7. CARDIOPATIAS CONGENITAS CIANOTICAS CON FLUJO
PULMONAR DISMINUIDO
TETRALOGIA DE FALLOT
4 componentes descritos por primera vez en 1888
CIV
Estenosis pulmonar (infundibular)
Cabalgamiento aórtico
Hipertrofia VD (pacientes con largo tiempo de evolución)
10-11% de Todos los casos de C.C
Hallazgos en RX de Tórax
Corazón en forma de ´´bota´´
RadioGraphics 2007
Figure 5. (c) Drawing depicts the pattern of blood flow
(arrows) with the characteristic ventricular septal defect (1),
infundibular pulmonary stenosis (2), overriding aorta (3), and
right ventricular hypertrophy (4). The oxygen-rich blood in the
left side of the heart (5) mixes with oxygen-poor blood in the
right side of the heart (6) before it proceeds to the aorta (7).
8. Figure 5. Tetralogy of Fallot. (a, b) Chest radiograph obtained in an infant with a right-sided aortic arch (b the same as a with a superimposed drawing) shows
the characteristic boot-shaped sign produced by upturning of the cardiac apex because of right ventricular hypertrophy and by the concavity of the main
pulmonary artery.
RadioGraphics 2007
9. CARDIOPATIAS CONGENITAS CIANOTICAS CON FLUJO PULMONAR DISMINUIDO
ATRESIA PULMONAR CON CIV
Evaluación en pacientes con Concordancia A-V y V-Arterial
Comportamiento tipo FALLOT EXTREMO
Ausencia de Flujo Pulmonar
Evaluación morfológica de la arteria Pulmonar: Planeamiento Qx
Puede estar presente o Ausente
Forma de Flujo Pulmonar
Multifocal
PDA
Vasos colaterales Aorto-Pulmonares
Afectación de vascular y parenquimal pulmonar.
RadioGraphics 2007
10. Figure 19. Pulmonary atresia with VSD. LPA left pulmonary artery, RPA right pulmonary artery. (a) CT scan shows the confluent portion of the
central pulmonary artery (arrowheads). (b) CT scan shows absence of the confluent portion of the central pulmonary artery (*). Each pulmonary
artery was supplied by a corresponding PDA (not shown).
RadioGraphics 2007
11. CARDIOPATIAS CONGENITAS CIANOTICAS CON FLUJO
PULMONAR DISMINUIDO (CON CARDIOMEGALIA)
ANOMALIA DE EBSTEIN
Descrita por primera vez en 1866
0.5-0.7 % de todos los casos de cardiopatía
congénita
Fuerte Asociación entre la ingesta de LITIO y la
presentación de A. Ebstein
Característica Importante
Aorta y T. Pulmonar: Ambos disminuidos de calibre
Desplazamiento caudal de las hojas de la V.
Tricuspide.
Formación de cámara V-A común derecha:
REGURGITACIÓN TRICUSPIDEA
Insuficiencia Tricuspidea: Dilatación del Tracto de
Salida V.D
Incremento de la cámara auricular derecha
Cianosis: SHUNT D-I a través de CIA
RadioGraphics 2007
(d) Drawing shows the pattern of blood flow (arrows) caused by downward
displacement of the tricuspid valve (1), with resultant formation of a common
chamber (3) consisting of the right ventricle (2) and the dilated right atrium
(4), and by the right to- left shunt of blood through a defect at the atrial level
(5). 6 left atrium, 7 left ventricle, 8 aorta, 9 pulmonary artery.
12. Figure 9. Ebstein anomaly. (a, b) Frontal (a) and lateral (b) views obtained with chest radiography in an infant show massive cardiomegaly with
decreased pulmonary flow. (c) Frontal view (same as a with a superimposed drawing) best depicts the box-shaped heart, an appearance caused
by enlargement of the right atrium and hypoplasia of the pulmonary trunk.
RadioGraphics 2007
13. Figure 9. Ebstein anomaly. (a, b) Frontal (a) and lateral (b) views obtained with chest radiography in an infant show massive cardiomegaly with
decreased pulmonary flow. (c) Frontal view (same as a with a superimposed drawing) best depicts the box-shaped heart, an appearance caused
by enlargement of the right atrium and hypoplasia of the pulmonary trunk.
RadioGraphics 2007
14. CARDIOPATIAS CONGENITAS CIANOTICAS CON FLUJO PULMONAR
AUMENTADO
TRANSPOSICIÓN DE GRANDES VASOS
Cardiopatía congénita cianótica mas frecuente en
NEONATOS
5-7% de las Cardiopatías congénitas
Mas común en hijos de madres con D.M
90% se presenta de forma aislada
CARACTERISTICAS
DISCORDANCIA VENTRICULO-ARTERIAL
Borde Auricular Derecho
Aurícula Izquierda Agrandada
PRESENCIA COMUNICACIÓN
Foramen Oval
CIA
CIV
FLUJO PULMONAR: NORMAL AL NACIMIENTO (D.A)
RadioGraphics 2007
(d) Drawing shows the pattern of blood flow (arrows) through the heart with
transposition of the great arteries. The aorta (1) arises from the right ventricle (2), and
the pulmonary artery (3) arises from the left ventricle (4). Communication between the
systemic and the pulmonary circulation—an interatrial septal defect (5), an
interventricular septal defect (6), or both—sustains life by allowing oxygenated blood
from the left atrium (7) to mix with deoxygenated blood from the right atrium (8) before it
flows via the right ventricle to the aorta and via the left ventricle to the pulmonary artery.
15. Figure 1. Transposition of the great arteries (a) Chest radiograph obtained in a neonate shows narrowing of the superior mediastinum, enlargement of the cardiac
silhouette with abnormal convexity of the right atrial border, and increased vascular flow—typical features of transposition of the great arteries. (b) Same image as a with
a superimposed drawing shows the characteristic cardiomediastinal silhouette: the egg-on-a-string sign.
RadioGraphics 2007
16.
17. CARDIOPATIAS CONGENITAS CIANOTICAS CON
FLUJO PULMONAR AUMENTADO
ATRESIA TRICUSPIDEA
Aurícula Derecha no tiene comunicación con
V.D.
Dos Tipos
Tipo I
Ausencia de Comunicación Atrio-
ventricular.
Tipo II
Válvula Tricúspide Atrésica esta
presente.
Figure 21. Tricuspid atresia. CT scan shows fatty tissue (arrowheads)
between the right atrium (RA) and the right ventricle (RV), which prevents any
direct connection between the two compartments. This case represents the
more common type of tricuspid atresia.
18. CARDIOPATIAS CONGENITAS CIANOTICAS CON FLUJO PULMONAR AUMENTADO
TRONCO ARTERIOSO
• Poco frecuente pero con alta tasa de letalidad
• Periodo Neonatal e Infancia temprana
• Origen común de arteria Aorta y Pulmonar
• Tipos
• Tipo I (Mas común : 48%)
• Tipo II
• Tipo III
• Tipo IV
FIGURE 45-1 Collett and Edwards classification:
type I, a pulmonary trunk connects the common
arterial trunk to the branch pulmonary arteries; type
II, branch pulmonary arteries arise closely from the
common arterial trunk; type III, branch pulmonary
arteries arise far apart from the common arterial
trunk; type IV, branch pulmonary arteries arise from
the descending aorta. LPA, left pulmonary artery;
RPA, right pulmonary artery.
Cardiovascular Imaging - Vincent B. Ho,
MD, MBA, FAHA
19. FIGURE 45-3
ECG gated CT scan of a Van Praagh and Van Praagh type 2
truncus arteriosus.
Volume rendered image shows the left pulmonary artery
(LPA) and the right pulmonary artery (RPA) arising
separately from the common arterial trunk (TA).
The LPA is typically positioned above the RPA. The topmost
branch is the left carotid artery (LCA).
Cardiovascular Imaging - Vincent B. Ho, MD, MBA, FAHA
20. FIGURE 45-4
ECG gated CT scan of a Van Praagh and Van Praagh type 3
truncus arteriosus.
Volume rendered image shows the right pulmonary artery (RPA)
arising from the common arterial trunk (TA).
The left pulmonary artery is connected by a major
aorticopulmonary collateral artery (MAPCA) to the descending
aorta (DA).
Cardiovascular Imaging - Vincent B. Ho, MD, MBA, FAHA