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Idiopathic fibrosing mediastinitis
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Idiopathic fibrosing mediastinitis

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    Idiopathic fibrosing mediastinitis Idiopathic fibrosing mediastinitis Presentation Transcript

    • I diopat hic Fibr osing Mediast init isOne Per son , One Voice , One Mission, I will make a Dif f er ence!
    • I diopat hic Fibr osing Mediast init is
    • I diopat hic Fibr osing Mediast init is
    • Gener al DiscussionM diastinal fibro sis is the le ast co mmo n, but the mo st se ve re , late co mplicatio n o f Histo plasmo sis. e M physicians be lie ve me diastinal fibro sis to be an abno rmal immuno lo g ic re spo nse to any antig e ns re le ase d by the so il-base d fung us Histo plasma capsulatum. I sho uld be t diffe re ntiate d fro m the many o the r le ss-se ve re me diastinal co mplicatio ns o f Histo plasmo sis, and fro m o the r cause s o f me diastinal fibro sis, which are te rme d idio pathic me diastinal fibro sis. I pathic Fibro sing M diastinitis is e ve n le ss co mmo n, but may have multiple dio e cause s, no ne o f which are re late d to Histo plasmo sis. A rding ly, the re are two type s o f cco Fibro sing M diastinitis; Histo plasmo sis-re late d Fibro sing M diastinitis, and idio pathic e e Fibro sing M diastinitis which may have multiple cause s unre late d to Histo plasmo sis. e B th type s are rare diso rde rs cause d by pro life ratio ns o f co llag e n, fibro sis tissue and asso ciate d o inflammato ry ce lls within the me diastinum (the space be twe e n the lung s). Po st Histo plasmo sis me diastinal fibro sis is characte rize d by invasive , calcifie d fibro sis ce nte re d o n lymph no de s, which, by de finitio n, o cclude s majo r ve sse ls o r airways. Ofte n sympto ms o f Fibro sing M diastinitis do no t de ve lo p until the dise ase has pro g re sse d to a e le ve l at which the re is damag e to so me ve sse l o r o rg an. The build up o f the scar tissue can be slo w g ro wing in so me case s and in o the rs the scar tissue may g ro w at a rapid rate .
    • Sympt oms of I diopat hic FM? Po ssibly chro nic co ug h, nig ht swe ats, fe ve r, fluid accumulatio n in the lung s and pe ricardial sac, sho rtne ss o f bre ath, che st pain wo uld be include d.I pathic FMcan have any o r all o f the sympto ms liste d abo ve . Othe r sympto ms may dio include swe lling o f face , ne ck and arms fro m co mpre ssio n o f the supe rio r ve na cava. So me patie nts with this fo rm o f FMmay also have fibro sis in re mo te lo catio ns, including the ne ck, the thyro id g land, o r be hind the abdo me n (re tro pe rito ne um), which may cause sympto ms re late d to dise ase in tho se site s.Co ug h and sho rtne ss o f bre ath o ccur with many lung dise ase s, so the y are no nspe cific sympto ms. I I pathic FMco ug h may be re late d to the dire ct co mpre ssio n o n the n dio airways, o r to fluid accumulatio n in the lung cause d by co mpre ssio n o f ve sse ls. The circulato ry syste m can be affe cte d by dire ct co mpre ssio n o f the pulmo nary arte rie s (which carry blo o d to the lung s) o r the pulmo nary ve ins (which carry blo o d fro m the lung s). Co mpre ssio n o f the supe rio r ve na cava may cause swe lling o f face o r arms, and e nlarg e me nt o f the ve ins o n the che st.
    • I diopat hic FM B cause the re are so fe w patie nts with I pathic FM re liable info rmatio n abo ut re spo nse to e dio , tre atme nt is scarce . The o nly tre atme nt data is fro m re po rts abo ut sho rt te rm tre atme nt o f individual patie nts. So me re po rts de scribe re spo nse s o f individual patie nts to pre dniso ne o r tamo xife n, but we ne e d be tte r info rmatio n abo ut the mag nitude o f re spo nse , its duratio n, and fo r what pe rce nt o f patie nts. A nswe r Fro m Do cto r Jame s Lo yd o n de ath,I my e xpe rie nce the po st Histo -re late d fo rm o f FMappe ars to be far mo re co mmo n, pe rhaps 1 0 n time s as co mmo n as diffuse pro life rative I pathic FM Ihave se e n abo ut 1 0 0 patie nts with dio . po st Histo FMduring the past 20 ye ars, and abo ut 1 0 patie nts with the I pathic diffuse fo rm dio in the past 8 ye ars. Patie nts in who m FMaffe cts bo th lung s are at the g re ate st risk, and appro ximate ly 1 0 -20 % o f patie nts with the po st Histo fo rm have bo th lung s affe cte d. Ikno w se ve ral patie nts (e le ve n) who die d fro m FMaffe cting bo th lung s, usually be cause o f re spirato ry failure o r he art failure . B cause the I pathic fo rm is far le ss co mmo n, the re is e dio far le ss info rmatio n abo ut the risk o f de ath fro m it. Ihave se e n so me patie nts in who m this dise ase cause d se rio us o bstructio n, so it has the po te ntial to be life thre ate ning ,
    • Super ior vena cava syndr ome
    • Super ior vena cava syndr omeSupe rio r ve na cava syndro me : The sympto ms that re sult fro m co mpre ssio n o f the larg e ve in that carrie s blo o d do wn to the he art. The supe rio r ve na cava is a larg e ve in that transmits blo o d fro m the uppe r bo dy back to the he art. The supe rio r ve na cava is lo cate d in the middle o f the che st and is surro unde d by rig id structure s and lymph no de s. The structure bo rde ring the supe rio r ve na cava include the trache a, ao rta, thymus, rig ht bro nchus o f the lung and pulmo nary arte ry.Co mpre ssio n o f the supe rio r ve na cava by dise ase o f any o f the structure s o r lymph no de s surro unding the supe rio r ve na cava can cause the supe rio r ve na cava syndro me . The supe rio r ve na cava syndro me is characte rize d by swe lling o f the face , ne ck and/o r arms with visible wide ning (dilatio n) o f the ve ins o f the ne ck. Patie nts o fte n have a pe rsiste nt co ug h and sho rtne ss o f bre ath. O the rs sympto ms can be pre se nt including ho arse ne ss, swe lling aro und the e ye s, fatig ue , che st pain, he adache s, and dizzine ss.
    • Super ior vena cava syndr ome The cause s o f the supe rio r ve na cava syndro me include cance r (malig nancie s) and no n-cance r (be nig n) co nditio ns. The co mmo n fo rms o f cance r that can cause the supe rio r ve na cava syndro me are lung cance r, lympho ma (cance r o f the lymph no de s), and cance r that has spre ad (me tastasis) to the che st, mo re co mmo nly bre ast and te sticular cance r. N n-cance r cause s o f the supe rio r ve na cava syndro me o include infe ctio ns (such as tube rculo sis, fung us, and syphilis), be nig n tumo rs (such as te rato mas, thymo ma, de rmo id cyst), ao rtic ane urysm, pe ricarditis, sarco ido sis, irradiatio n tre atme nt to the che st, air in the che st (pne umo tho rax), and co mplicatio n o f ce ntral line cathe te rs and co ng e nital he art surg e ry. The diag no sis o f supe rio r ve na cava syndro me can be made with the typical finding s abo ve . The diag no sis is suppo rte d by ide ntifying a cause fo r the supe rio r ve na cava syndro me , typically re q uiring X-ray imag ing o r CA o r M scanning . T RIThe tre atme nt o f supe rio r ve na cava syndro me is dire cte d to ward the e xact unde rlying cause . The re fo re , tre atme nt mig ht include radiatio n tre atme nt, antibio tics, che mo the rapy, clo t-busting (thro mbo lytic) drug s, blo o d thinne rs (antico ag ulatio n), and ballo o n ang io plasty, and e ve n surg e ry. The o utlo o k fo r patie nts with the supe rio r ve na cava syndro me de pe nds o n the unde rlying cause .
    • I diopat hic pulmonar y f ibr osis
    • I diopat hic pulmonar y f ibr osis I pathic pulmo nary fibro sis is scarring o r thicke ning o f the lung s witho ut a kno wn cause . dio Cause s, incide nce , and risk facto rsN o ne kno ws what cause s idio pathic pulmo nary fibro sis o r why so me pe o ple g e t it. I cause s the o t lung s to be co me scarre d and stiffe ne d. This stiffe ning may make it incre asing ly difficult to bre athe . I so me pe o ple the dise ase g e ts wo rse q uickly (o ve r mo nths to a fe w ye ars), but o the r n pe o ple have little wo rse ning o f the dise ase o ve r time . The co nditio n is be lie ve d to be due to an inflammato ry re spo nse to an unkno wn substance o r injury. " I pathic" me ans no cause can be fo und. The dise ase o ccurs mo st o fte n in pe o ple dio be twe e n 50 and 7 0 ye ars o ld. Sympto ms Che st pain (o ccasio nally) Co ug h (usually dry) De cre ase d to le rance fo r activity Sho rtne ss o f bre ath during activity (this sympto m lasts fo r mo nths o r ye ars, and o ve r time may also o ccur whe n at re st)N kno wn cure e xists fo r idio pathic pulmo nary fibro sis. Unfo rtunate ly, no me dicatio n has be e n o sho wn to impro ve the o utco me o f patie nts with this co nditio n.
    • Lumbo-sacr al or LumberLumbo -sacral dise ase is a te rm use d to de scribe co mpre ssio n o f the ne rve ro o ts and spinal co rd as the y pass thro ug h the lumbo -sacral po rtio n o f the lo we r spine , which is the lo we r back ne ar the hips. The lumbar spine is made up o f five ve rte bral bo die s in the lo we r back. N rve s e co ming o ff the spinal co rd trave l tho ug h the spinal canal and e xit the canal thro ug h small o pe ning s o n the side s o f the ve rte brae calle d fo ramina (sing ular = fo rame n). The se ne rve s transmit se nsatio ns fro m the butto cks and lo we r e xtre mitie s thro ug h the spinal co rd to the brain and transmit mo to r sig nals fro m the brain to the lo we r e xtre mitie s to pro duce mo ve me nt o f the le g s, to e s, and jo ints o f the lo we r e xtre mitie s.Lumbar ste no sis (spinal ste no sis) is a co nditio n whe re by e ithe r the spinal canal (ce ntral ste no sis) o r o ne o r mo re o f the ve rte bral fo ramina (fo raminal ste no sis) be co me s narro we d. I the f narro wing is substantial, it cause s co mpre ssio n o f the ne rve s, which cause s the painful sympto ms o f lumbar spinal ste no sis, including lo w back pain, butto ck pain, and le g pain and numbne ss that is made wo rse with walking and re lie ve d by re sting . The o utlo o k fo r patie nts with lumbar spinal ste no sis varie s and de pe nds o n the se ve rity and duratio n o f sympto ms at the time o f initiatio n o f tre atme nt. Ultimate ly, the o utlo o k de pe nds o n an individuals re spo nse to tre atme nt. The re spo nse to tre atme nt is also de pe nde nt o n the se ve rity and cause o f the lumbar spinal ste no sis as we ll as the unde rlying me dical co nditio n o f the patie nt.
    • With God all things are possible, I will win the battle one day at a time. I REFUSE to be a VICTIM to I diopat hic Fibr osing Mediast init is I diopat hic pulmonar y f ibr osis, Lumbo-sacr al or Lumber , Super ior vena cava syndr ome ONE PERSON, ONE VOICES, CAN MAKE A DIFFERENCES AND I CHOOSE TO BE THAT PERSON! FOR MORE INFO ON FIBROSING MEDIASTINITIS PLEASE VISIT MY WEBSITE AT,  http://fibrosingmediastinitis.webs.com/ Please take the time to read and learn, help save a life maybe even yours! Awareness is Powerful!
    • All Copy Rights, Jeanieann Marie Janis
    • Ovarian Cancer Survivor 2006 till 2012
    • BELIEVE FA P E IT O HH GODS LOVE STRENGTHEN                    ME AND MY WILL  TO LIVE F M My Awareness Ribbons C O