2. HYDRANENCEPHALY ETIOLOGY Occlusion of Bilateral ICA Supraclinoid part or MCA on either side. Infection sequael Diffuse hypoxic ishemicsequael. Thromboblastic material from the deceased co twin DIAGNOSTIC FEATURES Cortical mantle abscent Normal brain parenchyma is liquefied and lined by leptomeninges. Basal ganglia / brain stem intact ( may be atrophic). Cerebellum intact in most of the cases. (Primarily structures supplied with Posterior circulation).
3. OCCLUSION OF SUPRACLIONID ICA -ACL / MCL LEADING TO LIQUEFACTION OF BRAIN IN THE MENTIONED ARTERIAL TERRITORIES SPARING OF PCL AND TERRITORY SUPPLIE.D BY IT
4. FALX INTACT / HYPOPLASTIC CEREBELLUM INTACT BRAIN STEM – INTACT / HYPOPLASTIC THALAMI – USUALLY INTACT. NO CORTICAL MANTLE BRAIN STEM INTACT THALAMI INTACCT LIQUEFIED BRAIN WITH LEPTOMENINGES LINING
5. DIFFERENTIALS In all the mentioned cases cortical mantle is preserved. Hydrancephaly – Liquefied brain lined with leptomeninges. Hydrocephalus : Csf lining is of ependyma. DIFFERENTIALS Extreme Hydrocephalus Alobarholoprosencephaly Severe form of porencephaly
6. Hydro is water compressing the brain, as noted on the brain.Hydra is the existence of water, where brain matter is non existent. Most patients do however have a brain stem allowing them to function normally. The prognosis is that a slim percent will see their first birthday. The majority of babies born with this disorder, expire.
7. PRESENT CASE 2 & ½ MONTH MALE CHILD WITH MACROCRANIA
