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1
Syncope: Sudden, transient LOC associated with an
absence of postural tone secondary to relatively abrupt
cerebral hypo perfusion
SCD: Unexpected natural death from a cardiac cause
within a short time period, generally ≤1 hour from the
onset of symptoms, in a person with a known or unknown
cardiac cause
What???
4
5
Syncope: Children & adolescence
• Unlike adults: Cardiac abnormality as a cause of syncope: Rare
Autonomic syncope
Vasovagal syncope
Postural hypotension
Dyautonomia
6
Breath-holding spells Pallid spells Cyanotic spells
6 months-6Y 1Y--2Y 6months -2Y
Iron deficency Early form of VVS VSD+ PS physiology
7
Syncope: Evaluation to be done seriously
Main purpose is to determine whether the child
has increased risk of death
8
Suspect cardiac
syncope
• Lack of prodrome
• Palpitations/ chest pain
• Cardiac murmur/CVS exam
• Exercise induced syncope
• Family H/o-SCD/
arrhythmia/early death
• Previous h/o of cardiac
disease
Refer to
cardiologist
9
10
•BRUGADA SYNDROME
11
Brugada syndrome
RBB pattern
ST/J point elevation / coving pattern
V1-V3 leads
12
Management
13
Quinidine
Epicardial ablation
Fever treatment
14
•LQTS
15
16
17
18
19
20
21
22
•SQTS
23
• ICD: Therapy of choice
• Propafenone/ quinidine/
sotalol: May help prolong QTi
and decrease potential for VF
24
•CPVT
25
CPVT: Catecholaminergic polymorphic ventricular
tachycardia
Flecanide, Verapamil
LCSD
26
Non cardiac
IEM
Metabolic
Downs syndrome
5% channelopathies
27
28
Take home message…
• Exertional syncope: Points to cardiac cause of syncope
• All Syncope cases: Consider arrhythmia—> Get ECG done
• Inherited arrhythmias—> High index suspicion and genetic
testing of patient and family
• SCD: Warning and prodromal symptoms—> Taken seriously
and evaluated—> Prevent SCD
29
THANK YOU…
murtaza.vmmc@gmail.com
+91-9971259799
30

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PEDIATRIC SUDDEN CARDIAC DEATH, SYNCOPE, INHERITABLE ARRHYTHMIAS

Editor's Notes

  1. Syncope when, episodes previous, posture, duration, excertional, assoc symp, family--SCD