveloped roots with abnormal tissues
 Morphology and colour - normal
 Slightly amper or bluish brown shine in primary teeth with
no or immature root development.

10. Coronal dentin dysplasia:
 Tooth Discoloration
 Abmormlaities of the pulp chambers.
 Abnormally rounded (bulbous crown)
 Wearing away
 Premature loss of teeth

11. Clinical features:
Radicular
 Both dentition are affected.
 Exhibit extreme mobility
&exoliated prematurely as
result of short roots.
Coronal
 Both dentition are affected .
 Deciduous teeth have same
yellow,brown,appearance as
seen in dentinogenesis
imperfect
 However ,clinical appearance
of permanent dentition is
normal.

12. Clinical features:
 Clinical features can be modified by variation in
penetration and expressivity.
 Some individual inherit the mutant gene but are
phenotypically normal.
 This is referred to as incomplete penetrance.

13. Radiographic features:
Radicular
 In both dentition,root are
short,blunt,conical .
 In decidious teeth,pulp
chambers &root canals are
completely obliterated.
 In permanent teeth,crescent
shaped pulpal remanent still
seen in pulp chamber.
Coronal
 In deciduous teeth,pulp
chamber obliterated in type 1&
dentinogenesis obliterated.
 In permanent, exhibit abnormal
large pulp chamber in Coronal
portion of tooth = “thistle
tube”resemble pulpstone.

14. Histologic features
Radicular
 Type 1-normal
 Apical to this may be area of
tubular dentin but most of
that which obliterates pulp is
calcified tubular dentin
,osteodentin &fused
denticles.
Coronal
 Deciduous teeth exhibit
amorphous and atubular dentin
in Radicular portion While
Coronal portion is normal.
 Permanent teeth also shows
Relatively normal Coronal
dentin ,but the pulp has
multiple pulpstones or
denticles.

15. Treatment and prognosis:
There is no treatment for the disease.
Dental X-rays are the key to diagnose dentin dysplasia
especially on permanent teeth.
Its prognosis depends on the occurrence of Periapical lesion
due to increased mobility.