1. The most common infectious disease associated with
lymphocytopenia is:
a-AIDS
b-Influenza
c-Tuberculosis
d-Viral hepatitis
AIDS causes lymphocytopenia due to
destruction of CD4 T cells infected with HIV-1
or HIV-2.e-Typhoid fever
2. The relative risk of developing obesity is higher in
the following age group if they have obese parents:
a-0-1 month
b-1-3 month
c-3-6 month
d-Young children
e-Older children
3. The diagnosis of maple syrup urine disease is confirmed by:
a-Peculiar odor of maple syrup is noted in urine, sweat,
and cerumen.
B-Decreased plasma levels of leucine, isoleucine, and
valine
c-Increased plasma levels of leucine, isoleucine and valine
d-Decreased urine levels of leucine, isoleucine, and
valine.
E-Increased plasma levels of maple syrup
4. The preferred therapy in patients with maple syrup urine
disease is:
a-Peritoneal dialysis
b-Exchange transfusion
c-Sodium bicarbonate
d-Phenobarbital
e-Liver transplantation
5. Patients with galactosemia are at increased risk for
neonatal sepsis due to the following organism:
a-E. coli
b-Group B Streptococcus
c-Staphylococcus aureus
d-Candida albicans
e-Pseudomonas aeruginosa
6. A newborn develops pneumothorax on the
first day of life. All the following conditions
can produce pneumothorax except:
a-Renal malformations
b-Pulmonary hypoplasia
c-Meconium aspiration
d-Perinatal asphyxia
e-Spontaneous
7. A newborn develops respiratory distress at birth when
the mouth is closed. The most likely diagnosis is:
a-Choanal stenosis
b-Pierre Robin syndrome
c-DiGeorge syndrome
d-Deviated nasal septum
e-Choanal atresia
8. A newborn develops difficulty feeding and
breathing after birth. A P/E reveals flattened nose
and asymmetric nares. The most likely diagnosis is:
a-Down syndrome
b-Trisomy 13
c-Choanal stenosis
d-Nasolacrimal duct cyst
e-Dislocated cartilaginous portion of the nasal septum
9. The core team for care of children with rheumatic
disease includes all the following specialists except:
a-Pediatrician
b- Ophthalmologist
c-Orthopedic surgeon
d-Nurse
e-Pediatric rheumatologist
10. The serious complication of herpes simplex virus (HSV)
gingivostomatitis is:
a-Group B Streptococcus bacteremia
b-Group A Streptococcus bacteremia
c-Candida albicans bactremia
d-Candida albicans meningitis
e-E. coli bacteremia
11. The lymphadenitis commonly occurs in
acute herpetic gingivo-stomatitis is:
a-Preauricular
b-Tonsillar
c-Submandibular
d-Submaxillary
e-Supraclavicular
12. The lymphadenitis commonly occurs
in acute herpetic gingivo-stomatitis is:
a-Preauricular
b-Tonsillar
c-Submandibular
d-Submaxillary
e-Supraclavicular
13. Mother of a newborn infant develops varicella
zoster. The following statement is true about
the management of newborn:
a-VZIG should be given immediately.
B-VZIG should be given within 12 hours.
C-VZIG should be given within 24 hours.
D- should be given within 48 hours.
E-VZIG should not be given.
14. The most common cause of hemolytic
disease of the newborn is:
a-E. coli sepsis
b-Rh incompatibility
c-Biliary atresia
d-ABO incompatibility
e-Group B Streptococcus bacteremia
15. The side effect of IV calcium therapy is:
a-Tachycardia
b-Reduces digoxin toxicity
c-Hypoparathyroidism
d-Myocardial necrosis
e-Tissue necrosis
16. The preferred diagnostic study in patients
with parvovirus B19 infection is:
a-Viral culture
b-Anti-B19 IgG
c-Anti-B19 IgA
d-Anti-B19 IgE
e-Anti-B19 IgM
17. The most common cause of an abdominal
mass in newborn is:
A-Horseshoe kidney
b-Ectopic kidney
c-Polycystic kidney
d-Pyloric stenosis
e-Multicystic dysplastic kidney
18. The most urinary tract infections (UTIs)
occur due to:
a-Bacterial spread from blood
b-Descending infections
c-Ascending infections
d-Bacterial spread through lymphatics
e-Bacterial spread from perinephric tissues
19. Prune-belly syndrome is often associated
with the following intestinal anomaly:
a-Pyloric stenosis
b-Duodenal atresia
c-Jejunal atresia
d-Malrotation
e-Hirschsprung disease
20. The most common cause of death in children
with prune-belly syndrome in the first few
months of life is:
a-Renal failure
b-Pulmonary complications
c-Cardiac failure
d-Hepatic complications
e-Meningitis secondary to E. coli
21. The mean age when vesicoureteral reflux
resolves is:
a-2-3 years
b-3-4 years
c-4-5 years
d-5-6 years
e-6-7 years
22. A genotypic male infant P/W prenatal and postnatal growth
retardation, and mental retardation. A P/E reveals
microcephaly, ptosis, anteverted nares, broad alveolar ridges,
syndactyle of the 2nd-3rd toes, and ambiguous genitalia.
The most likely diagnosis is:
a-Noonan syndrome
b-Klinefelter syndrome
c-Down syndrome
d-Prader-willi syndrome
e-Smith-Lemli-Opitz syndrome
23. The mode of inheritance of Smith-Lemli-
Opitz syndrome is:
a-Autosomal recessive
b-Autosomal dominant
c-X-linked recessive
d-X-linked dominant
e-Multifactorial
24. The common associated anomaly in
patients with Smith-Lemli-Opitz type I is:
a-Pyloric stenosis
b-Hirschsprung disease
c-Cleft palate
d-Lipoma of pituitary gland
e-Skeletal abnormalities
25. The common associated anomaly in patients
with Smith-Lemli-Opitz syndrome type II:
a-Hirschspring disease
b-Cleft lip
c-Duodenal stenosis
d-Jejunal atresia
e-Imperforate anus
