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Telescopic nails in Osteogenesis Imperfecta
1. Telescopic Nails
in Osteogensis Imperfecta
Shady Mahmoud
Assistant lecturer
Orthopaedic surgery department - Ain
Shams University
2. What is OI?
A hereditary disease (AD or AR) caused in 70% of cases
by a mutation of 1 or 2 genes (COL1A1 and COL1A2),
which encode type 1 collagen (1)
It is approximately 1 in 10,000 live births
The major clinical features of OI are:
Bone fragility with or without multiple fractures,
osteopenia, and skeletal deformities of long bones
Spine deformity in the form of scoliosis in 39% to 80%
Craniocervical abnormalities are also associated as
basilar invagination, basilar impression, and platybasia (2)
4. How to treat bone fractures and
deformities?
Prevention:
Pamidronate, has shown its efficacy in
reducing fracture rates and pain,
enhancing bone density parameters,
and improving the quality of life in these
children. (2)
So, they start standing at a
younger age than the past (3)
However, it
has no effect on preexisting bone
deformities (2)
5. Treatment:
Most fractures can be treated by
immobilization especially if < 2 years.
However, surgical treatment is
sometimes required (long bones in > 2
years) (3)
6. What not to do?
Plates
Screw fixation in fragile bone is poor
Plates create stress risers and fractures above
and below the plate are likely to occur
7. Skeletal traction
- The traction pin may cut
through the bone
- Damage to the growth plate
may occur
9. Solid
Rush pins or K wires
Sofield - Millar procedure :
multiple realignment (“shish
kebab”) osteotomies over a
nontelescopic intramedullary rod
(4)
The revision rate is high as 73%,
and complications such as rod
migration are common. (4)
So, it is better used in
adolescents and patients with
limited growth potential (popcorn
physis) (3)
10. Telescopic
4 main types are developed:
Bailey-Dubow, Sheffield, Fassier-Duval, and
interlocking telescoping rods
These rods have a female hollow nail anchored
in the proximal epiphysis of the long bone and a
male solid nail anchored to the distal epiphysis.
They are elongated as the child grow. So, less
revision rates compared to solid (4)
11. According to a study (5)
, Mobility status and bone
growth were better in telescopic than in solid
rods.
The overall implant related complication rate
was 28.6% in telescoping in comparison to
68.4% in solid ones. (5)
Rod migration was twice more common in solid.
Bone outgrowing the rod and breakage of rods
with fracture was seen in solid rods only.
The three-year survival rate for telescoping rods
was 92.9% in contrast to 68.4% for solid rods.
The reoperation rate was 7.2% in telescoping
and 31.6% in solid rods. (5)
12. Rod diameter:
Larger diameter gives more stability but causes bone loss
around the rod
Therefore, thinner rods are recommended acting as
internal tutor and not replacing the bone
Leaving 2 mm around the rod in any plan is a safe method(3)
Rod length:
Pre-operative templates are essential taking into account
the osteotomies needed to straighten the bone.
Measure the length (L) between greater trochanter and
distal growth plate
Female rod length is (L) - 7 mm
Male rod length is (L) + (10-15) mm
13. Methods of fixation
Open osteotomy:
Better in narrow marrow
diameter (distal
segment is reamed)
But, more soft tissue
damage and risk of
devascularization (3)
15. According to the need of
arthrotomy they are divided into:
Those need:
Bailey-Dubow
Sheffield
Those do not need:
Fassier-Duval
Interlocking
16. Those need arthrotomy has limited use in
tibia compared to femur as they have a
higher complication rate compared to
femoral rodding (3)
The surgical trauma to the ankle ligaments
and the permenant damage to most of the
wieght bearing surface of the ankle joint
limit its use (3)
17. Bailey-Dubow
T piece is not a component of the rod and has to
be attached to it
No locking mechanism ensures the fixation to
epiphysis
Need arthrotomy for insertion
The reoperations rates are 21% - 32% (4)
18. Complications of Bailey and Dubow:
Proximal rod migration
Disengagement of the
epiphyseal T-piece (6)
Bending
Infection
19. Sheffield
Design with a fixed T-piece on either end
It is rotated intraoperatively for better fixation
within the epiphysis (4)
The reoperation rate is 20% (4)
Need arthrotomy for insertion
20. Fassier-Duval
The anchorage is achieved through
screw type fixation by threaded
portions at the proximal and distal ends
with improved “screw-in” fixation (4)
The advantage of this rod over the
traditional Bailey-Dubow and Sheffield
rods is the single proximal entry
point(2)
Reoperation rate is 13% in a study on
15 patients (4)
FD rods are safe and pose no risk of
migration, heating effects, or artifact
when undergoing an MRI of the spine
using a 1.5 T magnet (2)
22. Interlocking
The female rod is the same as Sheffield telescopic
rod system while The male rod has a hole at its
distal tip to receive the interlocking pin (7)
A revision rate of 9% at 2 years and 28% at 3
years.(4)
No need for
arthrotomy
proximal migrat-
-ion is 12.5 %(7)
23. Refrences
1) Zeitlin L, Fassier F, Glorieux FH. Modern approach to children with osteogenesis imperfecta.
In: Journal of Pediatric Orthopaedic B. Johari A ,ed. Philadelphia, Pa:Lippincott Williams &
Wilkins; 2003 Mar;12(2):77-87.
2) Makhdom A, Kishta W, Saran N et al. Are Fassier-Duval Rods at Risk of Migration in Patients
Undergoing Spine Magnetic Resonance Imaging?. In: Journal of Pediatric Orthopaedic
Hensinger r, Thompson G, eds. Philadelphia, Pa: Lippincott Williams & Wilkins; 2015 Apr-
May;35(3):323-7
3) Fassier F, Glorieux F. Osteogenesis imperfecta. In: surgical techniques in orthopaedics and
truamatology. Duparc DJ, ed. Philadelphia, Pa: Mosby Elsevier; 2003, 55-050-D-30
4) Birke O, Davies N, Latimer M, et al. Experience With the Fassier-Duval Telescopic Rod: First
24 Consecutive Cases With a Minimum of 1-Year Follow-up. In: Journal of Pediatric Orthopaedic
B. Johari A ,ed. Philadelphia, Pa:Lippincott Williams & Wilkins; 2011 Jun;31(4):458-64
5) EL-ADL G, KHALIL M, EL-LAKKANY r, et l. Telescoping versus non-telescoping rods in the
treatment of osteogenesis imperfecta. In : acta orthopaedic belgica. Barbier O, De Smet L ,eds.
2009, 75, 200-208
6) LANGSTEVENSON A, SHARRARD W. INTRAMEDULLARY RODDING WITH BAILEY-
DUBOW EXTENSIBLE RODS IN OSTEOGENESIS IMPERFECTA. In: The Journal of Bone &
Joint Surgery. Swiontkowski M, ed. Needham, MA: JBJS. 1984 Mar;66(2):227-32.
7) Joon Cho T, Ho Choi I, Chung C, et al. Interlocking Telescopic Rod for Patients with
Osteogenesis Imperfecta. In: The Journal of Bone & Joint Surgery. Swiontkowski M, ed.
Needham, MA: JBJS. 2007;89:1028-1035