2. INTRODUCTION
The term plagiocephaly derives from the Greek plagios meaning oblique and
cephalo referencing the head.
The term deformational plagiocephaly, deformational Brachiocephaly and
deformational Scaphocephaly refer to cranial deformities.
Cranial deformity features:-
• deviations in proportion and/or symmetry of
the neurocranium(i.e skull)
• Accompanied by misalignment of the bones
of the viscerocranium(i.e face).
3. Cont…
Cranial remoulding orhoses are usually in the shape of an adjustable helmet
or band that progressively molds the shape of the infants cranium by
applying corrective forces to prominences while leaving room for growth in
adjacent flattened areas.
A Cranial remoulding orthoses may be requested for the treatment of
positional or postsurgical synostosis in paediatric patient.
An asymmetrically shaped head may be synostotic(craniosynostosis) or
nonsynostotic(deformational).
Positional cranial deformity also known as deformational or nonsynostosis
cranial deformity. The nonsynostosis or deformational cranial deformity
refer to cranial deformities that are recognized in infancy and develop from
both prenatal and postnatal factors.
4. Synostosis defined as premature closures of the sutures of the cranium, may
result in functional deficits secondary to increasing intracranial pressure in
an abnormally or asymmetrically shaped cranium.
The type and degree of craniofascial deformity depends on the type of
synostosis.
Cranial deformity may be plagiocephaly ,brachiocephaly and scapho
cephaly.
5. Clinical anatomy of skull
• The shape and structure of the skull bones
are affected by genetic, metabolic, and
mechanical factors because deformation or
misalignment of one unit affects the
alignment and shape of adjoining structures
• The skull of the infant has nine bones of
the neurocranium
• The viscerocranium consists of 14 facial
bones.
• Alignment and orientation of viserocranium
structures are interdependent with the
alignment and orientation of the
neurocranium.
6. Pathophysiology
Causes:-
1. Abnormalities in brain shape or development- includes microcephaly,
macrocephaly and in uterocerebrovascular accident.
2. Abnormalities in bone or suture development- craniosyntosis, apert
syndrome, crouzon syndrome
3. Prenatal and postnatal deforming forces.
7. Common head deformities:-
Plagiocephaly
Most common cranial anomaly
Asymmetry of rt and lt side of skull
Asymmtery of the neurocranium and
viscerocranium
Unilateral occipital flattening
Ipsilateral anterior ear progression
Ipsilateral forehead bossing
Contralateral forehead depression
contralateral occipital bossing
Fascial asymmetry
Congenital muscular torticollis
Altered alignment of eyes, cheeks, nose,
,mouth and chin
8. Brachiocephaly
Less common
Present with primary disruption in cranial proportion
Disproportion of the neurocranium and viscerocranium
B/L occipital flattening
B/L forehead bossing
Increased height of cranial vault
Associated weakness of neck musculature
Increased cranial width
Decreased cranial length
Increased cranial vault height
9. Scaphocephaly
Disproportion of the neurocranium and viscerocranium
B/L parietal flattening
Anterior forehead bossing
Posterior occipital bossing
Associated weakness of neck
musculature
Increased cranial length
Decreased cranial width
11. Factors for creating cranial deformities
Prenatal factors-
Deforming forces in utero- Restrictive in utero environments
Fetal constraints
Sustained abnormal positioning
Deforming forces during birth process- Vaginal deliveries
Cesarean deliveries
Postnatal factors-
Premature infants due to increased plasticity of the underdeveloped cranial structure
1. Sustained supine positioning in compliance with the AAP Back to sleep program
2. Sustained supine positioning in neonatal intensive care units
3. Sustained supine positioning during normal daily infant/caregiver routines
4. Congenital muscular torticollis
5. Neck muscle asymmetry
6. Unilateral neck involvement
7. Cranial hemivertebrae
12. Evaluation of cranial deformities
Degree of asymmetry
Degree of disproportion
Plasticity of bony structure
Amount of translation of bony plates
Cellular disruption and alterations in suture development
Soft tissue involvement and/or contributions from neck musculature
Genetic predisposition
Effect of neurocranial structure and alterations on adjacent viscerocranial
structure
13. Historical perspective
Intentional cranial deformation
Different cultures applied a variety of measures to alter the shape of infants
skull
Boards, vines, cloth bandages and even weight of stones were applied to
the head of the infants to create a culturally desired shape.
Early and sustained application of intentional and specific force would
produce long standing changes in cranial shape.
In 1979, clarren et al, reported that many infants were treated for many
different congenital or hereditory disorders of the brain, bone or sutures.
Cranial remolding orthoses were being used postoperatively and infants
diagnosed with nonsynostosis deformity treated with cranial orthosis and
treatment concept was based on intentional cranial deformation.
14. Cont…
In early to mid 1990 – significant increase in the no. of infants with
asymmetrical and disproportional skull deformities coincided with AAP
back to sleep program.
Haung et al, outlined specific anatomy of deformational plagiocephaly
versus unilateral lambdoid synostosis.
Asymmetry and unilteral occipital flattening in both condition
Parallelogram head shape in plagiocephaly and trapezoid shape in lambdoid
syndrome.
Anterior ear progression in plagicephaly and posterior ear progression in
lamdoid synostosis
With the increasing no. of infants with these deformities orthotics
management with cranial remolding orthosis was developed and refined.
15. Management
Cranial distortion in newborn is common and generally dissolved within the
first 12 weeks of life.
Early identification of cranial deformities creates the opportunity for
altering external forces.
Treatment recommendations-
1. Repositioning
2. Therapeutic efforts
3. Orthosis- a cranial deformity is considered for orthotic intervention when
the infants abnormal skull proportion remains or fails to improve despite
early intervention of repositioning and therapeutic efforts during the first
3 months after birth
16. Repositioning technique
Goal- better distribution of external forces acting on the developing skull.
Time- first 3months of life
Techniques =
Tummy time
Strategic positioning during diapering, feeding, carrying and handling
Limitation on time spent in car seats, carriers and swings
Positioning of nursery furniture relative to bright areas
17. Anthropometic evaluation
Anthrometric skull measurements establish a baseline for clinical
documentation of improvement or progression of the skull deformity.
Common clinical measurements-
1. Cranial circumference
2. Cranial base
3. Cranial width
4. Cranial length
5. Cranial vault
6. Orbitotragial depth
7. Cranial base measurements.
8. Cranial vault asymmetry
9. Orbitotragial depth asymmetry(OTDA)
10. CVAI
11. Cephalic index(CI)
12. Cranial base asymmetry(CBA)
18. Cranial circumference and cranial width measurements
Taken at the equator
Euryon to euryon(EU- EU)
23. Normative values of cranial development
2cm of circumferential growth/ month in the first 3 months
1 cm of circumferential growth/ month between 4 and 6 months
Approx 0.5 cm of circumferential growth/ month between 6 and 12 months
After 12 months cranial growth slows significantly
24. Therapy technique
Continued cranial deformation
Developmental delay
Weakness and tightness of neck musculature
Hypotonicity
Asymmetry of nuchal fold
Persistent positional preference
Limitations in active and passive neck ROM
25. Orthotic management
Indication- moderate to severe deformities
Disruption in cranial symmetry and/or proportion result from the application
external forces acting on developing cranial structure.
Deformation of the infant skull occurs in response to the amount , direction,
mode and frequency of the forces applied.
Temporomandibular jt. Or orbital alignment may be affected.
Function-
1. Presumes growth
2. Balance the static and dyanamic forces acting on the developing structure
to ensure functional competence of both the neurocranium and
viscerocranium.
26. Goal
Achieve maximum correction of the deformity,
Establish symmetry and/or proportion of the skull,
Provide stimulus to cranium growth,
Encourage passive expansion of the cranium.
27. General consideration for orthosis in pediatric population
1. Time of onset of condition
2. Duration of deforming forces
3. Degree of severity
4. Degree of correctability
5. Diagnosis/etiology
6. Remaining growth of physiological structures
7. Overall health of physiological structures
8. Developmental level
28. Examination
Patient history:-
Prenatal and postnatal factors
Birth history:-
Gestational age, Weight , Length, Fetal positioning, Delivery
Associated medical conditions:-
Skin sensivity, head shape at birth and age when head deformity was first
noted.
Developmental observation:- preferred sleeping postion, repositioning
efforts by caregivers, acquisition of developmental milestone
29. Cont….
Physical examination of the infants skull
and face
1. Visual observation from all angles
2. Manual palpation of cranial structure
Documentation of Asymmetrical and
displaced skull and fascial features
Nonvertical orientation of the head relative
to the trunk
Neck musculature
ROM
Digital photographs and anthrometric
measurements
30. Discussion with caregivers
An overview of orthotic treatment program
Determination of treatment goals and expectatations
Importance of supervised prone position
Casting or scanning process
Fitting and follow up schedule
Orthotic cleaning regimen
Wearing schedule
Signs indicating the need for adjustments
Situations requiring removal of the cranial remolding orthosis
31. Fabrication of cranial remolding orthosis
Step -1
Measurement procedure:-
Goal- to obtain an accurate model with identifiable anatomical landmarks
necessary for rectification and fabrication of custom CRO.
1. Casting- produce an accurate negetive model of infants head
2. Scanning- produce digital representation of infants head.
33. Step -2
Rectification-
Goal- to create a new model with greater symmetry and/ or proportion
than currently exists.
Modification- areas of flattening are expanded to allow for planned
growth and Areas of bossing are maintained to resist growth.
Various orthosis use slightly different rectification technique but basic
theory is same.
34. Cranial mapping instrument
Adapted from a bremer pediatric halo crown
Was developed to measure deformational head shapes.
The instrument measures
1. The position and amount of depression or flatness,
2. The amount of displacement,
3. The orientation of head shape within the instrument.
4. Allows the orthotist to create a blueprint and establish the predicted shape
of the skull after orthotic treatment.
35. Creating the blueprint
After a plaster impression of the infant's head is made, it is essential to
critique the positive model for quality and biomechanical accuracy.
The model must be assessed
1. to ensure that it represents the exact model of the cranium
2. to ensure that all anatomic positions and marks are captured.
The anthropometric data collected during the evaluation must be compared
with the cast
36. Procedure
Clean and remove excess plaster from the model.
Remove all ridges and unnatural bumps using smooth finishing.
The positive model must be free of plaster irregularities.
The indelible pencil marks are transferred and reinforced on the mold
37. Cont…
Mark the following bony prominences and landmarks:
1. Glabella (the center at which the eyebrows meet);
2. Tuberosity of the frontal bone (left and right);
3. Frontozygomatic bone (at the level of the tragus);
4. Pinna beginning from the anterior inferior lobule to the posterior inferior
lobule (called auricle or trumpet);
5. External occipital protuberance;
6. The inferior edge of occipital bone; and
7. Sagittal and coronal lines dividing the mold into quadrants.
38. Establish the trimlines
Mark the glabella and make a horizontal
line around the cast at the level of the
supra orbital margin (eyebrow) extending
to the superior edge of the pinna.
This serves as a primary reference
line for anterior trim lines.
40. Cont….
In the sagittal plane, draw a vertical line 1 cm lateral to the supraorbital
margin and another 1 cm distal to the frontozygomatic bone. These lines
connect to create the anterior trim line. The width of the temporal extension
is maintained with 0.5-cm clearance anterior to tragus. A width
approximately 3 to 3.5 cm seems to be appropriate to distribute any pressure
exerted at the temporal area. Draw another line starting from the
frontozygomatic line following the mark of pinna to the posterior inferior
lobule. The line terminates 12 mm distal to the inferior border of occipital
bone
42. Cont….
The posterior trimline is established by joining two points drawn with the
anatomic curvature to facilitate neck extension without impingement.
43. Length and Width Dimensions
Once the trimlines are established, measure the length and width dimensions
of the cast. Compare these measurements with the anatomic measurements
recorded in the craniometry form.
44. Establishing symmetry
Symmetry is an attribute of a shape, an exact correspondence of form on
opposite sides of a dividing line or plane.
Mild asymmetry is usually found in human craniofacial bones and is present
in both affected and unaffected groups. 2 The left and right side differences
occur in variable degrees and could affect appearance. Absolute symmetry
could be considered when each half of the skull is exactly the same, like in a
mirror image.
45. Establishing proportion (displacement and orientation)
Proportion is the relationship of various parts of the skull to the overall
whole.
Maintaining proportion of the skull is an essential element of cranial
molding therapy. a sense of proportion by using a simple cranial mapping
instrument is developed.
46. Cont….
The anterior and posterior center
pins are placed at marks of
glabella and occipital
protuberance and joined.
the lateral lines are joined at the
midline from the center of the
superior border of the left pinna
to the superior border of the right
pinna.
The geometric center of the
instrument is marked by length
and width lines. Quadrant II is
displaced laterally compared with
the geometric center .
The ear displacement is
measured from the centerline and
documented.
47. Craniometry form
It was developed to document the linear
measurements of the cranium.
The distance is measured from the inner
border of the craniometry mapping instrument
to the outer surface of the positive mold.
amount of asymmetry present in the mold.
Repeat the measurements at the glabella,
lateral one third of the eyebrow, ears, lateral
one third of occipital bone, and occipital
protuberance.
Make further notations regarding the skin
condition, muscle tightness, range of motion,
facial asymmetry, and any other relevant
information.
48.
49. Factors affecting modification specification
AGE OF THE INFANT
The skull expands as the brain grows so that normal head growth is a sign of
healthy brain growth.
The philosophy behind the cranial molding orthosis is that the brain and the
skull grow very quickly during the first year of life.
This growth curve is quite steep in the early months and then starts to level
off after 6 months of age.
The cranial molding orthosis is designed to take advantage of that rapid
growth. Therefore, the sooner the treatment is initiated, the better the result.
50. DEGREE OF SEVERITY
Degree of severity affects potential outcomes and protocols of the orthotic
treatment program. In general, moderate to severe deformities can be treated
satisfactorily with a cranial molding orthosis.
51. HEAD SHAPE
The cranial base forms the platform on which the rest of the skull grows and
attaches, and it provides and protects the crucial foramina through which the
brain connects to the face and the rest of the body.
variations in the shape of the human neurocranium are influenced by
variations in the shape of the neurocranium growth and endocranial
expansion driven by brain growth. During normal growth in humans, the
upper half of the neurocranium enlarges and the cranial growth assumes that
overall shape.
This integrated growth occurs through many processes, like sutural
expansion, deposition, and drift.
Length and width changes of the skull occur through coronally oriented and
sagittally oriented sutures.
52. Types of cranial remoulding orthoses
The design and application of a cranial remolding orthosis does not alter the
magnitude of the intrinsic brain growth but merely its direction.
1. Types- Active or dynamics and passive
2. Rigid or flexible
3. Hinged or circumferential
Most cranial orthoses are passive.
Active part - ongoing growth of the infants brain and skull and the extent to
which orthotist is involved in directing head growth.
Different design variations include-
1. Variety of plastics and lining materials
2. Trimlines
3. Strapping
4. Construction of the inner liner
53. Postoperative use of cranial orthosis-
Goal- to maintain and enhance surgical procedure.
To allow for reduction of swelling.
To allow initial healing of suture site.
Protective,
preventing inadverent trauma to the skull.
To discourage growth along specific suture lines.
To maintain or improve the corrected head shape.
54.
55. Principle of cranial remoulding orthosis
to resist growth in undesired areas and directions and
promotes growth in desired areas and directions.
56. Factors for improvements in CRO
Effective fit of the orthosis
Treatment provided during periods of cranial growth
Compliance with wearing schedules.
Age
Design appropriate follow up
57. Effective fit
maintaining good suspension with room for growth,
appropriate trims,
no redness after 15 minutes' wear time,
control of rotation.
58. Age at the initiation of treatment
Cranial orthoses are approved for use an infants , aged 3 to 6 months.
Moderate to severe deformities who have not shown improvement after
atleast 6 to 8 weeks of repositioning( less than 6 months of age)
Best results have been observed in infants with 4 to 12 months age as a
result of greater malleability of the skull and rapid brain growth during that
period.
59. Wearing duration
Last from 3 to 6 months
Factors of length and the results of treatment program-
1. Biomechanics of skull growth
2. Neuromuscular maturation
3. Chronological age at initiation of treatment
4. Severity of deformity
5. Type of cranial deformity
6. Presence or absence of congenital muscular torticollis
7. Other neck weakness or asymmetry
8. Cranial growth pattern
60. Effect of torticollis on average of length of treatment
If torticollis is resolved it is unlikely to affect the duration of cranial orthosis
treatment.
If unresolved, then duration of cranial orthosis treatment should be
increased by 2 to 4 weeeks as a prophylactic measures.
61. Wearing schedule
May be immediate or implemented over a short period of time.
Depends on-
1. developmental level
2. Fit of the orthosis
3. Regional medical practices
Termination of treatment- an acceptable of improvements in symmetry
and/or proportion has been obtained.
Average wearing schedule:- 22 to 23 hours per day for 6 weeks to 6 months.
Having a full time schedule captures the redirection of growth to the
fullest.
62. Follow up
To evaluate acceptable cranial growth patterns and dimensions and
documents the maintenance of orthotic outcomes.
To ensure proper fit and function of the orthosis
Document changes in anthropometric measurements
Performs necessary adjustments and modification to the orthosis
Verify compliance and understanding of the treatment program
Provide guidance and support to caregivers
64. Craniosynostosis
The second most common group of infants with plagiocephaly is infants
diagnosed with craniosynostosis presenting as early closure of one or more
cranial sutures.
In any case, infants with asymmetrical head shapes will undergo definitive
diagnostic testing to identify the cause of the deformation.
DIAGNOSIS:-
Physical examination
X-ray
Computed tomography (CT) scan,
magnetic resonance imaging (MRI).
65. Treatment
SURGERY :- Performed between 3 and 9 months of age.
ORTHOSES:- Infants with craniosynostosis are contraindicated for cranial
remolding orthoses until the affected suture(s) have been surgically
addressed.
Orthoses can be used postoperatively for protection of the surgical site
and/or continued remodeling.
66. Treating Torticollis
Torticollis is the third most common musculoskeletal deviation in the
newborn after dislocated hips and clubfeet.
80-85% of all infants with positional plagiocephaly present with some
degree of torticollis caused by an asymmetrical tightness of the
sternocleidomastoid muscle.
The overall management of positional plagiocephaly requires the
coordinated treatment of torticollis
1. to prevent the child from continuing to rest on the same area of posterior
cranial flatness
2. to develop bilateral head, neck, and trunk symmetry.
67. TREATMENT
Provided before, during, and after the orthotic treatment program.
Infants under 3 months of age :-
1. Passive stretch to the sternocleidomastoid, upper trapezius, and ipsilateral
trunk muscles.
2. Specific handling and positioning instructions are provided
3. Supervised "tummy time" is used to provide active and passive stretch to
the neck musculature.
68. CONT…
The child reaches 4 to 6 months of age:-
EXECRCISES:-
1. Stretch and massage to the affected muscle is provided .
2. Encourage age-appropriate developmental exercises.
3. emphasize head and neck mobility,
4. equal weight bearing, and midline activities
ORTHOSES:- the cranial orthosis may be removed during these exercises.
Occasionally, a cervical orthosis may be needed to augment the orthotic
treatment program. Cervical orthoses block lateral flexion to the affected
side and prevent the head from rotating to the opposite shoulder.
Weaning time- Usually the orthosis is worn before orthotic treatment is
initiated or whenever the cranial orthosis is not in place.
69. Current research
A systematic review of literature support the need for orthotic treatment of
moderate and severe skull deformity.
1988, Rekate found that prenatal and postnatal factors contributed in skull
deformities and he also found three primary treatment options – observation
and repositioning, mechanical intervention and surgery.
A review by Lima in 2004 reiterated the lack of consistent terminology and
definitions. Difficulty in establishing the incidence of skull deformities in
young infants remained, although many citations suggested common risk
factors and early intervention.