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Wilms tumor
– imaging findings
= nephroblastoma
malignant
in 1-8 years age
commonly < 5 years age
large, well-defined
claw sign with the kidney
pseudocapsule – hypo T2
heterogeneous
hemorrhage, necrosis, cysts
fibrous septae
Ca++ rare, 15%
hypoenhancing
venous invasion – renal vein, IVC, heart cavities
adenopathy
pulmonary metastases
look for nephroblastomatosis
assess the other kidney – rare synchronous tumors
if ascites, suspect tumor rupture
pulmonary mets, CXR or CT for staging
Remember
large heterogeneous renal mass
with venous invasion in 1-8 years age

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