5. They are very fragile
Difficult to regulate the body temperature of
newborns & infants
80% of young child’s weight is fluids in comparison
with 60% in adults.
They more liable for electrolytes imbalances
They need special ways for feeding
Pain killers and using of narcotics are more risky for
children
6. They have small blood volume (in neonates about
80-85 ml/ kg)
Their full physiological functions and reserves are
little:
◦ Immature respiratory system
◦ Immature hepatic function
◦ Immature renal function
We do everything weight
based
We do everything warm
7. Why the OR is so hot?!!
Babies really can’t do that…
Have no fat in them
No hair on them
Don’t shiver , not built in them yet
8.
9. General assessment for operation (Heart chest
condition, anemia, hydration status,…..etc)
Local assessment of the site of operation (no
infection)
Assessment of parent knowledge and give then
simple preoperative information about operation.
(Family Consent )
Ensure that the child is physically and
psychologically prepared for surgery
Blood grouping , LAB Results ...
10. Measuring Vital signs
Assess urine for amount, color,…etc
Ensure Empty stomach !!
◦ Stop all food from the midnight before
surgery
◦ Stop breast feeding 4 hours before surgery
◦ Stop clear fluids 2 hours before surgery
◦ !! ....
11. Immediate post-operative day
General
◦ Positioning !!!
◦ Vital signs
◦ Level of consciousness
◦ Hydration
◦ Intake & output
Local
◦ Surgical incision
◦ wound care
◦ Assess for bleeding
◦ Pain medication
12. - General
◦ Vital signs
◦ Signs of infection
◦ Hydration
◦ Intake & output
Local
◦ Surgical incision
◦ Care of wound
Pain medication
15. CDH: Opening in the diaphragm through
which the abdominal contents herniates into
the thoracic cavity during prenatal
development.
16. on the left side in 85% of cases.
Loops of bowel, even most of the abdominal contents,
may protrude into the hemithorax on the involved side.
If the hernia is large, the lung on the affected left side
will be hypoplastic
Mortality rate 50-85%
17.
18. Antenatal ultrasound (abdominal organs
in chest)
Respiratory distress soon after birth
(RDS).
Respiratory difficulty develops a few
hours or days later
Scaphoid abdomen
Diminished air entery
Bowel sounds over chest
Auscultation of heart sounds on right
side of the chest
Persistent pulmonary hypertension
23. Operation: surgical reduction of hernia after
being physiologically stable.
Postoperative: respiratory support till lungs
function probably
24.
25. Preoperative care
oRoutine preoperative care
oSemi-Fowler’s position on affected
side with head of bed elevated.
oCare for respiratory distress
(positioning,oxygenation, mechanical
ventilation)
35. Past history of mother’s polyhydraminos
during pregnancy.
Plain X-ray
◦ Dilated proximal esophagus with air (Atresia)
◦ Abdominal distention (indicates presence of
fistula)
X-ray with contrast (Blind upper esophageal
pouch)
36. EA with TEF is a critical neonatal surgical
emergency.
The aim of preoperative management is to get the
infant into optimal condition for surgery.
Oral feedings are withheld.
Continuous suction
37.
38. NICU for prevention of aspiration
Aspirate from NG tube /5-10 minutes.
I.V. fluids
Surgical repair is the main line of treatment
39. The infant should be positioned
as the head elevated in the
reverse Trendelenberg
position
40. When the infant's condition is
stable, extrapleural surgical
repair of the esophageal
atresia and closure of the
tracheoesophageal fistula can
be performed end to end
anastomosis.
If the patient presented late
osophagostomy and
gastrostomy will be done
41. Immediately after birth:
Warm the baby
Give humidified oxygen
Prepare for surgery (general preoperative care)
X ray , after the NG tube
Ask for Echocardiogram
42. Immediate postoperative:
Care for chest tube (patency & output)
Care of esophagostomy:
◦ Clean with gauze to absorb saliva
◦ Change the gauze frequently to prevent constant wetness
Provide skin care
Oral stimulation with pacifier to allow practice in
swallowing
Care of Gastrostomy tube
43.
44. CHPS: Narrowing of the pyloric sphincter at
the outlet of the stomach.
Obstruction of the pyloric lumen due to pyloric
muscular hypertrophy
45.
46.
47. No abnormal signs in the first week or
two after birth.
Forceful projectile vomiting of
feedings without bile usually begins
late in the first month of life.
Gastric peristaltic waves may be
visible, crossing the epigastrium from
left to right.
Weight loss, dehydration
48. Distended upper abdomen
Decreased frequency and quantity of
stool
Visible gastric peristalsis
Delayed diagnosis may lead to repeated
vomiting, dehydration, failure to gain
weight
49. Palpation of a discrete, 2- to 3-cm, firm,
movable pyloric olive-like mass deep in the
right side of the epigastrium.
Abdominal Ultrasonography.
If the diagnosis is uncertain, a barium swallow
will show delayed gastric emptying and the
typical "string sign" of a markedly narrowed,
elongated pyloric lumen.
50. Restore hydration status by I.V.
fluids
Assess the amount,
characteristics, and frequency of
vomiting.
Monitoring intake and output
Careful observation and
recording of vomiting and bowel
elimination.
54. Ensure adequate hydration
Care for operative side
NG tube should be maintained, oral hygiene
should offered
Give clear oral fluids from 4-6 hours
postoperatively as ordered.
Feed the baby slowly; burp frequently, and
in high Fowler's position on the right side
after feeding.
Family teaching and follow-up
60. Jaundice
Dark urine, stained diapers.
Stool color becomes white or tan.
Hepatosplenomegaly
Poor fat metabolism, failure to thrive.
Pruritus, irritability.
If uncorrected the child may develops liver cirrhosis
62. Many children develop progressive cirrhosis and
need liver transplantation
High-caloric formula containing fats that can be
digested without bile.
63. The child should provide water soluble
vitamins
Phenobarbital may be given to promote
bile flow.
Low-salt diet and diuretics Supportive
care for parents
Comfort measures for child.
64.
65. Absence of the anus in its
normal position in the perineum
66. Low IA: Blind pouch below the Levator ani
muscles
High IA: Blind pouch above Levator ani muscles
67.
68.
69. o Failure to pass meconium
o Absence or stenosis of anal canal
o Presence of anal membrane
o External fistula to perineum
o Passage of meconium from the vagina or in
urine
70. Nursing Care of the child with IA:
Role in diagnosis:
Ensure that meconium is not passed in the first 24
hours after birth
Look at anus
Pass a rectal thermometer to determine its patency.
If there is stool in urine or vagina: report immediately
nursing assessment, to identify other GI or urogenital
problems
Immediate plans are made for surgical intervention
73. Low IA: Perineal anoplasty, followed by anal
dilatation
High IA: Sigmoid colostomy , Pull- through
technique (pulling the colon from the abdomen
through the perineum), anal dilatation and closure
of colostomy.
74. In low lesions (Perineal Surgical Incision)
Skin care at anoplasty site
Parent teaching about anal dilatation
In addition to general post-operative care
In high lesions (Colostomy /pull-through)
◦ Colostomy care
◦ Skin care
◦ Home care & parent teaching
76. Absence of ganglion cells in the rectum and
to varying degrees upwards in the colon,
causing functional obstruction
77.
78.
79. ◦ Affects males 4 times as frequently as females.
◦ In approximately 12.5% of patients
Hirschsprung disease may be familial
80. Neonatal period
Delayed passage of meconium within the 1st 24
hours after birth.
Reluctance to ingest milk
Bile-stained vomitus
81. Infancy period
Failure to thrive
Abdominal distention.
Chronic constipation, fever
Attacks of vomiting and
Explosive watery diarrhea
(Ominous sign)
82. Childhood period
Chronic constipation
Abdominal pain and distention
Ribbon like, foul-smelling stools
Visible peristalsis
palpable fecal mass
Failure to thrive
Narrow spastic rectum, no stool during per rectum
examination
Bowel obstruction, attacks of enterocolitis
The longer the disease goes untreated, the greater
the chance of developing toxic enterocolitis (toxic
Megacolon).
85. Surgical removal of all Aganglionic bowel
segment.
Colo-anal anastomosis (Abdominal-Perineal
pull-through operation).
Relive chronic constipation by stool softeners
and rectal irrigation
Temporary colostomy
86.
87. Improve nutritional status by
providing smaller and more frequent
feedings
Assess hydration status by
monitoring intake and out put and
daily weight
88. Note and record the frequency and
characteristics of stools
Administer enema to relive constipation
(Isotonic solution)
No rectal temperature
89. Periodically measure abdominal girth
Assess for any R.D. due to abdominal distention
Giving medication (Antibiotic and stool softeners)
Support the parent and child
Care for colostomy
91. Invagination or telescoping of one portion of
the intestine into another, causing
obstruction
92. The cause of intussusceptions is unknown. It may
be linked to viral infections, intestinal polyps,
lymphoma, and foreign body obstruction.
Incidence is about three times higher in males
than in females
93. Sever paroxysmal abdominal
pain, causing the child to scream and
draw his or her knees to the abdomen
Vomiting of gastric contents (Bile-
stained or fecal emesis)
Currant Jelly stool containing
blood and mucus
94. Tender, distended abdomen, possibly
with a palpable mass
Shock like syndrome
Palpable sausage-shaped mass in
upper right quadrant
Empty lower right quadrant
Fever and signs of peritonitis.
98. Assess hydration status Encourage intake of
clear fluids after surgery
Monitor bowel elimination status
Postoperatively: monitor for signs of infections,
assess surgical wound, V.S
Support the child and family
Routine postoperative care
99.
100. Clefts of lip and palate are facial malformations that
occurred during embryonic development appear
separately or, more often, together.
101. Deformed dental structures are
associated with CL.
CL with or without CP is more
common in males.
CP alone is more common in
females.
102.
103.
104. collaborative efforts of a number of specialists:
pediatrician, nurses, plastic surgeon, orthodontist,
and speech therapist.
Medical management is directed toward closure of
the cleft (s),
prevention of complications, and
facilitation of normal G&D.
105. Surgical correction of CL (Z- plasty) usually done at
1-3 months of age
Surgical correction of CP (Platoplasty) is done 12-
18 months of age, before the child develops faulty
speech habits.
106. Routine preoperative care
Feed in an upright
position to prevent aspiration,
a soft, large-holed nipple
or rubber-tipped syringe
or cleft lip or palate bottle
may be used.
107. Burp frequently because of swallowed air.
Prevent infection from irritation of the lip, restrain infant's arms
if needed.
Teach parents the need for dental hygiene and regular
dental supervision.
Emotional support to the parent (emphasize the positive
appearance of the child after surgical correction).
Help the mother to give breast milk using alternative methods.
108. Maintain a patent airway because of edema
and infant's habit of mouth breathing.
Protection the operative site from trauma
and infection.
109. Elbow restraints are needed to prevent the
child from rubbing the suture line of surgery.
CL correction the child should be scurried in
supine or upright position.
Prevent crying, because of pressure on suture
line; encourage a parent to stay.
110. CP correction the child should be scurried in prone
position.
Gentle aspiration of mouth and nasopharyngeal
section may be needed to prevent aspiration.
111. Feed same as before surgery
Clear fluids are offered when the infant has fully
recovered from anesthesia.
When the baby returned to his feeding, mouth
care after each feeding is must.
Skin care on the suture line should be
maintained.
Family teaching and discharge plan.
112.
113.
114.
115. Write down what should be done as a routine pre-operative work up
Choose the best single answer
After 2 hours of delivering a newborn baby ,the
nurse noticed the oxygen saturation goes down
(cyanosis ) , she reported to the doctor who
noticed a scaphoid abdomen , Bowel sounds
over chest and ordered an X-ray that shows
some abdominal content in the chest , what is the
most likely
diagnosis
116. Choose the best single answer
In the NICU , the nurse noticed that her newborn
assigned baby , have too much saliva , while she
tried to pass the Nasogastric tube , she failed , so
she called on the Doctor, who found the tube
recoils and comes back up , what is the most
probable diagnosis of this case
117. Choose the best single answer
A mother walks in the clinic , with her 45 days old
child, she have a smell , also her shoulder is
stained with milk ,she says that her child always
vomit shortly after feeding , the child looks
underweight and dehydrated,
What is the most probable diagnosis
What is the operation done to correct this
condition
118. Choose the best single answer
A 3 weeks old baby with Jaundice ,Dark urine,
stained diapers, Stool color is white or tan and
Hepatosplenomegaly
What is the operation done to correct this
condition
What is the most probable diagnosis
119. Choose the best single answer
Newborn baby , with imperforate anus , the
invertogram shows Blind pouch above Levator ani
muscles
What is the type of this anomaly
What is the operation done to correct this
condition
120. Choose the best single answer
Delayed passage of meconium within the 1st 48
hours after birth increases the suspicion of which
disease
121. Choose the best single answer
A 9 month old boy , come to the emergency
department , with sever abdominal colicky pain ,
with red current jelly stool in the diaper , what is
the most possible diagnosis
What is the first line of treatment
I will give you my Glossary , the buzz words , phrases , Que terms …list of terms , list with pictures …will cover what you might see in life and in exam
I live this life >>
في الطواريء ED ER
لو عيان جالك ..
HR 180 BP 80 systolic ….will catch your attention
But if a baby falls off a changing table , and they bring him to the ED with the same data , it means something totally different
When you deal with littele babies , Reboot your system on vital signs
Vital signs
Body surface area
Fluid
Tempreature
We do everything weight based
We do everything warm
Baby , brand new , cyanotic with a scaphoid abdomen …
For us , it is our life …the question is , should I run to the NICU ..or continue my launch
Is it a near catastrophic event
It is a physiologic emergency , what we try to battle is pulm hypertension , persistant fetal circulation
Stabilize , reduce pulm hypertension , not rush to the OR
We drool on ourself , it is the case
The next question we gonna ask , do they have any gas in the GIT
If yes , not only tof , but there is a fistula
We run up , we don’t rush the to the OR
We look for other assosiated anomalies
We quickly ask for ECHO , rt or lt side aortic arch
Forcefull vomitting , but non billious
You see the baby later , in a 5 week old
Look at the mom , her shoulder is nasty
It is an acquired disease , we no longer think of it as a conginetal diseae
You almost never have met a baby who has pyloric stenosis at birth
It comes after 2-3 weeks , it ends at 7-8 weeks …