Nager syndrome is similar to HFM but also includes preaxial limb anomalies such as hypoplastic or aplastic thumbs and radial hypoplasia. It also involves agenesis of the soft palate, known as the "sign post" sign, as well as ear defects and TMJ ankyloses.

1. Nager syndrome
Similar to HFM but with
 preaxial limb anomalies (hypoplastic or aplastic thumbs most commonly
but radial hypoplasia
 Agenesis of the soft palate ‘’sign post’’ sign
 Ear defects
 TMJ ankyloses