Syndromes Related To Romavable Rehabilitation

2. Streeter’s Syndrome
(Ectodermal Dysplasia)
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 Definition : ED is groap of abnormalities in ectodermal
structure ( hair – skin – salivary gland – teeth)
 symptomes on teeth : congenital abscent of teeth
(mostly permanent ) & peg shape teeth with defective
enamel
 TTT :multiple denture replacement or cosmotic ttt

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4. Papillion lefever syndrome
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 Definition :Papillon–Lefèvre syndrome (PLS)is an
autosomal recessive genetic disorder (Mutations in the
cathepsin C gene )
 Characterstics:
PLS is characterized by periodontitis and palmoplantar
keratoderma. The severe destruction of periodontium results
in loss of most primary teeth by the age of 4 and most
permanent teeth by age 14. Hyperkeratosis of palms and
soles of feet appear in first few years of life.

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7. Down syndrome
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Definition:
down syndrome also known as trisomy 21, is
a genetic disorder caused by replication of
chromosome 21
Characteristics:
Mental retardation
 Mild to moderate disability
Facial feature
 delayed eruption
 Deciduous….4-5.years.
 Permanent anterior…..8-9 years

8. Down syndrome
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 Small crowns & short roots and missing teeth
 Enlarged tongue
 V-shaped palate, soft palate insufficiency
 Deficient maxilla , crowded upper teeth , cross bite
 Gum disease, high caries risk

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13. Cherubism
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 Definition :rare autosomal dominant disease of the
maxilla and mandible.
 Characteristics:
 enlarged face due to Osteoclastic and osteoblastic
remodeling contributes to the change of normal bone
to fibrous tissue
 The sponge-like bone formations lead to early tooth
loss and permanent tooth eruption problems.

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 ttt : Surgical bone grafting & prothetic rehabilitation for
missing teeth
Cherubism

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facial appearance of 37 years old
woman diagnosed with cherubism

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19. Kelly syndrome
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 Definition :Combination syndrome (dental origin)
commonly occurs in patients with completely
edentulous maxilla opposed by a bilateral distal
extension partial denture.
 Characteristics: loss of bone from the anterior
edentulous maxilla with flabby tissues and super-eruption
of unopposed mandibular anterior teeth &
overgrowth of the tuberosities

20. ttt
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 Prevention phase :Presevation of posterior occlusion
and avoidance of anterior hyperfunction are
considered the primary treatment
 Prothetic phase of ttt
 Ex : Implant supported prothesis to distribute
occlusal force or upperCD & lowerRPD with
precautions

21. Case Report
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 A 73-year-old male patient .The patient's chief complaints were
inadequate retention of maxillary complete denture and inability to
chew comfortably.On examination, the patient had an edentulous
maxilla and nine natural mandibular anterior teeth . Clinically, the
patient displayed anterior bone loss and flabby tissue of
the maxillary ridge, overgrowth of the maxillary
tuberosities, and over-erupted mandibular anterior teeth
. The patient rejected any surgery and implant therapy due to
financial considerations. The patient agreed to have a new complete
denture and a mandibular removable partial denture

22. Case Report (continue)
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 minimum anterior contact for reducing further bone
loss caused by hyperfunction of anterior teeth.
Balanced occlusion was indicated for this case to
assure an even distribution of occlusal force and prevent
occlusal interferences on the residual ridge.

23. Case Report (continue)
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 preliminary impression of the maxillary and mandibular
arches was made with irreversible hydrocolloid
materials and poured with dental stone. A custom tray
was fabricated for the maxillary complete denture
impression and a wax relief was applied to the
anterior flabby tissue area. A green modeling compound
was then used to obtain accurate denture border
position and seal. The definitive impression of the
maxillary arch was made with vinyl polysiloxane
impression material. After prescrip, both casts were
remounted, adjusted, and polished.

24. Case Report (continue)
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 At a subsequent appointment, the finished prostheses
were delivered and minimal occlusal adjustment was
needed. The patient was pleased with their appearance
and chewing ability. A maintenance program including
oral hygiene instruction and prosthesis home care was
established. At the 18-month maintenance visit, no
complications were observed.

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