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BRUGADA SYNDROME A Brief Overview
What is Brugada Syndrome?	 ,[object Object]
Hereditary-60% of Brugada patients have a family history of SCD
A Few Facts ,[object Object]
Arrhythmias frequently occur during sleep
More common in certain ethnic groups,[object Object]
First described at NASPE meeting in 1991
Review of literature estimates that Brugada causes 4-12% of unexpected sudden deaths worldwide -Plus up to 50% of SCD in patients with normal hearts
Patient Characteristics ,[object Object]
Predominantly male
No structural heart disease,[object Object]
Pseudo RBBB,[object Object]
              Signs & Symptoms ,[object Object]
Syncope- typically due to NSVT	-Check for family history of SCD 	-Perform PES ,[object Object],[object Object]

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Brugada Syndrome: Genetic Cardiac Sodium Channel Abnormality

Editor's Notes

  1. Polymorphic VT
  2. SE Asia- problem has been know for decades. In Thailand, it is called Lai Tai (death during sleep)
  3. May be a higher percentage due to unfamiliarity with disease- “you see only what you look for- you recognize only what you know”
  4. Causes of EKG variance
  5. Confirms diagnosis of Brugada syndrome, and pt can be treated accordingly.
  6. Hopefully, more and more will be discovered about this condition, so we can identify the patients at risk and get them the treatment they need.