Tricuspid atresia

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Some babies with tricuspid atresia have other conditions, such as pulmonary stenosis or transposition of the great arteries, that also affect blood flow through their heart. These conditions require treatment, too.

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Tricuspid atresia

  1. 1. Tricuspid atresia   http://en.wikipedia.org/wiki/Tricuspid_atresia
  2. 2. <ul><li>is a form of  congenital heart disease  whereby there is a complete absence of the  tricuspid valve . Therefore, there is an absence of right atrioventricular connection. This leads to a  hypoplastic  (undersized) or absent  right ventricle . </li></ul>
  3. 3. <ul><li>This defect is contracted during prenatal development, when the heart does not finish developing. It causes the heart to be unable to properly oxygenate the rest of the blood in the body. Because of this, the body does not have enough oxygen to live, and steps must be taken to keep the child alive. Because of the lack of an A-V connection, an  atrial septal defect  (ASD)  must  be present to maintain blood flow. </li></ul>
  4. 4. <ul><li>Also, since there is a lack of a right ventricle there  must  be a way to pump blood into the  pulmonary arteries , and this is accomplished by a  ventricular septal defect  (VSD). </li></ul>
  5. 5. <ul><li>Blood is mixed in the  left atrium . Because the only way the pulmonary circulation receives blood is through the VSD, a  patent ductus arteriosus  is usually also formed to increase pulmonary flow. </li></ul>
  6. 6. Clinical manifestations <ul><li>progressive  cyanosis </li></ul><ul><li>poor feeding </li></ul><ul><li>tachypnea  over the first 2 weeks of life </li></ul><ul><li>holosystolic   murmur  due to the VSD </li></ul><ul><li>left axis deviation  on  electrocardiography  and  left ventricular hypertrophy  (since it must pump blood to both the pulmonary and systemic systems) </li></ul><ul><li>normal  heart size </li></ul>
  7. 7. Other heart problems <ul><li>Some babies with tricuspid atresia have other conditions, such as  pulmonary stenosis  or  transposition of the great arteries , that also affect blood flow through their heart. These conditions require treatment, too. </li></ul>
  8. 8. Treatment <ul><li>PGE1  to maintain  patent ductus arteriosus </li></ul><ul><li>modified  Blalock-Taussig  shunt to maintain pulmonary blood flow by placing a  Gore-Tex  conduit between the  subclavian artery  and the pulmonary artery . </li></ul><ul><li>cavopulmonary anastomosis ( hemi-Fontan  or  bidirectional Glenn ) to provide stable pulmonary flow </li></ul><ul><li>Fontan procedure  to redirect  inferior vena cava  and  hepatic vein  flow into the pulmonary circulation </li></ul>

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