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DEAFNESS
IN CHILDREN
TYPES OF DEAFNESS
► Conductive
► Sensory
► Neural
► Mixed
► Non organic
CONGENITAL DISORDERS
► Genetic
► Non genetic
► Congenital disorders in childhood
CAUSES OF CONDUCTIVE
       DEAFNESS
► Down syndrome
► Marfan syndrome
► Treacher Collin Syndrome
► Osteogenesis imperfecta
► Otosclerosis
CONGENITAL DISORDERS
      CAUSING OME
► Cystic fibrosis
► Immotile cilia syndrome
► Cleft palate
► Immune deficiency disease
ACQUIRED CAUSES OF
     CONDUCTIVE DEAFNESS
► Inflammation
   Trauma
   Foreign body
► Wax
► Otitis externa
► ASOM
► CSOM
► OME
CAUSES OF
SENSORINEURAL DEAFNESS
► Genetic
   Inherited dominant recessive x-linked
► Non-genetic
     Infections
     Ototoxic drugs
     Metabolic disorders
     Inherited dominant, recessive x-linked trait
     Rubella, CMV, Toxoplasmosis, Syphilis, HSV
PERINATAL CAUSES
► Ototoxic drugs
► Radiation
► Ultrasound
► Maternal diabetes
     Hypoxia
     Hyperbilirubinemia
     Preterm delivery
     Low birth weight
DEAFNESS IN CHILDREN
Hearing centre   80% maturation by two years
                 98% by 5 years
stimulation



Speech centre



Development of speech   Larynx, tongue, oral cavity, pharynx
RISK FACTORS FOR HEARING
          IMPAIRMENT
► Positive family history
► Intrauterine infection
    Rubella, Syphilis, CMV, Toxo (TORCH)
► Anatomical abnormalities (Ear,Head,Neck)
► Low birth weight < 1500 g
► Neonatal asphyxia
► Hyperbilirubinaemia
► Bacterial meningitis
► Ototoxic drugs
EARLY SCREENING AND
          MANAGEMENT
► Before 2 years   Excellent
► 2-5 years        Good
► After 5 years    Poor
Neonatal responses
► Startling reflex (Responds to loud sound)
► Aural-palpebral reflex
► Change in heart rate
► Change in pattern of respiration
► Backward head jerk
► Moro reflex (increase in general body
 activity)
Aged 4 months
► Child notices sound
► Responds by stilling and listening
► Child becomes still and smiles to a parent’s
 voice
Aged 6 months

► Begins to turn its head to the source of
 sound
Aged 9 months

► Localizes quite sound on a horizontal plane
► Turns readily to a parent’s voice
► Search for source of sound
Aged 12 months

► Localized quiet sound on any plane
► Can speak single words
Aged 24 months
► Readily localized sound and search for
  sound source
► By 18 months answers to simple questions
  like “where is your nose?”
► By 2 years picks out toys on request
► Simple speech assessment can be
  introduced
SUSPICION OF DEAFNESS
► Non-development of speech
► Inattentive child
► Hyperactive child
► Non-responding
► Poor performance at school
LEVEL OF DEAFNESS
► Normal hearing          0-20dB
► Mild hearing loss       20-40dB
► Moderate hearing loss   40-60dB
► Severe hearing loss     > 80 dB
► Complete hearing loss   No response
                          upto 110 Db
Pre-lingual deafness
Post-lingual deafness
AUDIOLOGICAL ASSESSMENT

► Pure tone audiogram
► Tympanogram
► Brainstem evoked response audiometry
  (BERA)
► Confirm the degree of deafness, type and
  level of deafness
PREVENTION
► Prevention
► Treatment of underlying cause
► Hearing aid
► Cochlear implant
THANK YOU

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Congenital deafness

  • 1.
  • 3. TYPES OF DEAFNESS ► Conductive ► Sensory ► Neural ► Mixed ► Non organic
  • 4. CONGENITAL DISORDERS ► Genetic ► Non genetic ► Congenital disorders in childhood
  • 5. CAUSES OF CONDUCTIVE DEAFNESS ► Down syndrome ► Marfan syndrome ► Treacher Collin Syndrome ► Osteogenesis imperfecta ► Otosclerosis
  • 6. CONGENITAL DISORDERS CAUSING OME ► Cystic fibrosis ► Immotile cilia syndrome ► Cleft palate ► Immune deficiency disease
  • 7. ACQUIRED CAUSES OF CONDUCTIVE DEAFNESS ► Inflammation  Trauma  Foreign body ► Wax ► Otitis externa ► ASOM ► CSOM ► OME
  • 8. CAUSES OF SENSORINEURAL DEAFNESS ► Genetic  Inherited dominant recessive x-linked ► Non-genetic  Infections  Ototoxic drugs  Metabolic disorders  Inherited dominant, recessive x-linked trait  Rubella, CMV, Toxoplasmosis, Syphilis, HSV
  • 9. PERINATAL CAUSES ► Ototoxic drugs ► Radiation ► Ultrasound ► Maternal diabetes  Hypoxia  Hyperbilirubinemia  Preterm delivery  Low birth weight
  • 10. DEAFNESS IN CHILDREN Hearing centre 80% maturation by two years 98% by 5 years stimulation Speech centre Development of speech Larynx, tongue, oral cavity, pharynx
  • 11. RISK FACTORS FOR HEARING IMPAIRMENT ► Positive family history ► Intrauterine infection  Rubella, Syphilis, CMV, Toxo (TORCH) ► Anatomical abnormalities (Ear,Head,Neck) ► Low birth weight < 1500 g ► Neonatal asphyxia ► Hyperbilirubinaemia ► Bacterial meningitis ► Ototoxic drugs
  • 12. EARLY SCREENING AND MANAGEMENT ► Before 2 years Excellent ► 2-5 years Good ► After 5 years Poor
  • 13. Neonatal responses ► Startling reflex (Responds to loud sound) ► Aural-palpebral reflex ► Change in heart rate ► Change in pattern of respiration ► Backward head jerk ► Moro reflex (increase in general body activity)
  • 14. Aged 4 months ► Child notices sound ► Responds by stilling and listening ► Child becomes still and smiles to a parent’s voice
  • 15. Aged 6 months ► Begins to turn its head to the source of sound
  • 16. Aged 9 months ► Localizes quite sound on a horizontal plane ► Turns readily to a parent’s voice ► Search for source of sound
  • 17. Aged 12 months ► Localized quiet sound on any plane ► Can speak single words
  • 18. Aged 24 months ► Readily localized sound and search for sound source ► By 18 months answers to simple questions like “where is your nose?” ► By 2 years picks out toys on request ► Simple speech assessment can be introduced
  • 19. SUSPICION OF DEAFNESS ► Non-development of speech ► Inattentive child ► Hyperactive child ► Non-responding ► Poor performance at school
  • 20. LEVEL OF DEAFNESS ► Normal hearing 0-20dB ► Mild hearing loss 20-40dB ► Moderate hearing loss 40-60dB ► Severe hearing loss > 80 dB ► Complete hearing loss No response upto 110 Db Pre-lingual deafness Post-lingual deafness
  • 21. AUDIOLOGICAL ASSESSMENT ► Pure tone audiogram ► Tympanogram ► Brainstem evoked response audiometry (BERA) ► Confirm the degree of deafness, type and level of deafness
  • 22. PREVENTION ► Prevention ► Treatment of underlying cause ► Hearing aid ► Cochlear implant