5. TETRALOGY OF FALLOT
ā¢ It is the most common cause of cyanosis beyond one year of
age.
ā¢ It constitutes 10% of all congenital heart defects.
ā¢ Fallot defined it as a constellation of four abnormalities to
include :
ā¢ Ventricular septal defect (VSD),
ā¢ Pulmonary stenosis (PS),
ā¢ Right ventricular hypertrophy
ā¢ Dextroposition of the aorta or An overriding aorta is a congenital heart
defect where the aorta is positioned directly over a ventricular septal defect
(VSD), instead of over the left ventricle
6.
7. Clinical Manifestation
ā¢ Become symptomatic any time after birth
ā¢ Paroxysmal attack of dyspnea
ā¢ Cyanosis may be present from birth or make its appearance some
years after birth
ā¢ Commonest symptoms are dyspnea on exertion and exercise
intolerance
ā¢ Patients assume a sitting posture ā squatting ā as soon as they get
dyspneic. Although squatting is not specific for TOF, it is the
commonest congenital lesion in which squatting is noted
ā¢ Anoxic spells occur predominantly after waking up or following
exertion.
8. ā¢ Normal growth and development depend on a normal workload for
the heart and normal flow of oxygen-rich blood to all parts of the
body. Babies who have tetralogy of Fallot may not gain weight or
grow as quickly as children who have healthy hearts because they
tire easily while feeding.
ā¢ Squatting (a compensatory mechanism) is uniquely characteristic
of a right-to-left shunt that presents in the exercising child.
Squatting increases the peripheral vascular resistance, which
diminishes the right-to-left shunt and increases pulmonary blood
flow.
āChild becomes more cyanosed while crying, these are called
ācyanotic spellsāor Fallotās spells.
9. What causes a spell ?
ā¢ Due to "spasm" or contraction of a band of muscle in the right
ventricle just under the pulmonary valve. When this muscle contracts,
it further narrows the channel for blood flow into the lungs. As a
result, oxygen delivery becomes further reduced. This causes a spell
10. Investigations
Physical Examination
ā¢ Cyanosis , clubbing, slightly prominent `a ā wave in the jugular venous
pulse, normal sized heart with parasternal impulse, a systolic thrill in
less than 30 % patients.
ā¢ Normal first sound,
ā¢ Single second sound and
ā¢ An ejection systolic murmur at 3rd ICS
11. Chest X ā ray :
ā¢ Boot shaped heart (it means apex is
lifted up & there is a concavity in the
region of pulmonary artery)
12. Treatment
ā¢ Management of complications and correction of anemia
ā¢ Treatment of Anoxic spells :
ā¢ Knee chest position to increase aortic resistance. The increased aortic
and left ventricular pressure reduces the rush of blood through the
septal hole from the right ventricle and improves blood circulation to
the lungs, decreasing the right to left shunt thus decreasing the
amount of deoxygenated blood entering the systemic circulation.
ā¢ Oxygen through a face mask to increase the amount of oxygen in the
blood.
13. ā¢ beta-blockers such as propranolol
ā¢ acute episodes may require rapid intervention with morphine to
reduce ventilatory drive and a vasopressor such as epinephrine,
phenylephrine, or norepinephrine to increase blood pressure.
ā¢ Correction of anemia
ā¢ Consider operation
14. Surgical Management
ā¢ Blalock-Taussig operation : connection between the right subclavian
artery, and the right pulmonary artery, which increases the amount of red
oxygenated blood reaching the lungs, relieving cyanosis.
ā¢ Pott`s shunt : descending aorta is anastomosed to the pulmonary artery
ā¢ Waterstont`s shunt : ascending aorta right pulmonary artery anastomosis
ā¢ Total correction: The hole in the ventricular septum is closed with a patch
and the obstruction to right ventricular outflow, pulmonic stenosis,
is opened.
ā¢ These corrections allow blood flow to the lungs for oxygenation before
being pumped out into the body.
15. Surgical Management
ā¢ If oxygen levels are critically low soon after birth, a prostaglandin E1
infusion is usually initiated to keep the ductus arteriosus open which
will provide additional pulmonary blood flow and increase the child's
oxygen level.
ā¢ Complete repair is usually done electively when children are about 6
months of age, as long as the oxygen levels remain adequate.
ā¢ Surgical correction of the defect is always necessary. Occasionally,
patients will require a surgical palliative procedure prior to the final
correction.
ā¢ Corrective repair of tetralogy of Fallot involves closure of the
ventricular septal defect with a synthetic Dacron patch so that the
blood can flow normally from the left ventricle to the aorta.
16. ā¢ The narrowing of the pulmonary valve and right ventricular
outflow tract is then augmented (enlarged) by a combination of
cutting away (resecting) obstructive muscle tissue in the right
ventricle and by enlarging the outflow pathway with a patch.
ā¢ In some babies, however, the coronary arteries will branch
across the right ventricular outflow tract where the patch would
normally be placed. In these babies an incision in this area to
place the patch would damage the coronary artery so this
cannot safely be done.
ā¢ When this occurs, a hole is made in the front surface of the right
ventricle (avoiding the coronary artery) and a conduit (tube) is
sewn from the right ventricle to the bifurcation of the pulmonary
arteries to provide unobstructed blood flow from the right
ventricle to the lungs.
17. ā¢ Surgical repair is more difficult when the pulmonary arteries are
critically small or when the lung blood flow is supplied
predominantly by aortopulmonary collaterals.
ā¢ Most babies are fairly sick in the first few days after surgery,
since the right ventricle is "stiff" from the previous hypertrophy
(thickness) and because an incision is made into the muscle of
the ventricle, making the muscle temporarily weaker.
ā¢ This right ventricular dysfunction usually improves significantly
in the days following surgery. Patients may also have rhythm
problems after surgery.
18. ā¢ An abnormally fast rhythm (called junctional tachycardia) may
occur and may require treatment with medication or the use of a
temporary pacemaker. This abnormal rhythm is usually
temporary and the rhythm generally will return to normal as the
right ventricle recovers.
ā¢ Patients are also at risk for slow heart rates after surgery due to
heart block. Heart block may be caused by injury to or
inflammation of the conduction system in the heart. In many
patients, the conduction improves and normal rhythm returns.
Rarely, a permanent pacemaker may be necessary.
ā¢ Since a normal circulation is produced by the tetralogy of Fallot
repair procedure, long-term cardiac function is usually excellent.
19. ā¢ However, the repair does usually leave the child with a leaky (insufficient)
pulmonary valve. In this situation, after the right ventricle pumps blood out
to the pulmonary arteries, some of the blood will flow back into the right
ventricle. This creates extra volume in the right ventricle forcing it to work
harder and become dilated.
ā¢ In a small percentage of children, this pulmonary insufficiency can lead to
diminished function of the right ventricle. Symptoms of fatigue, especially
with exercise, may develop. In these cases, replacement of the pulmonary
valve is often recommended.
ā¢ Patients who have had repair of tetralogy of Fallot can also redevelop a
narrowing at the outflow area or in the branch (left or right) pulmonary
arteries, which will cause the right ventricle to pump at abnormally high
pressures.
20. ā¢ If these problems occur, surgical intervention to further widen the
outflow tract or pulmonary arteries may be necessary. Narrowing the
pulmonary arteries can sometimes be treated without surgery, with
balloon dilation of the vessels during cardiac catheterization.
ā¢ Long-term follow-up with a cardiologist to detect recurrent or new
problems as early as possible is essential. Follow-up visits in the
cardiology clinic usually consist of a physical
examination, electrocardiogram and periodic echocardiography. In
addition, these visits will also include occasional cardiac MRI scans,
exercise stress tests and Holter evaluations as a child reaches the
teenage and adult years.
21. Palliative Management
ā¢ It was common in the past to do temporary surgery during infancy in babies who
had tetralogy of Fallot. This surgery improved blood flow to the lungs. ... In the
temporary surgery, the surgeon places a tube called a shunt between a large
artery branching off the aorta and the pulmonary artery.
ā¢ The BlalockāThomasāTaussig shunt (commonly called the BlalockāTaussig
shunt) is a surgical procedure used to increase pulmonary blood flow for
palliation in duct dependent cyanotic heart defects like pulmonary atresia, which
are common causes of blue baby syndrome.
22. i.Classic BT shunt: The subclavian artery is
anastomosed to the ipsilateral pulmonary
artery (PA). This procedure is usually
performed in infants older than 3- months; a
right-sided shunt is performed in patients with
left aortic arch; a left sided shunt is performed
for right aortic arch.
ii.Modified Blalock-Taussig shunt: A Gore-Tex
interposition graft is placed between the
subclavian artery and the ipsilateral PA. This
is the most popular procedure for any age,
especially for small infants younger than 3
months of age. A left-sided shunt is preferred
for patients with a right aortic arch
23. TRICUSPID ATRESIA
ā¢ Tricuspid atresia is a type of
heart disease that is present at
birth (congenital heart disease),
in which the tricuspid heart
valve is missing or abnormally
developed. The defect blocks
blood flow from the right atrium
to the right ventricle.
ā¢ Incidence: 0.06/1000 live births
25. Risk factors
ā¢ A mother who had German measles (rubella) or another viral illness during early
pregnancy
ā¢ A parent who has a congenital heart defect
ā¢ Older parental age at conception
ā¢ Mother's obesity
ā¢ Drinking alcohol during pregnancy
ā¢ Smoking before or during pregnancy
ā¢ A mother who has poorly controlled diabetes
ā¢ Use of some types of medications during pregnancy, such as the acne drug
isotretinoin (Claravis, Amnesteem, others), some anti-seizure medications and
some bipolar disorder medications
ā¢ The presence of Down syndrome, a genetic condition that results from an extra
21st chromosome
27. Enters
LV
Blood enters
RV through
VSD
From RV
blood enters
Pulmonary
trunk
Blood enters
enters pul
trunk via
PDA
Increased
pulmonary
blood flow
LA and LV
hypertrophy CHF
28. Clinical Manifestation
ā¢ The clinical feature of tricuspid atresia largely depend on the quantity
of pulmonary blood flow
ā¢ Decreased pulm flow:
- Severe cyanosis
- Hypoxemia
- Acidosis
- Pulmonary oligemia
- May have central cyanosis
- Tachypnoea
29. Increased pulm flow
ā¢ Difficult to diagnose
ā¢ May not appear cyanotic but may present with signs of heart failure
later in infancy
ā¢ Pulmonary plethora present with symptoms of dyspnoea, fatigue,
difficulty in feeding, and perspiration which are suggestive of
congestive heart failure.
ā¢ Cyanosis is minimal
30. Other features
ā¢ Holosystolic murmur at the lower sternal border
ā¢ Problems related to chronic cyanosis like
ā¢ Clubbing
ā¢ Polycythemia, relative anemia
ā¢ Stroke
ā¢ Coagulation abnormalities
ā¢ Some babies or older people with tricuspid atresia also develop symptoms
of heart failure, including:
ā¢ Fatigue and weakness
ā¢ Shortness of breath
ā¢ Swelling (edema) in the legs, ankles and feet
ā¢ Swelling of the abdomen (ascites)
ā¢ Sudden weight gain from fluid retention
32. Therapeutic Management
ā¢ For the neonate, whose pulmonary blood flow depends on the
patency of the ductus arteriosus, a continuous infusion of
prostaglandin E1 (0.03-0.1 mcg/kg/min) is started until surgical
intervention can be arranged.
ā¢ Digoxin
ā¢ Diuretics
33.
34. Palliation for decreased pulm blood flow
ā¢ Systemic to pulmonary artery shunt: increases pulmonary blood flow
through surgically created left to right shunt at the great vessels.
35.
36.
37. Palliation for increased pulm blood flow
ā¢ Control amount of pulmonary blood flow to prevent CHF and
pulmonary vascular disease from pulmonary over circulation
39. Fontan Procedure
ā¢ Between the ages of 2 and 5 years, children with
tricuspid atresia will be ready for the third
operation required to optimize their circulation.
ā¢ This operation is called the Fontan procedure,
and involves connection of the inferior vena
cava directly to the pulmonary artery, which
forces all blood returning from the body to pass
through the lungs and pick up oxygen before
being pumped to the body.
ā¢ This allows a more normal color in the skin and
lips as well due to a more normal oxygen
saturation in the blood.
40. Modified Fontan Procedure
ā¢ Systemic venous return is directed to the lungs without a ventricular
pump through surgical connections between the right atrium and the
pulmonary artery
ā¢ A fenestration (opening) in the right arterial baffle is sometimes done
to relieve pressure.
ā¢ The patient must have normal ventricular function and a low
pulmonary vascular resistance for the procedure to be successful
41. Bidirectional Glenn Procedure
ā¢ The operation at 3 to 6 months is called a bidirectional Glenn. The
superior vena cava is detached from the heart and connected directly
to the pulmonary artery.
ā¢ This allows blood from the upper body to flow directly to the lungs to
pick up oxygen without having to be pumped by the heart.
ā¢ It also prevents blood that already has oxygen from returning to the
lungs, and, thereby, keeps the heart from doing unnecessary work.
ā¢ After this operation, however, there is still blood returning from the
body through the inferior vena cava going directly back to the body
without first passing through the lungs. Because of this, some level of
cyanosis will persist.
42.
43. Complications later in life
ā¢ Although treatment greatly improves the outcome for babies with
tricuspid atresia, complications can develop later in life, including:
ā¢ Formation of blood clots that can lead to a clot blocking an artery in
the lungs (pulmonary embolism) or cause a stroke
ā¢ Easy tiring when participating in activity or exercise
ā¢ Heart rhythm abnormalities (arrhythmias)
ā¢ Kidney or liver disease
46. Transposition of Great Arteries (TGA)
ā¢ Second most common form (5-7%)
of congenital cardiac anomalies.
ā¢ Aorta arises from RV and
Pulmonary Arteries from LV.
ā¢ Most common in males.
ā¢ Without an abnormality, life would
not be possible.
ā¢ ASD
ā¢ VSD (30-40%)
ā¢ PDA
47. Transposition of Great Arteries (TGA)
ā¢ The transposition of the
great arteries is ventriculo
arterial discordance, in
which the aorta arises
from the morphologic
right ventricle and the
pulmonary artery arises
from the morphologic left
artery.
48. Etiology
ā¢ Idiopathic
ā¢ Genetic causes
ā¢ Rubella infection to mother during pregnancy
ā¢ Maternal age over 40years
ā¢ Incidence is more in infants of diabetic mothers
49. Pathophysiology
Pumped to the systemic circulation effectively bypassing the lungs
Deoxygenated systemic venous blood returns to the right atrium and right ventricle
Recirculated to the pulmonary vascular bed via the abdominal pulmonary arterial
connection to the left ventricle
Oxygenated pulmonary venous blood returns to the left atrium and left ventricle
Transposition of great arteries
50. If remain untreated, Heart Failure
ASD,VSD,PDA
It is incompatible with prolonged survival unless mixing of oxygenated
and deoxygenated blood occurs at some anatomic level like
51. Clinical Manifestation
ā¢ Depends on the type and size of associated defects.
ā¢ Cyanosis
ā¢ Tachypnoea
ā¢ Tachycardia
ā¢ Diaphoresis
ā¢ Failure to gain wight
ā¢ Signs and symptoms of heart failure.
ā¢ Cardiomegaly
52. Investigations
ā¢ Auscultation- a single or narrowly
split, diminished second heart
sound. Systolic ejection murmur
may be present.
ā¢ ABG analysis
ā¢ Chest X-Ray: āEgg on a Stringā
ā¢ Echocardiography
ā¢ Cardiac Catheterization
53. Medical Management
ā¢ To provide interacting mixing: The administration of intravenous
prostaglandin E1 may be initiated to temporarily increase blood
mixing if systemic and pulmonary mixing is inadequate to provide an
oxygen saturation of 75% or to maintain cardiac output.
ā¢ Bicarbonate administration for Acidosis
ā¢ During cardiac catheterization, a balloon atrial septostomy (Rashkind
procedure) may also be performed to increase mixing and maintain
cardiac output over a longer period.
54. Surgical Treatment
Atrial Switch Procedure-
ā¢ Procedure of choice performed in first week of life involves
transecting the great arteries and anastomosing the main
pulmonary artery to the proximal aorta (just above the aortic
valve) and anastomosing the ascending aorta to the proximal
pulmonary artery.
ā¢ The coronary arteries are switched from the proximal aorta to the
proximal aorta to the proximal pulmonary artery creating a new
aorta.
ā¢ Potential complication of the arterial switch includes narrowing at
the great artery anastomosis or coronary artery insufficiency
55. Intra-atrial baffle repairs
ā¢ It is created to divert venous blood to
the mitral valve and pulmonary
venous blood to the tricuspid valve
using the septum (Stenning
procedure) or a prosthetic material
(mustard procedure)
ā¢ These are performed in the first year
of life. A disadvantage is the
continuing role of the right ventricle
as the systemic pump and the late
development of right ventricular
failure and rhythm disturbances
56. Rastelli Procedure
ā¢ It involves closure of the VSD with a
baffle directing left ventricular blood
through the VSD in to the aorta.
ā¢ The pulmonic valve is then closed and a
conduit is placed from the right ventricle
to the pulmonary artery creating a
physiologically normal circulation.
ā¢ Unfortunately this procedure requires
multiple conduit replacement as the
child grows.
57.
58. Hypoplastic Left Heart Syndrome
ā¢ Hypoplastic left heart syndrome occurs when parts of the left side
of the heart (mitral valve, left ventricle, aortic valve and aorta) do
not develop completely.
ā¢ The left ventricle is non-functional
ā¢ Thus the left side of the heart is completely unable to supply
blood to the systemic circulation
59. Defects
1. Patent foramen ovale
2. Coarctation of the aorta
3. Patent ductus arteriosus
4. Narrowed aorta
5. Hypo plastic left ventricle
6. Aortic atresia
ā¢ It is the 4th most common
congenital heart defect.
ā¢ Occurs in up to 4% of cases
of CHD
60. Pathophysiology
The right ventricle must then pump blood to the lungs and also to the systemic circulation
through PDA
Blood returning from the lungs into the left atrium must pass through an ASD to the right side of
the heart.
As a result, the right side of the heart must maintain the circulation for both the lungs and the
body.
In patient with HLHS, the left side of the heart is unable to send enough blood to the body.
61. The right ventricle can support the circulation to the both lungs
and the body for a while, but this extra workload eventually
causes the right side of the heart to fail.
A few days after birth when the ductus arteriosus closes, the
heart cannot pump blood into the systemic circulation, causing
poor perfusion of the vital organs & shock.
62. Clinical Manifestation
ā¢ The neonates are born healthy, no cyanosis, no murmur.
ā¢ But after some hours to a day or two, the infant become critically ill
and may die due to closure of ductus.
ā¢ Cyanosis
ā¢ Irritability
ā¢ Low volume pulse with hypotension
ā¢ Single heart sound
63. Investigations
ā¢ Health History: Onset of cyanosis, poor feeding, history of tiring easily
ā¢ Physical examination: Evaluate vital signs, noting tachycardia,
tachypnea, hypothermia. Observe for increased work of breathing
and gradually increasing cyanosis. Note pallor of the extremities.
ā¢ Pulse oximetry- shows decreased oxygen saturation.
ā¢ Auscultation- Adventitious breath sound, a gallop rhythm, a single
second heart sound, and a soft systolic ejection or holosystolic
murmur
ā¢ Echocardiogam- can diagnose this syndrome in prenatal period
ā¢ USG ā for prenatal diagnosis
64. Medical Management
ā¢ After diagnosis, baby will be admitted in neonatal intensive care unit.
ā¢ A ventilator may be needed for breathing support
ā¢ Prostaglandin E1 is used to keep ductus arteriosus open
65. Surgical treatment of hypo plastic left heart
syndrome
ā¢ Three separate surgeries.
ā¢ Norwood procedure
ā¢ First few days after birth.
ā¢ Glenn Shunt (Cavo Pulmonary
Connection)
ā¢ 3-9 months of age
ā¢ Fontan Procedure
ā¢ 2 years of age
ā¢ Less wait because of damage from
pulmonary hypertension
66. Norwood procedure (Stage I)
ā¢ It consist of building a new aorta by using the pulmonary
valve and artery
ā¢ Connecting the hypoplastic old aorta and coronary arteries
to the new aorta
ā¢ Removing the wall between the atrial septum
ā¢ Making an artificial connection from right ventricle to the
pulmonary artery to maintain blood flow to the lungs (called
a shunt)
67. Glenn Shunt (Stage II)
ā¢ The operation at 3 to 6 months is called a bidirectional Glenn. The
superior vena cava is detached from the heart and connected
directly to the pulmonary artery.
ā¢ This allows blood from the upper body to flow directly to the lungs
to pick up oxygen without having to be pumped by the heart.
ā¢ It also prevents blood that already has oxygen from returning to the
lungs, and, thereby, keeps the heart from doing unnecessary work.
68. Fontan Procedure (Stage III)
ā¢ IVC is connected directly to the pulmonary arteries.
ā¢ The right ventricle now serves only as the pumping chamber for the
body.
ā¢ This surgery is usually performed when the baby is 18months to
3years old.
ā¢ After this final step baby is no longer blue.
69.
70. Heart Transplantation
ā¢ In some cases, heart transplantation is considered a better choice
than the three step surgery process.
ā¢ However there are few donated hearts available for small infants.
71.
72. Total Anomalies Venous Return
ā¢ TAPVR is a congenital heart defect in which the pulmonary veins do
not connect normally to the left atrium. Instead they connect to the
right atrium, often by way of the superior venacava.
ā¢ Relatively rare, it occurs in about 1 in 17,000 live birth.
ā¢ ASD or foramen ovale is always present.
74. Supra cardiac TAPVR
ā¢ The pulmonary veins drain into
the right atrium through the
superior vena cava.
ā¢ The superior vena cava is a
large vein that normally carries
only deoxygenated, or āblue,ā
blood into the right atrium
from the upper half of the
body.
75. Infra cardiac TAPVR
ā¢ The pulmonary veins drain into the
right atrium through the liver
(hepatic) veins and the inferior
vena cava.
ā¢ The inferior vena cava is another
large vein that normally carries
only deoxygenated blood into the
right atrium from the lower half of
the body.
76. Cardiac TAPVR
ā¢ There are two types. In one, the pulmonary veins can directly enter
into the right side of the heart, into the right atrium.
ā¢ Alternatively, the pulmonary veins can drain into the coronary sinus.
The coronary sinus is a vein that normally carries deoxygenated blood
from the heart muscle into the right atrium.
ā¢ This vein is usually very small, but becomes quite large with this
abnormal amount of blood.
Mixed TAPVR
ā¢ The pulmonary veins split up and drain partially to more than one of
these options.
77. Pathophysiology
ā¢ Oxygenated blood that would normally enter the left atrium now enters
the right ventricle.
ā¢ As a result the pressure on the right side of the heart increases, leading to
hypertrophy.
ā¢ Since none of the pulmonary veins connect normally to the left atrium, the
only source of blood to the left atrium is blood that is shunted from the
right atrium across the defect to the left side of the heart.
ā¢ The highly oxygenated blood from the lungs completely mixes with the
poorly oxygenated blood returning from the systemic circulation.
ā¢ This can cause an overload of the right atrium and right ventricle.
ā¢ The increase blood volume going into the lungs can lead to pulmonary
hypertension and pulmonary edema
78. Clinical Manifestations
ā¢ In some cases, newborns with TAPVR have difficulty breathing and quickly
become very ill. This occurs when the pulmonary veins are too narrow or are
obstructed at some point, and blood canāt flow from the lungs as quickly as it
should. This is called TAPVR with pulmonary obstruction. These children are
typically transported to the Cardiac Center.
ā¢ In other cases, TAPVR is diagnosed in the first few months of life, after a child
demonstrates milder symptoms such as a heart murmur or cyanosis (blue tint to
skin).
ā¢ Blue or purple tint to lips, skin and nails (cyanosis)
ā¢ Rapid breathing or working harder while breathing, especially while eating
ā¢ Heart murmur, S2 wide and split.
ā¢ The severity of TAPVR symptoms varies.
79. ā¢ Chest X-ray: this will show right heart
enlargement and increased blood flow through
the pulmonary artery. If the veins are obstructed,
there will be pulmonary edema (buildup of fluid
in the lungs).
ā¢ Electrocardiogram (ECG): This usually shows
evidence of right heart hypertrophy, right axis
deviation.
ā¢ Echocardiogram
ā¢ Pulse oximetry
ā¢ Cardiac catheterization- to visualize the abnormal
connection of pulmonary veins particularly if an
obstruction is present.
ā¢ Cardiac MRI
Investigations
80. Management
ā¢ TAPVR require open-heart surgery in all cases.
ā¢ Critically ill newborn will have surgery immediately.
ā¢ If the child is not critically ill, Doctors may wait up to two months to
perform surgery, depending on the strength of the child and on the
heart anatomy.
81. ā¢ To understand the surgery, one important thing to know about TAPVR is that the
pulmonary veins, despite their abnormal connections to other veins, all end in a
collection (called a āconfluenceā) at the back of the left atrium.
ā¢ The surgeon opens the confluence so that the veins can drain into the left atrium.
Then he or she ties off all the abnormal connections between the pulmonary
veins and other veins, so that blood can follow only the path to the left atrium.
ā¢ The surgeon also closes septal defects (the abnormal holes) with tiny patches or
stitches, and closes the patent ductus arteriosus. As the child ages, the lining of
the heart will grow over the stitches
Surgical Management
82.
83. LIST OF NURSING DIAGNOSIS (PRE-OPERATIVE)
ā¢ Ineffective breathing pattern related to pulmonary congestion
ā¢ Decreased cardiac output related to structural defect secondary to
atrial septal defect
ā¢ Activity intolerance related to imbalance between oxygen supply and
demand
ā¢ Fluid volume excess related to compromised regulatory mechanism
secondary to heart failure
ā¢ Altered family process related to a child with life threatening illness
84. LIST OF NURSING DIAGNOSIS (POST-OPERATIVE)
ā¢ Decreased cardiac output related to increased demand of
myocardium
ā¢ Ineffective breastfeeding related to generalized weakness secondary
to postoperative status
ā¢ Risk for hyperthermia related to the infectious process secondary to
presence of IV lines, etc.
ā¢ Risk for infection related to presence of chest tube drainage
ā¢ Deficient knowledge related to the postoperative care