Interstitial lung disease (ILD) causes inflammation and scarring around the balloon-like air sacs in your lungs, called the alveoli.

1. Otsource Strategies International
Headquarters:
8596 E. 101st Street, Suite H
Tulsa, OK 74133
Interstitial Lung Diseases - Stay
Updated with ICD-10 and CPT Codes
Interstitial lung disease (ILD) causes
inflammation and scarring around the
balloon-like air sacs in your lungs,
called the alveoli.

2. www.outsourcestrategies.com 918-221-7769
Interstitial lung disease (ILD) is an umbrella term for a large
group of lung disorders that cause inflammation and
progressive scarring of lung tissue (around the balloon-like air
sacs in your lungs, called the alveoli). As oxygen travels through
the alveoli into your bloodstream, the associated scarring
affects your ability to breathe and get enough oxygen into your
bloodstream. Generally, these groups of lung disorders are
classified together as they affect the tissue and space around
the alveoli (air sacs), called the “interstitium”.Depending on the
specific disease, other compartments of the lung, including the
airways (trachea, bronchi, and bronchioles), blood vessels, and
pleura (outside lining of the lung), may also be affected.If left
untreated, these disorders can lead to a series of life-
threatening complications, including - high blood pressure in
your lungs (pulmonary hypertension), right-sided heart failure
(cor pulmonale) and respiratory failure. Diagnosis of this lung
disorder is quite challenging, and there is currently no cure for
the same. However, incorporating key lifestyle changes along
with medications can help with effective management of the
symptoms in the long-run. Pulmonologists or other specialists
dealing with lung disorders must make sure that they correctly
document all the procedures performed in the patient’s
medical records. Outsourcing medical billing and coding tasks
to a reliable and established medical billing and coding

3. www.outsourcestrategies.com 918-221-7769
company can help physicians simplify their complete
documentation procedures.
There are many types of interstitial lung disease (ILD), majority
of which affect the interstitium.According to the American
Thoracic Society, there are more than 200 different lung
disorders that affect the interstitium. Some of the common
disorders include - interstitial pneumonia, chronic silicosis,
siderosis, idiopathic pulmonary fibrosis, sarcoidosis, asbestosis
and more. The causes of ILD are several and these include –
autoimmune disorders (that damage the lungs and other
organs), long-term exposure to toxic or hazardous materials
and anti-inflammatory medications and other drugs. In some
cases, however, the causes remain unknown.
What Are the Typical Symptoms?
Interstitial lung diseases can vary from one person to another
and may depend on the specific potential causes.Symptoms can
range from mild to severe. In some cases, symptoms progress
slowly, while in other cases they worsen quickly. Most common
symptoms include – dry cough and shortness of breath at rest
or aggravated by exertion.
As and when these symptoms appear, irreversible lung damage
might havealready occurred. Therefore, it is important to
consult your physician as soon as you experience serious
breathing difficulty. Getting an early and accurate diagnosis will

4. www.outsourcestrategies.com 918-221-7769
help in proper treatment.Exposure to occupational and
environmental toxins, habit of smoking, gastroesophageal
reflux disease, age, and radiation and chemotherapy are some
of the potential risk factors associated with the condition.
Need for Early Diagnosis and Treatment of ILD
Making a clear and definitive diagnosis of ILDcan be challenging
as a large number of disorders fall into this broad category. In
addition, the signs and symptoms can often mimic other types
of medical conditions. Certain blood tests may be conducted
during the initial stage of diagnosis to detect proteins,
antibodies and other markers of autoimmune diseases or
inflammatory responses to environmental exposures, (such as
those caused by molds or bird protein).
A wide range of other diagnostic imaging tests like -
Computerized tomography (CT) scan, X-ray and pulmonary
function tests (such as Spirometry and diffusion capacity,
Oximetry) will be conducted as part of the diagnosis. In
addition, lung tissue analysis will be conducted by examining a
small amount of lung tissue (biopsy) in a laboratory. The tissue
sample may be obtained through procedures like –
Bronchoscopy, Bronchoalveolar lavage and surgical biopsy.
There are currently no treatment options that can completely
reverse the lung scarring that occurs in interstitial lung.
However, treatment modalities may help improve symptoms

5. www.outsourcestrategies.com 918-221-7769
and slow the progression of scarring, and allow a person to
breathe more freely. Pulmonologists may prescribe
medications like - corticosteroids (prednisone), pirfenidone
(Esbriet) and nintedanib (Ofev) to slow the disease progression.
As gastro esophageal reflux disease is one of the top risk factors
for ILD, physicians may prescribe medications including H-2-
receptor antagonists or proton pump inhibitors such as
lansoprazole (Prevacid 24HR), omeprazole (Prilosec OTC) and
pantoprazole (protonix) to reduce stomach acid and other
symptoms of acid reflux. In addition, oxygen therapy and
pulmonary rehabilitation can help patients improve breathing
and lung efficiency. Lung transplantation may be considered as
a last resort for people with severe interstitial lung disease who
haven't benefited from other treatment options.
Radiology medical coding involves the use of relevant diagnosis
and procedure codes to bill the procedure correctly. The
relevant ICD-10 and CPT codes to document different types of
interstitial lung diseases (ILD) include –
ICD – 10 Codes
J84 - Other interstitial pulmonary diseases
J84.0 - Alveolar and parieto-alveolar conditions
 J84.01 - Alveolar proteinosis
 J84.02 - Pulmonary alveolar microlithiasis

6. www.outsourcestrategies.com 918-221-7769
 J84.03 - Idiopathic pulmonary hemosiderosis
 J84.09 - Other alveolar and parieto-alveolar conditions
J84.1 - Other interstitial pulmonary diseases with fibrosis
 J84.10 - Pulmonary fibrosis, unspecified
J84.11 - Idiopathic interstitial pneumonia
 J84.111 - Idiopathic interstitial pneumonia, not otherwise
specified
 J84.112 - Idiopathic pulmonary fibrosis
 J84.113 - Idiopathic non-specific interstitial pneumonitis
 J84.114 - Acute interstitial pneumonitis
 J84.115 - Respiratory bronchiolitis interstitial lung disease
 J84.116 - Cryptogenic organizing pneumonia
 J84.117 - Desquamative interstitial pneumonia
J84.17 - Other interstitial pulmonary diseases with fibrosis, in
diseases classified elsewhere
J84.2 - Lymphoid interstitial pneumonia
J84.8 - Other specified interstitial pulmonary diseases
 J84.81 - Lymphangioleiomyomatosis

7. www.outsourcestrategies.com 918-221-7769
 J84.82 - Adult pulmonary Langerhans cell histiocytosis
 J84.83 - Surfactant mutations of the lung
J84.84 - Other interstitial lung diseases of childhood
 J84.841 - Neuroendocrine cell hyperplasia of infancy
 J84.842 - Pulmonary interstitial glycogenosis
 J84.843 - Alveolar capillary dysplasia with vein
misalignment
 J84.848 - Other interstitial lung diseases of childhood
J84.89 - Other specified interstitial pulmonary diseases
J84.9 - Interstitial pulmonary disease, unspecified
CPT Codes
 94010 - Spirometry Complete, includes graphic record
total and timed vital capacity, expiratory flow rate
measurement(s) with or without maximal voluntary
ventilation (94010 should not be reported with 94150,
94200, 94375, 94728)
 94011 - Measurement of spirometry forced expiratory
flows in an infant or child through 2 years of age

8. www.outsourcestrategies.com 918-221-7769
 94012 - Measurement of spirometry forced expiratory
flows, before and after bronchodilator, in an infant or child
through 2 years of age
 94013 - Measurement of lung volumes (i.e., functional
residual capacity (FRC); forced vital capacity (FVC), and
expiratory reserve volume (ERV) in an infant or child
through 2 years of age
 94014 - Patient-initiated spirometry recording per 30 day
period of time; includes reinforced education,
transmission of spirometry tracing, data capture, analysis
of transmitted data, periodic recalibration and review and
interpretation by a physician or other qualified health
professional
 94015 - [Patient-initiated spirometry] recording (includes
hook-up, reinforced education, data transmission, data
capture, trend analysis, and periodic recalibration)
 94016 - [Patient-initiated spirometry] review and
interpretation only by a physician or other qualified health
professional
 94060 - Bronchodilation Responsiveness, spirometry as in
94010, pre- and post bronchodilator administration.
(94060 should not be reported with 94150, 94200, 94375,

9. www.outsourcestrategies.com 918-221-7769
94640, and 94728. For prolonged exercise test for
bronchospasm with pre- and post-spirometry use 94620)
 94070 - Bronchspasm provocation evaluation, multiple
spirometric determination as in 94010, with administered
agents (eg. antigen(s), cold air, methacholine)
 94150 - Vital capacity, total (separate procedure) (Do not
report in conjunction with 94010, 94060, 94728)
 94200 - Maximum breathing capacity, maximum voluntary
ventilation. (Do not report in conjunction with 94010,
94060).
 94250 - Expired gas collection, quantitative, single
procedure (separate procedure).
 94375 - Respiratory flow volume loop (Do not report in
conjunction with 94010, 94060, 94728)
 94400 - Breathing response to CO2 (CO2 response curve).
 94450 - Breathing response to hypoxia (hypoxia response
curve) (For high altitude simulation test (HAST) see 94452,
94453).
 94452 - High altitude simulation test (HAST) with
interpretation and report by a physician or other qualified
health professional (Do not report in conjunction with
94453, 94760, 94761)

10. www.outsourcestrategies.com 918-221-7769
 94453 – (HAST) with supplemental oxygen titration (Do
not report in conjunction with 94452, 94760, 94761).
 94620 - Pulmonary stress test simple.
 94621 - Pulmonary stress test, complex (including
measurement if CO2 production, O2 uptake, and
electrocardiographic recordings).
 94680 - Oxygen uptake, expired gas analysis, rest and
exercise, direct, simple
 94681 - [Oxygen uptake] including CO2 output, percentage
oxygen extracted.
 94690 - [Oxygen uptake] rest, indirect (separate
procedure)
 94726 - Plethysmography for determination of lung
volumes and when performed, airway resistance (Do not
report in conjunction with 94727)
 94727 - Gas dilution or washout for determination of lung
volumes, and when performed distribution of ventilation
and closing volume (Do not report in conjunction with
94726)
 94728 - Airway resistance by impulse oscillometry (Do not
report in conjunction with 94010, 94060, 94070, 94375,
94726).

11. www.outsourcestrategies.com 918-221-7769
 94729 - Diffusing capacity (Must be reported in
conjunction with 94010, 94060, 94070, 94375, 94726,
94727 or 94728).
Living with chronic interstitial lung disease is really challenging.
Getting actively involved in treatment programs and staying as
healthy as possible are essential to living with ILD. Eating a
balanced healthy diet, quitting the habit of smoking and getting
vaccinated (to prevent respiratory infections) can help reduce
the complications associated with ILD and prevent its
symptoms in the long-run.
Medical coding for various lung disorders can be difficult. With
all the complexities involved, the support of a reliable medical
billing and coding outsourcing company can assist in timely
medical billing and claims submission for optimal
reimbursement.