What is dentinogenesis imperfecta? <ul><li>Dentinogenesis imperfecta is a disorder of tooth development. This condition causes the teeth to be discolored (most often a blue-gray or yellow-brown color) and translucent. Teeth are also weaker than normal, making them prone to rapid wear, breakage, and loss. These problems can affect both primary (baby) teeth and permanent teeth. </li></ul>
How common is dentinogenesis imperfecta? <ul><li>Dentinogenesis imperfecta affects an estimated 1 in 6,000 to 8,000 people. </li></ul>
Types <ul><li>Types of dentinogenesis imperfecta with similar dental formalities usually an autosomal dominant trait with variable expressivity but can be recessive if the associated osteogenesis imperfecta is of recessive type. This type is no l </li></ul><ul><li>Type II : Occurs in people without other inherited disorders.It is an autosomal dominant trait. A few families with type II have progressive hearing loss in addition to dental abnormalities. </li></ul><ul><li>Mutations in the DSPP gene have been identified in people with type II and type III dentinogenesis imperfecta. Type I occurs as part of osteogenesis imperfecta. </li></ul>
Histology <ul><li>Dentinal tubules are irregular and are bigger in diameter. Areas of uncalcified matrix are seen. Sometimes odontoblasts are seen in dentin. </li></ul>
Radiographic features <ul><li>Type I and II show total obliteration of the pulp chamber. </li></ul><ul><li>Type III shows thin dentin and extremely enormous pulp chamber.These teeth are usually known as Shell Teeth . </li></ul>
How do people inherit dentinogenesis imperfecta? <ul><li>This condition is inherited in an autosomal dominant pattern, which means one copy of the altered gene in each cell is sufficient to cause the disorder. </li></ul><ul><li>In most cases, an affected person has one parent with the condition. </li></ul>
Treatment <ul><li>One treatment option is bonding, putting lighter enamel on the weakened enamel of the teeth and with lots of treatments of this bonding, the teeth appear whiter to the eye, but the teeth on the inside and under that cover are still the same. </li></ul><ul><li>Due to the weakened condition of the teeth, many common cosmetic procedures such as braces and bridges are inappropriate for patients with Dentinogenesis imperfecta and are likely to cause even more damage than the situation they were intended to correct. </li></ul>
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