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Case 4 2007
Clinical history
61-year-old male with progressive lower
extremity weakness and spasticity.
Imaging A
Diagnosis ?
C
CONGENITAL DISEASES, MALDEVELOPMENT, MIGRATIONAL DISORDERS, VARIANTS
I
BACTERIA, RICKETTSIA, FUNGUS,VIRUS, PARASITES, PRION
M
METABOLIC, IMMUNE, GLIOSIS, SCLEROSIS, DEGENERATION
T
CONTUSION, HEMATOMAS SUBDURAL, EPIDURAL, TRAUMA COMPLICATIONS,
RADIOTERHAPY, CHEMOTHERAPHY
V
VASCULAR MALFORMATIONS ( AVM, VENOUS ANOMALY, CAPILLARY, CAVERNOUS ),
ANEURYSMS,ANGIOPATHY, INTRACEREBRAL HEMORRHAGE, INFARCT, THROMBOSIS
DISSECTION
N
PRIMARY
SECONDARY
Diagnosis ?
a.Infarct
b.Transverse myelitis
c.Multiple sclerosis
d.AVM
C
CONGENITAL DISEASES, MALDEVELOPMENT, MIGRATIONAL DISORDERS, VARIANTS
I
BACTERIA, RICKETTSIA, FUNGUS,VIRUS, PARASITES, PRION
M
METABOLIC, IMMUNE, GLIOSIS, SCLEROSIS, DEGENERATION
T
CONTUSION, HEMATOMAS SUBDURAL, EPIDURAL, TRAUMA COMPLICATIONS,
RADIOTERHAPY, CHEMOTHERAPHY
V
VASCULAR MALFORMATIONS ( AVM, VENOUS ANOMALY, CAPILLARY, CAVERNOUS ),
ANEURYSMS,ANGIOPATHY, INTRACEREBRAL HEMORRHAGE, INFARCT, THROMBOSIS
DISSECTION
N
PRIMARY
SECONDARY
Diagnosis
a.Infarct
b.Transverse myelitis
c.Multiple sclerosis
d.AVM
Dural AVM , small arteriovenous communication supplied by
dural branches arising from intercostal, lumbar or sacral
arteries and drained by perimedullary veins (ascending or
descending)
Nidus is in dura covering proximal nerve root.
Most (98-99%) are single lesions; double lesions in 1-2% of
patients.
Clinically: middle-aged or elderly men, slowly progressive and
ascending myelopathy due to cord edema (sometimes called:
Foix Alajouanine syndrome)
Contrast enhancement in cord is common.
Treatment: occlusion of draining veins by endovascular or
surgical means
Foix–Alajouanine syndrome ?
Foix–Alajouanine syndrome
Is a spinal cord disorder caused by an arteriovenous malformation of the spinal
cord.[
The patients present with symptoms indicating spinal cord involvement (paralysis of
arms and legs, numbness and loss of sensation and sphincter dysfunction),
Pathological examination reveals disseminated nerve cell death in the spinal cord
and abnormally dilated and tortuous vessels situated on the surface of the spinal
cord.
Treatment :
Surgical intervention ( removal of the nidus)
Endovascular occlusion of the nidus
Steroids for the myelopathy
CASO 5

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CASO 5

  • 2. Clinical history 61-year-old male with progressive lower extremity weakness and spasticity.
  • 5. C CONGENITAL DISEASES, MALDEVELOPMENT, MIGRATIONAL DISORDERS, VARIANTS I BACTERIA, RICKETTSIA, FUNGUS,VIRUS, PARASITES, PRION M METABOLIC, IMMUNE, GLIOSIS, SCLEROSIS, DEGENERATION T CONTUSION, HEMATOMAS SUBDURAL, EPIDURAL, TRAUMA COMPLICATIONS, RADIOTERHAPY, CHEMOTHERAPHY V VASCULAR MALFORMATIONS ( AVM, VENOUS ANOMALY, CAPILLARY, CAVERNOUS ), ANEURYSMS,ANGIOPATHY, INTRACEREBRAL HEMORRHAGE, INFARCT, THROMBOSIS DISSECTION N PRIMARY SECONDARY
  • 7. C CONGENITAL DISEASES, MALDEVELOPMENT, MIGRATIONAL DISORDERS, VARIANTS I BACTERIA, RICKETTSIA, FUNGUS,VIRUS, PARASITES, PRION M METABOLIC, IMMUNE, GLIOSIS, SCLEROSIS, DEGENERATION T CONTUSION, HEMATOMAS SUBDURAL, EPIDURAL, TRAUMA COMPLICATIONS, RADIOTERHAPY, CHEMOTHERAPHY V VASCULAR MALFORMATIONS ( AVM, VENOUS ANOMALY, CAPILLARY, CAVERNOUS ), ANEURYSMS,ANGIOPATHY, INTRACEREBRAL HEMORRHAGE, INFARCT, THROMBOSIS DISSECTION N PRIMARY SECONDARY
  • 9. Dural AVM , small arteriovenous communication supplied by dural branches arising from intercostal, lumbar or sacral arteries and drained by perimedullary veins (ascending or descending) Nidus is in dura covering proximal nerve root. Most (98-99%) are single lesions; double lesions in 1-2% of patients. Clinically: middle-aged or elderly men, slowly progressive and ascending myelopathy due to cord edema (sometimes called: Foix Alajouanine syndrome) Contrast enhancement in cord is common. Treatment: occlusion of draining veins by endovascular or surgical means
  • 11. Foix–Alajouanine syndrome Is a spinal cord disorder caused by an arteriovenous malformation of the spinal cord.[ The patients present with symptoms indicating spinal cord involvement (paralysis of arms and legs, numbness and loss of sensation and sphincter dysfunction), Pathological examination reveals disseminated nerve cell death in the spinal cord and abnormally dilated and tortuous vessels situated on the surface of the spinal cord. Treatment : Surgical intervention ( removal of the nidus) Endovascular occlusion of the nidus Steroids for the myelopathy