MariaCarmela L. Domocmat, RN, MSN
Intructor
Northen LuzonAdventistCollege 1
◾ Talipes
◾ Congenital hip dysplasia
◾ a congenital deformity in which the foot is
twisted out of shape or position;
◾ Aka: clubfoot
MariaCarmela L. Domocmat, RN, MSN 4
Dorland'sMedical Dictionaryfor Health Consumers. © 2007 by Saunders, an imprint of Elsevier, Inc. All rights reserved.
◾ dorsiflexion - t. calca´neus
◾ plantar flexion - t. equi´nus
◾ abducted and everted -t.val´gus or flatfoot
◾ abducted and inverted - t. va´rus
◾ various combinations
 t. calcaneoval´gus
 t. calcaneova´rus
 t. equinoval´gus
MariaCarmela L. Domocmat, RN, MSN 5
 t. equinova´rus Dorland's MedicalDictionaryfor Health Consumers. © 2007 by Saunders, an
imprint of Elsevier, Inc. All rights reserved.
◾ t. calcaneoval´gus
 the foot is turned outwards with the toes pointing
upwards
◾ t. calcaneova´rus
 the foot points inwards and up
◾ t. equinoval´gus
 the foot points outwards and down
◾ t. equinova´rus
 most common type
 foot is fixed in plantar flexion (downward) and
deviated medially (inward)
MariaCarmela L. Domocmat, RN, MSN 6
http://img.tfd.com/dorland/thumbs/talipes.jpg
MariaCarmela L. Domocmat, RN, MSN 7
http://www.abdn.ac.uk/~gen155/graphics/clubfoot.jpeg
http://www.fpnotebook.com/_media/Ortho
PedsFootCF.jpg
MariaCarmela L. Domocmat, RN, MSN 8
http://1.bp.blogspot.com/_IZV_l47MkXQ/TRpGEJogmHI/AAAAAAAAAGw/X1VQqO
DtJG4/s1600/child_foot_clubfoot_intro01.jpg
MariaCarmela L. Domocmat, RN, MSN 9
o The true etiology of congenital clubfoot is
unknown
o Extrinsic associations include
 Teratogenic agents (eg, sodium aminopterin)
 Oligohydramnios
 Congenital constriction rings
MariaCarmela L. Domocmat, RN, MSN 10
o Genetic associations include
o mendelian inheritance (eg, diastrophic dwarfism;
o autosomal recessive pattern of clubfoot inheritance).
o Cytogenetic abnormalities (eg, congenital talipes
equinovarus [CTEV]) can be seen in syndromes
involving chromosomal deletion.
MariaCarmela L. Domocmat, RN, MSN 11
o Talipes may be positional or structural.
 Positional talipes is caused by abnormal pressures
compressing the foot while it's developing, as a result
of its position in the womb.
 Structural talipes is a more complex condition and
probably caused by a combination of factors, such as
a genetic predisposition
MariaCarmela L. Domocmat, RN, MSN 12
o deformity is readily apparent at birth
o can be detected antenatally during the routine
development ultrasound scan around 20 weeks.
o X-rays may be needed to confirm diagnosis.
MariaCarmela L. Domocmat, RN, MSN 13
o treatment is most successful when started
early in infancy because delay causes muscles
and bones of legs to develop abnormally,
with shortening of tendons
MariaCarmela L. Domocmat, RN, MSN 14
 gentle, manipulation of foot with casting
 done every few days for 1 to 2 weeks then at 1- to 2-week
intervals
 Ponseti’s Method of treatment
MariaCarmela L. Domocmat, RN, MSN 15
MariaCarmela L. Domocmat, RN, MSN 16
 involves serial manipulation and plaster casting of the
clubfoot.
 The ligaments and tendons of the foot are gently
stretched with weekly, gently manipulations.
 Aplaster cast is then applied after each weekly
sessions to retain the degree of correction obtained
and to soften the ligaments. Thereby, the displaced
bones are gradually brought into the correct
alignment.
 Four to five long leg (from the toes to the hip) are
applied with the knee at a right angle.
MariaCarmela L. Domocmat, RN, MSN 17
LONG LEG CAST DENNIS BROWNSPLINT
http://www2.massgeneral.org/ORTHO/DennisBrownBrace.gif
http://www2.massgeneral.org/ORTHO/BabyCast.gif
MariaCarmela L. Domocmat, RN, MSN 18
MariaCarmela L. Domocmat, RN, MSN 19
◾ MakingA Difference:Caring ForClubfoot at
the Sinai Hospital of Baltimore at
http://www.youtube.com/watch?v=Rmkrrvw
MH4A&feature=player_embedded#!
MariaCarmela L. Domocmat, RN, MSN 20
◾done if nonsurgical treatment not effective
◾tight ligaments released
◾tendons lengthened or transplanted
◾Other surgical treatments
- circumferential release: "cincinati incision"
- Goldner four quadrant approach:
- medial release
- posterior release
- posteromedial release
- tendon transfers
MariaCarmela L. Domocmat, RN, MSN 21
◾extended medical supervision is required
 bcoz there is a tendency for this deformity to recur
(considered cured when the child is able to wear
normal shoes and walk properly)
◾care emphasizes muscle reeducation (by
manipulation) and proper walking
MariaCarmela L. Domocmat, RN, MSN 22
◾heels and soles of braces or shoes
prescribed following correction must be
kept in repair
◾corrective shoes may have sole and heel lifts
on lateral border to maintain proper
positioning
MariaCarmela L. Domocmat, RN, MSN 23
 Approximately 50-60% of club feet in newborns
can be corrected non-operatively.
 About 20% of infants requiring surgery need
further surgery at a later stage.
MariaCarmela L. Domocmat, RN, MSN 24
MariaCarmela L. Domocmat, RN, MSN 25
MariaCarmela L. Domocmat, RN, MSN 26
 imperfect development of hip –can affect
femoral head, acetabulum, or both
 head of femur does not lie deep enough within
the acetabulum and slips out on movement
 occurs in females 7 times more often than males
MariaCarmela L. Domocmat, RN, MSN 27
MariaCarmela L. Domocmat, RN, MSN 28
o acetabular dysplasia
 mildest form
 femoral head remains in acetabulum
o subluxation
 most common form
 femoral head partially displaced
o dislocation
 femoral head not in contact with acetabulum
 displaced posteriorly and superiorly
MariaCarmela L. Domocmat, RN, MSN 29
o limitation in abduction of leg on affected
side
o asymmetry of gluteal, popliteal, and thigh
folds
o Waddling gait and lordosis when child
begins to walk
MariaCarmela L. Domocmat, RN, MSN 30
MariaCarmela L. Domocmat, RN, MSN 31
◾ With child in a
supine position,
the right knee
on the side of
the subluxation
appears lower
than the left
because of
malposition of
the femur head.
MariaCarmela L. Domocmat, RN, MSN 32
◾ infant on a supine position.
◾ Doctor abducts the hips by moving the bent
hips and knees apart.
◾ If the hip feels like it can be pushed out the
back of the socket, this is considered
abnormal.
◾ This is called a positive Barlow'sTest and is a
sign of instability in the hip.
MariaCarmela L. Domocmat, RN, MSN 33
◾ As the hip is abducted further, the doctor
might feel the ball portion (the femoral head)
slide forward as it slips back into the socket.
◾ Or audible click when abducting and
externally rotating hip on affected side:
MariaCarmela L. Domocmat, RN, MSN 34
MariaCarmela L. Domocmat, RN, MSN 35
⦿ directed toward enlarging and deepening the
acetabulum by placing the head of femur within the
acetabulum and applying constant pressure
⦿ proper positioning: legs slightly flexed and abducted
⦿ Surgical Ix
MariaCarmela L. Domocmat, RN, MSN 36
o proper positioning: legs slightly flexed and
abducted
 Pavlik harness
 Frejka pillow: a pillow splint that maintains
abduction of legs
 Bryant’s traction
 Spica cast
 Closed reduction
MariaCarmela L. Domocmat, RN, MSN 37
◾ Hip abduction splint
◾ holds the hips in an
abduction position,
forcing the femur
head into the
acetabulum.
MariaCarmela L. Domocmat, RN, MSN 38
MariaCarmela L. Domocmat, RN, MSN 39
http://www.orthopediatrics.com/binary/org/ORTHOPEDIATRICS/images/hi
pimages/child_hip_devel_dysp_treatment01.jpg
MariaCarmela L. Domocmat, RN, MSN 40
http://www.lpch.org/media/images/c
onditions/ei_0239.gif
MariaCarmela L. Domocmat, RN, MSN 41
MariaCarmela L. Domocmat, RN, MSN 42
◾ A hip abduction cast for correction of
subluxation of the hip.
MariaCarmela L. Domocmat, RN, MSN 43
MariaCarmela L. Domocmat, RN, MSN 44
MariaCarmela L. Domocmat, RN, MSN 45
http://isakssonsgummifabrik.com/pics/babyfront.jpg
MariaCarmela L. Domocmat, RN, MSN 46
 open reduction with casting
 derotational osteotomy
 Pelvic osteotomies
MariaCarmela L. Domocmat, RN, MSN 47
◾ femur is cut and rotated to make it easier to
keep the femoral head inside the acetabulum.
◾ When this procedure is done, the soft tissues
loosen up and the forces of the muscles tend to
keep the femoral head reduced.
◾ Once again, the child is put in a spica cast for
several months while the bone heals.
◾ ACT scan may be used to confirm successful
reduction before removing the cast.
MariaCarmela L. Domocmat, RN, MSN 48
MariaCarmela L. Domocmat, RN, MSN 49
◾ for children older than 18 months which may require
additional surgery to change the acetabulum
(socket) in addition to the femur (thighbone)
 The problem has been present longer and the anatomy has grown
more distorted over the longer period of time.
MariaCarmela L. Domocmat, RN, MSN 50
MariaCarmela L. Domocmat, RN, MSN 51
◾ Several different types of osteotomies are used to
tilt the acetabulum in a more horizontal angle to the
floor. By doing this, the femoral head is less likely to
slide up and out of the socket with weightbearing.
◾ Types : Steele osteotomy;Salter osteotomy;
Pemberton osteotomy
MariaCarmela L. Domocmat, RN, MSN 52
◾ This can stop the femoral head from sliding
up and out of the socket.
◾ Over time this shelf of bone above the
acetabulum remodels and forms a deeper
acetabulum.
◾ the bone of the pelvis just above the
acetabulum is cut to allow the bone to slide
out and form a new roof over the hip joint.
MariaCarmela L. Domocmat, RN, MSN 53
MariaCarmela L. Domocmat, RN, MSN 54
◾ uses a bone graft placed just above the hip
joint to create a new, wider roof, or shelf over
the acetabulum.
◾ This keeps the femoral head from sliding up
and out of the socket and, as it heals, makes a
larger weightbearing surface to spread out
the weight that needs to be transferred from
the femoral head to the acetabulum and
pelvis.
MariaCarmela L. Domocmat, RN, MSN 55
MariaCarmela L. Domocmat, RN, MSN 56
◾ not as common
◾ the entire acetabulum is cut free of the pelvis
and moved or dialed at the best angle and
then allowed to heal in that position.
MariaCarmela L. Domocmat, RN, MSN 57
o Same with other clients with cast and
braces; pre- and post-op care
o Transportation and positioning
 use wagon or stroller with back flat or mechanic’s
creeper
 protect child from falling when positioned
 never pick up child by the bar between the legs of
cast (use two people to provide adequate body
support if necessary)
MariaCarmela L. Domocmat, RN, MSN 58
◾ A patient's guide to developmental dysplasia of the hip in children
retrieved on September 4, 2011 at
http://www.orthopediatrics.com/docs/Guides/dysplasia.html
◾ MassachusetsGeneral Hospital. Pediatric orthopaedic ailments:
Clubfoot. Retrieved onSeptember 4, 2011 at
http://www2.massgeneral.org/ORTHO/ClubFoot.htm
◾ Saxton, Nugent, and Pelikan. (2006). Mosby’s comprehensive
review of nursing [18th ed].St. Louis: Mosby
◾ Talipes Equinovarus. Retrieved onSeptember 4, 2011 at
http://www.patient.co.uk/doctor/Club-Foot.htm
◾ Wheeless’ Textbook of Orthopaedics.Talipes
equinovarus/Clubfoot Retrieved on September 4, 2011 at
http://www.wheelessonline.com/ortho/talipes_equinovarus_clubf
oot
MariaCarmela L. Domocmat, RN, MSN 59

congenitalskeletalmalformationscld-120308073040-phpapp02.pptx

  • 1.
    MariaCarmela L. Domocmat,RN, MSN Intructor Northen LuzonAdventistCollege 1
  • 2.
  • 4.
    ◾ a congenitaldeformity in which the foot is twisted out of shape or position; ◾ Aka: clubfoot MariaCarmela L. Domocmat, RN, MSN 4 Dorland'sMedical Dictionaryfor Health Consumers. © 2007 by Saunders, an imprint of Elsevier, Inc. All rights reserved.
  • 5.
    ◾ dorsiflexion -t. calca´neus ◾ plantar flexion - t. equi´nus ◾ abducted and everted -t.val´gus or flatfoot ◾ abducted and inverted - t. va´rus ◾ various combinations  t. calcaneoval´gus  t. calcaneova´rus  t. equinoval´gus MariaCarmela L. Domocmat, RN, MSN 5  t. equinova´rus Dorland's MedicalDictionaryfor Health Consumers. © 2007 by Saunders, an imprint of Elsevier, Inc. All rights reserved.
  • 6.
    ◾ t. calcaneoval´gus the foot is turned outwards with the toes pointing upwards ◾ t. calcaneova´rus  the foot points inwards and up ◾ t. equinoval´gus  the foot points outwards and down ◾ t. equinova´rus  most common type  foot is fixed in plantar flexion (downward) and deviated medially (inward) MariaCarmela L. Domocmat, RN, MSN 6
  • 7.
  • 8.
  • 9.
  • 10.
    o The trueetiology of congenital clubfoot is unknown o Extrinsic associations include  Teratogenic agents (eg, sodium aminopterin)  Oligohydramnios  Congenital constriction rings MariaCarmela L. Domocmat, RN, MSN 10
  • 11.
    o Genetic associationsinclude o mendelian inheritance (eg, diastrophic dwarfism; o autosomal recessive pattern of clubfoot inheritance). o Cytogenetic abnormalities (eg, congenital talipes equinovarus [CTEV]) can be seen in syndromes involving chromosomal deletion. MariaCarmela L. Domocmat, RN, MSN 11
  • 12.
    o Talipes maybe positional or structural.  Positional talipes is caused by abnormal pressures compressing the foot while it's developing, as a result of its position in the womb.  Structural talipes is a more complex condition and probably caused by a combination of factors, such as a genetic predisposition MariaCarmela L. Domocmat, RN, MSN 12
  • 13.
    o deformity isreadily apparent at birth o can be detected antenatally during the routine development ultrasound scan around 20 weeks. o X-rays may be needed to confirm diagnosis. MariaCarmela L. Domocmat, RN, MSN 13
  • 14.
    o treatment ismost successful when started early in infancy because delay causes muscles and bones of legs to develop abnormally, with shortening of tendons MariaCarmela L. Domocmat, RN, MSN 14
  • 15.
     gentle, manipulationof foot with casting  done every few days for 1 to 2 weeks then at 1- to 2-week intervals  Ponseti’s Method of treatment MariaCarmela L. Domocmat, RN, MSN 15
  • 16.
  • 17.
     involves serialmanipulation and plaster casting of the clubfoot.  The ligaments and tendons of the foot are gently stretched with weekly, gently manipulations.  Aplaster cast is then applied after each weekly sessions to retain the degree of correction obtained and to soften the ligaments. Thereby, the displaced bones are gradually brought into the correct alignment.  Four to five long leg (from the toes to the hip) are applied with the knee at a right angle. MariaCarmela L. Domocmat, RN, MSN 17
  • 18.
    LONG LEG CASTDENNIS BROWNSPLINT http://www2.massgeneral.org/ORTHO/DennisBrownBrace.gif http://www2.massgeneral.org/ORTHO/BabyCast.gif MariaCarmela L. Domocmat, RN, MSN 18
  • 19.
  • 20.
    ◾ MakingA Difference:CaringForClubfoot at the Sinai Hospital of Baltimore at http://www.youtube.com/watch?v=Rmkrrvw MH4A&feature=player_embedded#! MariaCarmela L. Domocmat, RN, MSN 20
  • 21.
    ◾done if nonsurgicaltreatment not effective ◾tight ligaments released ◾tendons lengthened or transplanted ◾Other surgical treatments - circumferential release: "cincinati incision" - Goldner four quadrant approach: - medial release - posterior release - posteromedial release - tendon transfers MariaCarmela L. Domocmat, RN, MSN 21
  • 22.
    ◾extended medical supervisionis required  bcoz there is a tendency for this deformity to recur (considered cured when the child is able to wear normal shoes and walk properly) ◾care emphasizes muscle reeducation (by manipulation) and proper walking MariaCarmela L. Domocmat, RN, MSN 22
  • 23.
    ◾heels and solesof braces or shoes prescribed following correction must be kept in repair ◾corrective shoes may have sole and heel lifts on lateral border to maintain proper positioning MariaCarmela L. Domocmat, RN, MSN 23
  • 24.
     Approximately 50-60%of club feet in newborns can be corrected non-operatively.  About 20% of infants requiring surgery need further surgery at a later stage. MariaCarmela L. Domocmat, RN, MSN 24
  • 25.
  • 26.
  • 27.
     imperfect developmentof hip –can affect femoral head, acetabulum, or both  head of femur does not lie deep enough within the acetabulum and slips out on movement  occurs in females 7 times more often than males MariaCarmela L. Domocmat, RN, MSN 27
  • 28.
  • 29.
    o acetabular dysplasia mildest form  femoral head remains in acetabulum o subluxation  most common form  femoral head partially displaced o dislocation  femoral head not in contact with acetabulum  displaced posteriorly and superiorly MariaCarmela L. Domocmat, RN, MSN 29
  • 30.
    o limitation inabduction of leg on affected side o asymmetry of gluteal, popliteal, and thigh folds o Waddling gait and lordosis when child begins to walk MariaCarmela L. Domocmat, RN, MSN 30
  • 31.
  • 32.
    ◾ With childin a supine position, the right knee on the side of the subluxation appears lower than the left because of malposition of the femur head. MariaCarmela L. Domocmat, RN, MSN 32
  • 33.
    ◾ infant ona supine position. ◾ Doctor abducts the hips by moving the bent hips and knees apart. ◾ If the hip feels like it can be pushed out the back of the socket, this is considered abnormal. ◾ This is called a positive Barlow'sTest and is a sign of instability in the hip. MariaCarmela L. Domocmat, RN, MSN 33
  • 34.
    ◾ As thehip is abducted further, the doctor might feel the ball portion (the femoral head) slide forward as it slips back into the socket. ◾ Or audible click when abducting and externally rotating hip on affected side: MariaCarmela L. Domocmat, RN, MSN 34
  • 35.
  • 36.
    ⦿ directed towardenlarging and deepening the acetabulum by placing the head of femur within the acetabulum and applying constant pressure ⦿ proper positioning: legs slightly flexed and abducted ⦿ Surgical Ix MariaCarmela L. Domocmat, RN, MSN 36
  • 37.
    o proper positioning:legs slightly flexed and abducted  Pavlik harness  Frejka pillow: a pillow splint that maintains abduction of legs  Bryant’s traction  Spica cast  Closed reduction MariaCarmela L. Domocmat, RN, MSN 37
  • 38.
    ◾ Hip abductionsplint ◾ holds the hips in an abduction position, forcing the femur head into the acetabulum. MariaCarmela L. Domocmat, RN, MSN 38
  • 39.
  • 40.
  • 41.
  • 42.
  • 43.
    ◾ A hipabduction cast for correction of subluxation of the hip. MariaCarmela L. Domocmat, RN, MSN 43
  • 44.
  • 45.
  • 46.
  • 47.
     open reductionwith casting  derotational osteotomy  Pelvic osteotomies MariaCarmela L. Domocmat, RN, MSN 47
  • 48.
    ◾ femur iscut and rotated to make it easier to keep the femoral head inside the acetabulum. ◾ When this procedure is done, the soft tissues loosen up and the forces of the muscles tend to keep the femoral head reduced. ◾ Once again, the child is put in a spica cast for several months while the bone heals. ◾ ACT scan may be used to confirm successful reduction before removing the cast. MariaCarmela L. Domocmat, RN, MSN 48
  • 49.
  • 50.
    ◾ for childrenolder than 18 months which may require additional surgery to change the acetabulum (socket) in addition to the femur (thighbone)  The problem has been present longer and the anatomy has grown more distorted over the longer period of time. MariaCarmela L. Domocmat, RN, MSN 50
  • 51.
  • 52.
    ◾ Several differenttypes of osteotomies are used to tilt the acetabulum in a more horizontal angle to the floor. By doing this, the femoral head is less likely to slide up and out of the socket with weightbearing. ◾ Types : Steele osteotomy;Salter osteotomy; Pemberton osteotomy MariaCarmela L. Domocmat, RN, MSN 52
  • 53.
    ◾ This canstop the femoral head from sliding up and out of the socket. ◾ Over time this shelf of bone above the acetabulum remodels and forms a deeper acetabulum. ◾ the bone of the pelvis just above the acetabulum is cut to allow the bone to slide out and form a new roof over the hip joint. MariaCarmela L. Domocmat, RN, MSN 53
  • 54.
  • 55.
    ◾ uses abone graft placed just above the hip joint to create a new, wider roof, or shelf over the acetabulum. ◾ This keeps the femoral head from sliding up and out of the socket and, as it heals, makes a larger weightbearing surface to spread out the weight that needs to be transferred from the femoral head to the acetabulum and pelvis. MariaCarmela L. Domocmat, RN, MSN 55
  • 56.
  • 57.
    ◾ not ascommon ◾ the entire acetabulum is cut free of the pelvis and moved or dialed at the best angle and then allowed to heal in that position. MariaCarmela L. Domocmat, RN, MSN 57
  • 58.
    o Same withother clients with cast and braces; pre- and post-op care o Transportation and positioning  use wagon or stroller with back flat or mechanic’s creeper  protect child from falling when positioned  never pick up child by the bar between the legs of cast (use two people to provide adequate body support if necessary) MariaCarmela L. Domocmat, RN, MSN 58
  • 59.
    ◾ A patient'sguide to developmental dysplasia of the hip in children retrieved on September 4, 2011 at http://www.orthopediatrics.com/docs/Guides/dysplasia.html ◾ MassachusetsGeneral Hospital. Pediatric orthopaedic ailments: Clubfoot. Retrieved onSeptember 4, 2011 at http://www2.massgeneral.org/ORTHO/ClubFoot.htm ◾ Saxton, Nugent, and Pelikan. (2006). Mosby’s comprehensive review of nursing [18th ed].St. Louis: Mosby ◾ Talipes Equinovarus. Retrieved onSeptember 4, 2011 at http://www.patient.co.uk/doctor/Club-Foot.htm ◾ Wheeless’ Textbook of Orthopaedics.Talipes equinovarus/Clubfoot Retrieved on September 4, 2011 at http://www.wheelessonline.com/ortho/talipes_equinovarus_clubf oot MariaCarmela L. Domocmat, RN, MSN 59